
Sickle Cell Medical Articles
Articles in the Medical Literature
See NLM- Medline articles about sickle cell disease for the past 6 months
May 2008
Alvarez O, Lopez-Mitnik G, Zilleruelo G. Short-term follow-up of patients with sickle cell disease and albuminuria. Pediatr Blood Cancer. 2008 Jun;50(6):1236-9. http://www.ncbi.nlm.nih.gov/pubmed/18293385?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Singh SA, Koumbourlis AC, Aygun B. Resolution of chronic hypoxemia in pediatric sickle cell patients after treatment with hydroxyurea. Pediatr Blood Cancer. 2008 Jun;50(6):1258-60. http://www.ncbi.nlm.nih.gov/pubmed/18293380?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Thein SL. Genetic modifiers of the beta-haemoglobinopathies. Br J Haematol. 2008 May;141(3):357-66. http://www.ncbi.nlm.nih.gov/pubmed/18410570?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Lisowski L, Sadelain M. Current status of globin gene therapy for the treatment of beta-thalassaemia. Br J Haematol. 2008 May;141(3):335-45. http://www.ncbi.nlm.nih.gov/pubmed/18410569?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hagar W, Vichinsky E. Advances in clinical research in sickle cell disease. Br J Haematol. 2008 May;141(3):346-56. Epub 2008 Mar 12. http://www.ncbi.nlm.nih.gov/pubmed/18341629?ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Pinto FO, Roberts I. Cord blood stem cell transplantation for haemoglobinopathies. Br J Haematol. 2008 May;141(3):309-24. Epub 2008 Feb 26. http://www.ncbi.nlm.nih.gov/pubmed/18307566?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Ataga KI, Smith WR, De Castro LM, Swerdlow P, Saunthararajah Y, Castro O, Vichinsky E, Kutlar A, Orringer EP, Rigdon GC, Stocker JW; ICA-17043-05 Investigators. Efficacy and safety of the Gardos channel blocker, senicapoc (ICA-17043), in patients with sickle cell anemia. Blood. 2008 Apr 15;111(8):3991-7. Epub 2008 Jan 11. http://www.ncbi.nlm.nih.gov/pubmed/18192510?ordinalpos=37&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
April 2008
Strouse JJ, Takemoto CM, Keefer JR, Kato GJ, Casella JF. Corticosteroids and increased risk of readmission after acute chest syndrome in children with sickle cell disease. Pediatr Blood Cancer. 2008 May;50(5):1006-12. http://www.ncbi.nlm.nih.gov/pubmed/17849474?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Wood KC, Hsu LL, Gladwin MT. Sickle cell disease vasculopathy: A state of nitric oxide resistance. Free Radic Biol Med. 2008 Apr 15;44(8):1506-28. Epub 2008 Jan 26. http://www.ncbi.nlm.nih.gov/pubmed/18261470?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Zempsky WT, Loiselle KA, McKay K, Blake GL, Hagstrom JN, Schechter NL, Kain ZN. Retrospective evaluation of pain assessment and treatment for acute vasoocclusive episodes in children with sickle cell disease. Pediatr Blood Cancer. 2008 Apr 3; http://www.ncbi.nlm.nih.gov/pubmed/18386784?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Adewoye AH, Chen TC, Ma Q, McMahon L, Mathieu J, Malabanan A, Steinberg MH, Holick MF. Sickle cell bone disease: Response to vitamin D and calcium. Am J Hematol. 2008 Apr;83(4):271-4. http://www.ncbi.nlm.nih.gov/pubmed/17924548?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Delea TE, Hagiwara M, Thomas SK, Baladi JF, Phatak PD, Coates TD. Outcomes, utilization, and costs among thalassemia and sickle cell disease patients receiving deferoxamine therapy in the United States. Am J Hematol. 2008 Apr;83(4):263-70. http://www.ncbi.nlm.nih.gov/pubmed/17924547?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Saunthararajah Y, Molokie R, Saraf S, Sidhwani S, Gowhari M, Vara S, Lavelle D, DeSimone J. Clinical effectiveness of decitabine in severe sickle cell disease. Br J Haematol. 2008 Apr;141(1):126-9. http://www.ncbi.nlm.nih.gov/pubmed/18324975?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Johnson C, Telen MJ. Adhesion molecules and hydroxyurea in the pathophysiology of sickle cell disease. Haematologica. 2008 Apr;93(4):481-5. http://www.haematologica.org/cgi/content/full/93/4/481
Canalli AA, Franco-Penteado CF, Saad ST, Conran N, Costa FF. Increased adhesive properties of neutrophils in sickle cell disease may be reversed by pharmacological nitric oxide donation. Haematologica. 2008 Apr;93(4):605-9. Epub 2008 Mar 6. http://www.ncbi.nlm.nih.gov/pubmed/18326523?ordinalpos=20&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Heeney MM, Ware RE. Hydroxyurea for children with sickle cell disease. Pediatr Clin North Am. 2008 Apr;55(2):483-501. http://www.ncbi.nlm.nih.gov/pubmed/18381097?ordinalpos=33&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Field JJ, Austin PF, An P, Yan Y, Debaun MR. Enuresis Is a Common and Persistent Problem Among Children and Young Adults with Sickle Cell Anemia. Urology. 2008 Apr 1; http://www.ncbi.nlm.nih.gov/pubmed/18384865?ordinalpos=41&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Platt OS. Hydroxyurea for the treatment of sickle cell anemia. N Engl J Med. 2008 Mar 27;358(13):1362-9. Review. http://content.nejm.org/cgi/content/extract/358/13/1362
van Beers EJ, van Tuijn CF, Mac Gillavry MR, van der Giessen A, Schnog JJ, Biemond BJ; on behalf of the CURAMA study group. Sickle cell disease-related organ damage occurs irrespective of pain rate: implications for clinical practice. Haematologica. 2008 Mar 26; http://www.ncbi.nlm.nih.gov/pubmed/18367483?ordinalpos=48&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Raphael JL, Kamdar A, Beavers MB, Mahoney DH, Mueller BU. Treatment of uncomplicated vaso-occlusive crises in children with sickle cell disease in a day hospital. Pediatr Blood Cancer. 2008 Mar 26; http://www.ncbi.nlm.nih.gov/pubmed/18383165?ordinalpos=49&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
March 2008
Valrie CR, Gil KM, Redding-Lallinger R, Daeschner C. Brief report: daily mood as a mediator or moderator of the pain-sleep relationship in children with sickle cell disease. J Pediatr Psychol. 2008 Apr;33(3):317-22. Epub 2007 Aug 8. http://www.ncbi.nlm.nih.gov/pubmed/17690117?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
McCarville MB, Goodin GS, Fortner G, Li CS, Smeltzer MP, Adams R, Wang W. Evaluation of a comprehensive transcranial doppler screening program for children with sickle cell anemia.Pediatr Blood Cancer. 2008 Apr;50(4):818-21. http://www.ncbi.nlm.nih.gov/pubmed/18085672?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Mekontso Dessap A, Leon R, Habibi A, Nzouakou R, Roudot-Thoraval F, Adnot S,Godeau B, Galacteros F, Brun-Buisson C, Brochard L, Maitre B. Pulmonary hypertension and cor pulmonale during severe acute chest syndrome in sickle cell disease. Am J Respir Crit Care Med. 2008 Mar 15;177(6):646-53. Epub 2008 Jan 3. http://www.ncbi.nlm.nih.gov/pubmed/18174543?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
van den Tweel XW, Hatzmann J, Ensink E, van der Lee JH, Peters M, Fijnvandraat K, Grootenhuis M. Quality of life of female caregivers of children with sickle cell disease: a survey. Haematologica. 2008 Mar 5; http://www.ncbi.nlm.nih.gov/pubmed/18322259?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Odièvre MH, Bony V, Benkerrou M, Lapouméroulie C, Alberti C, Ducrocq R, Jacqz-Aigrain E, Elion J, Cartron JP. Modulation of erythroid adhesion receptors expression by hydroxyurea in children with sickle cell disease. Haematologica. 2008 Mar 5; http://www.ncbi.nlm.nih.gov/pubmed/18322255?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Lucarelli G, Gaziev J. Advances in the allogeneic transplantation for thalassemia. Blood Rev. 2008 Mar;22(2):53-63. Epub 2007 Nov 26. http://www.ncbi.nlm.nih.gov/pubmed/18039551?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Locock L, Kai J. Parents' experiences of universal screening for haemoglobin disorders: implications for practice in a new genetics era. Br J Gen Pract. 2008 Mar;58(548):161-8. http://www.ncbi.nlm.nih.gov/pubmed/18318970?ordinalpos=21&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Colombatti R, Dalla Pozza LV, Mazzucato M, Sainati L, Pierobon M, Facchin P. Hospitalization of children with sickle cell disease in a region with increasing immigration rates. Haematologica. 2008 Mar;93(3):463-4. http://www.ncbi.nlm.nih.gov/pubmed/18310539?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Geller AK, O'Connor MK. The Sickle Cell Crisis: A Dilemma in Pain Relief. Mayo Clin Proc. 2008 Mar;83(3):320-323. http://www.mayoclinicproceedings.com/Abstract.asp?AID=4623&Abst=Abstract&UID=
Adamkiewicz TV, Silk BJ, Howgate J, Baughman W, Strayhorn G, Sullivan K, Farley MM. Effectiveness of the 7-valent pneumococcal conjugate vaccine in children with sickle cell disease in the first decade of life. Pediatrics. 2008 Mar;121(3):562-9. http://www.ncbi.nlm.nih.gov/pubmed/18310206?ordinalpos=38&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
February 2008
Darbari DS, van Schaik RH, Capparelli EV, Rana S, McCarter R, van den Anker J. UGT2B7 promoter variant -840G>A contributes to the variability in hepatic clearance of morphine in patients with sickle cell disease. Am J Hematol. 2008 Mar;83(3):200-2. http://www.ncbi.nlm.nih.gov/pubmed/17724700?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Shord SS, Chew L, Villano J. Evaluation of opioid induced nausea and vomiting in sickle cell disease. Am J Hematol. 2008 Mar;83(3):196-9. http://www.ncbi.nlm.nih.gov/pubmed/17724690?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Darbari DS, Minniti CP, Rana S, van den Anker J. Pharmacogenetics of morphine: Potential implications in sickle cell disease. Am J Hematol. 2008 Mar;83(3):233-6.
http://www.ncbi.nlm.nih.gov/pubmed/17722074?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum]
Appenzeller S, Fattori A, Saad ST, Costallat LT. Systemic lupus erythematosus in patients with sickle cell disease. Clin Rheumatol. 2008 Mar;27(3):359-64. Epub 2007 Nov 14. http://www.ncbi.nlm.nih.gov/pubmed/18000698?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Lebensburger J, Persons DA. Progress toward safe and effective gene therapy for beta-thalassemia and sickle cell disease. Curr Opin Drug Discov Devel. 2008 Mar;11(2):225-32. http://www.ncbi.nlm.nih.gov/pubmed/18283610?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
McNaughton-Smith GA, Burns JF, Stocker JW, Rigdon GC, Creech C, Arrington S, Shelton T, de Franceschi L. Novel inhibitors of the gardos channel for the treatment of sickle cell disease. J Med Chem. 2008 Feb 28;51(4):976-82. Epub 2008 Jan 31. http://www.ncbi.nlm.nih.gov/pubmed/18232633?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Singh SA, Koumbourlis AC, Aygun B. Resolution of chronic hypoxemia in pediatric sickle cell patients after treatment with hydroxyurea.
Pediatr Blood Cancer. 2008 Feb 21; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/18293380?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Jenerette CM, Murdaugh C. Testing the theory of self-care management for sickle cell disease. Res Nurs Health. 2008 Feb 4; http://www.ncbi.nlm.nih.gov/pubmed/18247376?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Solomon LR. Treatment and prevention of pain due to vaso-occlusive crises in adults with sickle cell disease: an educational void. Blood. 2008 Feb 1;111(3):997-1003. Epub 2007 Oct 16. http://www.ncbi.nlm.nih.gov/pubmed/17940207?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Frei-Jones MJ, Baxter AL, Rogers ZR, Buchanan GR. Vaso-occlusive episodes in older children with sickle cell disease: emergency department management and pain assessment. J Pediatr. 2008 Feb;152(2):281-5. Epub 2007 Oct 24.
http://www.ncbi.nlm.nih.gov/pubmed/18206703?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hankins JS, Helton KJ, McCarville MB, Li CS, Wang WC, Ware RE. Preservation of spleen and brain function in children with sickle cell anemia treated with hydroxyurea. Pediatr Blood Cancer. 2008 Feb;50(2):293-7. http://www.ncbi.nlm.nih.gov/pubmed/17554794?ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hines P, Dover GJ, Resar LM. Pulsed-dosing with oral sodium phenylbutyrate increases hemoglobin F in a patient with sickle cell anemia.
Pediatr Blood Cancer. 2008 Feb;50(2):357-9. http://www.ncbi.nlm.nih.gov/pubmed/17253639?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Levenson JL, McClish DK, Dahman BA, Bovbjerg VE, de A Citero V, Penberthy LT, Aisiku IP, Roberts JD, Roseff SD, Smith WR. Depression and anxiety in adults with sickle cell disease: the PiSCES project. Psychosom Med. 2008 Feb;70(2):192-6. Epub 2007 Dec 24. http://www.ncbi.nlm.nih.gov/pubmed/18158366?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
January 2008
King AA, Noetzel M, White DA, McKinstry RC, Debaun MR. Blood transfusion therapy is feasible in a clinical trial setting in children with sickle cell disease and silent cerebral infarcts. Pediatr Blood Cancer. 2008 Mar;50(3):599-602.
http://www.ncbi.nlm.nih.gov/pubmed/17985350?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Halabi-Tawil M, Lionnet F, Girot R, Bachmeyer C, Lévy PP, Aractingi S. Sickle cell leg ulcers: a frequently disabling complication and a marker of severity. Br J Dermatol. 2008 Feb;158(2):339-44. Epub 2007 Nov 28. http://www.ncbi.nlm.nih.gov/pubmed/18047512?ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hernigou P, Zilber S, Filippini P, Mathieu G, Poignard A, Galacteros F. Total THA in Adult Osteonecrosis Related to Sickle Cell Disease. Clin Orthop Relat Res. 2008 Feb;466(2):300-8. Epub 2008 Jan 10. http://www.ncbi.nlm.nih.gov/pubmed/18196410?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Frei-Jones MJ, Baxter AL, Rogers ZR, Buchanan GR. Vaso-occlusive episodes in older children with sickle cell disease: emergency department management and pain assessment. J Pediatr. 2008 Feb;152(2):281-5. Epub 2007 Oct 24. http://www.ncbi.nlm.nih.gov/pubmed/18206703?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Smiley D, Dagogo-Jack S, Umpierrez G. Therapy insight: metabolic and endocrine disorders in sickle cell disease. Nat Clin Pract Endocrinol Metab. 2008 Feb;4(2):102-9. http://www.ncbi.nlm.nih.gov/pubmed/18212812?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Barnett CF, Hsue PY, Machado RF. Pulmonary hypertension: an increasingly recognized complication of hereditary hemolytic anemias and HIV infection. JAMA. 2008 Jan 23;299(3):324-31. Review. http://www.ncbi.nlm.nih.gov/pubmed/18212317?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Kavanagh PL, Wang CJ, Therrell BL, Sprinz PG, Bauchner H. Communication of positive newborn screening results for sickle cell disease and sickle cell trait: Variation across states.Am J Med Genet C Semin Med Genet. 2008 Jan 15;148C(1):15-22 [Epub ahead of print] http://www.ncbi.nlm.nih.gov/pubmed/18200513?ordinalpos=35&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Smith WR, Penberthy LT, Bovbjerg VE, McClish DK, Roberts JD, Dahman B, Aisiku IP, Levenson JL, Roseff SD. Daily assessment of pain in adults with sickle cell disease.Ann Intern Med. 2008 Jan 15;148(2):94-101. http://www.ncbi.nlm.nih.gov/pubmed/18195334?ordinalpos=36&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
December 2007
Jastaniah W, Harmatz P, Pakbaz Z, Fischer R, Vichinsky E, Walters MC. Transfusional iron burden and liver toxicity after bone marrow transplantation
for acute myelogenous leukemia and hemoglobinopathies.Pediatr Blood Cancer. 2008 Feb;50(2):319-24.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17557314&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hankins JS, Helton KJ, McCarville MB, Li CS, Wang WC, Ware RE. Preservation of spleen and brain function in children with sickle cell anemiatre ated with hydroxyurea. Pediatr Blood Cancer. 2008 Feb;50(2):293-7.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17554794&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hines P, Dover GJ, Resar LM. Pulsed-dosing with oral sodium phenylbutyrate increases hemoglobin F in a patient with sickle cell anemia. Pediatr Blood Cancer. 2008 Feb;50(2):357-9.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17253639&ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Spivey JF, Uong EC, Strunk R, Boslaugh SE, DeBaun MR. Low daytime pulse oximetry reading is associated with nocturnal desaturation and obstructive sleep apnea in children with sickle cell anemia. Pediatr Blood Cancer. 2008 Feb;50(2):359-62.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17072857&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hagar RW, Michlitsch JG, Gardner J, Vichinsky EP, Morris CR. Clinical differences between children and adults with pulmonary hypertension and sickle cell disease. Br J Haematol. 2008 Jan;140(1):104-12. Epub 2007 Oct 3.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17916102&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Karam LB, Disco D, Jackson SM, Lewin D, McKie V, Baker RD, Baker SS, Laver JH, Nietert PJ, Abboud MR. Liver biopsy results in patients with sickle cell disease on chronic transfusions: poor correlation with ferritin levels. Pediatr Blood Cancer. 2008 Jan;50(1):62-5.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17457853&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Shankar SM, Arbogast PG, Mitchel E, Ding H, Wang WC, Griffin MR. Impact of proximity to comprehensive sickle cell center on utilization of healthcare services among children with sickle cell disease. Pediatr Blood Cancer. 2008 Jan;50(1):66-71.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=16998856&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Pawar SS, Panepinto JA, Brousseau DC. The effect of acute pain crisis on exhaled nitric oxide levels in children with sickle cell disease. Pediatr Blood Cancer. 2008 Jan;50(1):111-3.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=16619223&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Citero Vde A, Levenson JL, McClish DK, Bovbjerg VE, Cole PL, Dahman BA,Penberthy LT, Aisiku IP, Roseff SD, Smith WR. The role of catastrophizing in sickle cell disease--the PiSCES project. Pain. 2007 Dec 15;133(1-3):39-46. Epub 2007 Apr 3.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17408858&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hanna J, Wernig M, Markoulaki S, Sun CW, Meissner A, Cassady JP, Beard C, Brambrink T, Wu LC, Townes TM, Jaenisch R. Treatment of Sickle Cell Anemia Mouse Model with iPS Cells Generated from Autologous Skin. Science. 2007 Dec 6; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=18063756&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Bhatia M, Walters MC. Hematopoietic cell transplantation for thalassemia and sickle cell disease: past, present and future. Bone Marrow Transplant. 2007 Dec 3; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=18059330&ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
November 2007
Shawn M. Bediako, Annette R. Lavender and Zahida Yasin Racial Centrality and Health Care Use Among African American Adults With Sickle Cell Disease Journal of Black Psychology 2007; 33; 422 http://jbp.sagepub.com/cgi/content/abstract/33/4/422
Aslan M, Freeman BA. Redox-dependent impairment of vascular function in sickle cell disease.Free Radic Biol Med. 2007 Dec 1;43(11):1469-83. Epub 2007 Aug 31. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17964418&ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Inati A, Jradi O, Tarabay H, Moallem H, Rachkidi Y, El Accaoui R, Isma'eel H, Wehbe R, Mfarrej BG, Dabbous I, Taher A. Sickle cell disease: the Lebanese experience. Int J Lab Hematol. 2007 Dec;29(6):399-408. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17988293&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Ozbek OY, Malbora B, Sen N, Yazici AC, Ozyurek E, Ozbek N. Airway hyperreactivity detected by methacholine challenge in children with sickle
cell disease. Pediatr Pulmonol. 2007 Dec;42(12):1187-92. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17960821&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Appenzeller S, Fattori A, Saad ST, Costallat LT. Systemic lupus erythematosus in patients with sickle cell disease.Clin Rheumatol. 2007 Nov 14; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=18000698&ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hankins JS, Wynn LW, Brugnara C, Hillery CA, Li CS, Wang WC. Phase I study of magnesium pidolate in combination with hydroxycarbamide for children with sickle cell anaemia.Br J Haematol. 2007 Nov 7; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17991298&ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Shenoy S. Has stem cell transplantation come of age in the treatment of sickle cell disease? Bone Marrow Transplant. 2007 Nov;40(9):813-21. Epub 2007 Aug 20. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17704797&ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Tripette J, Hardy-Dessources MD, Sara F, Montout-Hedreville M, Saint-Martin C, Hue O, Connes P. Does Repeated and Heavy Exercise Impair Blood Rheology in Carriers of Sickle Cell Trait? Clin J Sport Med. 2007 Nov;17(6):465-470. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17993789&ordinalpos=25&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Marlin L, Sara F, Antoine-Jonville S, Connes P, Etienne-Julan M, Hue O. Ventilatory and lactic thresholds in subjects with sickle cell trait. Int J Sports Med. 2007 Nov;28(11):916-20. Epub 2007 May 11. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17497586&ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Lionnet F, Bachmeyer C, Sloma I, Rossier A, Thioliere B, Maier M, Grateau G, Girot R, Cadranel J. Tuberculosis in adult patients with sickle cell disease.
J Infect. 2007 Nov;55(5):439-44. Epub 2007 Aug 22. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17714789&ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Schatz J, Roberts CW. Neurobehavioral impact of sickle cell disease in early childhood. J Int Neuropsychol Soc. 2007 Nov;13(6):933-43. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17942011&ordinalpos=30&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Barakat LP, Patterson CA, Weinberger BS, Simon K, Gonzalez ER, Dampier C. A Prospective Study of the Role of Coping and Family Functioning in Health
Outcomes for Adolescents With Sickle Cell Disease. J Pediatr Hematol Oncol. 2007 Nov;29(11):752-760.
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October 2007
Dyson, SM; Atkin, K; Culley, LA and Dyson, SE (2007) The educational experiences of young people with sickle cell disorder: a commentary on existing literature. Disability and Society 22 (6): 581-594. http://www.informaworld.com/openurl?genre=article&issn=0968-7599&volume=22&issue=6&spage=581
Lee SP, Ataga KI, Zayed M, Manganello JM, Orringer EP, Phillips DR, Parise LV. Phase I study of eptifibatide in patients with sickle cell anaemia. Br J Haematol. 2007 Oct 3; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17916103&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Lavelle D, Chin J, Vaitkus K, Redkar S, Phiasivongsa P, Tang C, Will R, Hankewych M, Roxas B, Singh M, Saunthararajah Y, Desimone J. Oral decitabine reactivates expression of the methylated gamma-globin gene in Papio anubis. Am J Hematol. 2007 Nov;82(11):981-5. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17696208&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
van Beers EJ, van Tuijn CF, Nieuwkerk PT, Friederich PW, Vranken JH, Biemond BJ. Patient-controlled analgesia versus continuous infusion of morphine during vaso-occlusive crisis in sickle cell disease, a randomized controlled trial. Am J Hematol. 2007 Nov;82(11):955-60. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17617790&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Wu CJ, Gladwin M, Tisdale J, Hsieh M, Law T, Biernacki M, Rogers S, Wang X, Walters M, Zahrieh D, Antin JH, Ritz J, Krishnamurti L. Mixed haematopoietic chimerism for sickle cell disease prevents intravascular haemolysis. Br J Haematol. 2007 Nov;139(3):504-7. No abstract available.
McLeod BC. Evidence based therapeutic apheresis in autoimmune and other hemolytic anemias. Curr Opin Hematol. 2007 Nov;14(6):647-54. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17898570&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Klings ES. Pulmonary hypertension of sickle cell disease: More than just another lung disease. Am J Hematol. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17924550&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
H Adewoye A, C Chen T, Ma Q, McMahon L, Mathieu J, Malabanan A, H Steinberg M, F Holick M. Sickle cell bone disease: Response to vitamin D and calcium. Am J Hematol. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17924548&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Delea TE, Hagiwara M, Thomas SK, Baladi JF, Phatak PD, Coates TD. Outcomes, utilization, and costs among thalassemia and sickle cell disease patients receiving deferoxamine therapy in the United States. Am J Hematol. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17924547&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Deane C, Goss D, O'driscoll S, Melllor S, Pohl K, Dick MC, Height SE, Rees DC. Transcranial Doppler Scanning and the Assessment of Stroke Risk in Children with HbSC disease. Arch Dis Child. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17925326&ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hagar RW, Michlitsch JG, Gardner J, Vichinsky EP, Morris CR. Clinical differences between children and adults with pulmonary hypertension and sickle cell disease. Br J Haematol. 2007 Oct 3; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17916102&ordinalpos=15&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Marlin L, Connes P, Antoine-Jonville S, Tripette J, Montout-Hedreville M, Sanouiller A, Etienne-Julan M, Hue O. Cardiorespiratory responses during three repeated incremental exercise tests in sickle cell trait carriers. Eur J Appl Physiol. 2007 Oct 2; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17909842&ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Quinn CT, Lee NJ, Shull EP, Ahmad N, Rogers ZR, Buchanan GR. Prediction of adverse outcomes in children with sickle cell anemia: a study of the Dallas Newborn Cohort. Blood. 2007 Oct 1; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17909076&ordinalpos=21&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Bernaudin F, Socie G, Kuentz M, Chevret S, Duval M, Bertrand Y, Vannier JP, Yakouben K, Thuret I, Bordigoni P, Fischer A, Lutz P, Stephan JL, Dhedin N, Plouvier E, Margueritte G, Bories D, Verlhac S, Esperou H, Coic L, Vernant JP, Gluckman E; SFGM-TC. Long-term results of related myeloablative stem-cell transplantation to cure sickle cell disease. Blood. 2007 Oct 1;110(7):2749-56. Epub 2007 Jul 2. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17606762&ordinalpos=23&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Sebastiani P, Nolan VG, Baldwin CT, Abad-Grau MM, Wang L, Adewoye AH, McMahon LC, Farrer LA, Taylor JG 4th, Kato GJ, Gladwin MT, Steinberg MH. A network model to predict the risk of death in sickle cell disease. Blood. 2007 Oct 1;110(7):2727-35. Epub 2007 Jun 28. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17600133&ordinalpos=24&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Vasavda N, Ulug P, Kondaveeti S, Ramasamy K, Sugai T, Cheung G, Rees DC, Awogbade M, Bannister S, Cunningham J, Menzel S, Thein SL. Circulating DNA: a potential marker of sickle cell crisis. Br J Haematol. 2007 Oct;139(2):331-6. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17897311&ordinalpos=26&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Vekilov PG. Sickle-cell haemoglobin polymerization: is it the primary pathogenic event of sickle-cell anaemia? Br J Haematol. 2007 Oct;139(2):173-84. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17897293&ordinalpos=27&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
September 2007
The National Toxicology Program (NTP) Center for the Evaluation of Risks to Human
Reproduction (CERHR) convened an expert panel on January 24–26, 2007, in Alexandria, Virginia to evaluate hydroxyurea. The report in full text is available atAtaga KI, Cappellini MD, Rachmilewitz EA. beta-Thalassaemia and sickle cell anaemia as paradigms of hypercoagulability. Br J Haematol. 2007 Oct;139(1):3-13. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17854302&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Villagra J, Shiva S, Hunter LA, Machado RF, Gladwin MT, Kato GJ. Platelet activation in patients with sickle disease, hemolysis-associated pulmonary hypertension, and nitric oxide scavenging by cell-free hemoglobin. Blood. 2007 Sep 15;110(6):2166-72. Epub 2007 May 29. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17536019&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Morris CR, Suh JH, Hagar W, Larkin S, Bland DA, Steinberg MH, Vichinsky EP,Shigenaga M, Ames B, Kuypers FA, Klings ES. Erythrocyte glutamine depletion, altered redox environment, and pulmonary hypertension in sickle cell disease. Blood. 2007 Sep 11; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17848621&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Strouse JJ, Takemoto CM, Keefer JR, Kato GJ, Casella JF. Corticosteroids and increased risk of readmission after acute chest syndrome in children with sickle cell disease. Pediatr Blood Cancer. 2007 Sep 11; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17849474&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Traina F, Jorge SG, Yamanaka A, de Meirelles LR, Costa FF, Saad ST. Chronic Liver Abnormalities in Sickle Cell Disease: A Clinicopathological Study in 70 Living Patients.Acta Haematol. 2007 Sep 3;118(3):129-135 [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17785963&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Mazumdar M, Heeney MM, Sox CM, Lieu TA. Preventing Stroke Among Children With Sickle Cell Anemia: An Analysis of Strategies That Involve Transcranial Doppler Testing and Chronic Transfusion. Pediatrics. 2007 Sep 3; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17768181&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Sylvester K, Patey R, Rafferty G, Rees D, Thein S, Greenough A. Peak expiratory flow in Afro-Caribbean children with and without sickle cell anaemia. Acta Paediatr. 2007 Sep;96(9):1308-10. Epub 2007 Jul 31. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17666101&ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Krejza J, Rudzinski W, Pawlak MA, Tomaszewski M, Ichord R, Kwiatkowski J, Gor D, Melhem ER. Angle-Corrected Imaging Transcranial Doppler Sonography versus Imaging and Nonimaging Transcranial Doppler Sonography in Children with Sickle Cell Disease. AJNR Am J Neuroradiol. 2007 Sep;28(8):1613-8. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17846223&ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Pakbaz Z, Fischer R, Fung E, Nielsen P, Harmatz P, Vichinsky E. Serum ferritin underestimates liver iron concentration in transfusion independent thalassemia patients as compared to regularly transfused thalassemia and sickle cell patients. Pediatr Blood Cancer. 2007 Sep;49(3):329-32. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17554789&ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Morris, C Hemolysis-Associated Pulmonary Hypertension in Sickle Cell Disease: Global Disruption of the Arginine-Nitric Oxide Pathway Current Hypertension Reviews, Volume 3, Number 3, August 2007 , pp. 223-230(8) http://www.ingentaconnect.com/content/ben/chyr/2007/00000003/00000003/art00009
August 2007
Galkin, O., Nagel, R. L. & Vekilov, P. G. (2007). The kinetics of nucleation and growth of sickle cell hemoglobin fibers. J. Mol. Biol. 365,
425-439.Full Text PDF
Pan, W., Galkin, O., Filobelo, L., Nagel, R. L. & Vekilov, P. G. (2007). Metastable mesoscopic clusters in solutions of sickle cell hemoglobin.
Biophys. J. 92, 267-277. Full Text PDF
Galkin, O., Pan, W., Filobelo, L., Hirsch, R. E., Nagel, R. L. & Vekilov,
P. G. (2007). Two-step mechanism of homogeneous nucleation of sickle cell
hemoglobin polymers. Biophys. J. 92, 902-913. Full
Text PDF
Creary, M., Williamson, D, Kulkarni, R. Journal of Women's Health. 2007, 16(5): 575-582. doi:10.1089/jwh.2007.CDC4. http://www.liebertonline.com/doi/abs/10.1089/jwh.2007.CDC4
Pakbaz Z, Fischer R, Fung E, Nielsen P, Harmatz P, Vichinsky E. Serum ferritin underestimates liver iron concentration in transfusion independent thalassemia patients as compared to regularly transfused thalassemia and sickle cell patients. Pediatr Blood Cancer. 2007 Sep;49(3):329-32. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17554789&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Brambilla DJ, Miller ST, Adams RJ. Intra-individual variation in blood flow velocities in cerebral arteries of children with sickle cell disease. Pediatr Blood Cancer. 2007 Sep;49(3):318-22. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17243135&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Adamkiewicz TV, Szabolcs P, Haight A, Baker KS, Staba S, Kedar A, Chiang KY, Krishnamurti L, Boyer MW, Kurtzberg J, Wagner JE, Wingard JR, Yeager AM. Unrelated cord blood transplantation in children with sickle cell disease: Review of four-center experience. Pediatr Transplant. 2007 Sep;11(6):641-4.
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Sylvester KP, Patey RA, Kassim Z, Rafferty GF, Rees D, Thein SL, Greenough A. Lung gas transfer in children with sickle cell anaemia. Respir Physiol Neurobiol. 2007 Aug 15;158(1):70-4. Epub 2007 Apr 8. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17512804&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Hanchard N, Elzein A, Trafford C, Rockett K, Pinder M, Jallow M, Harding R,Kwiatkowski D, McKenzie C. Classical beta-globin sickle haplotypes exhibit a high degree of long-range haplotype similarity in African and Afro-Caribbean populations. BMC Genet. 2007 Aug 10;8(1):52 http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17688704&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Onyekwere OC, Campbell A, Teshome M, Onyeagoro S, Sylvan C, Akintilo A, Hutchinson S, Ensing G, Gaskin P, Kato G, Rana S, Kwagyan J, Gordeuk V, Williams J, Castro O. Pulmonary Hypertension in Children and Adolescents with Sickle Cell Disease. Pediatr Cardiol. 2007 Aug 7; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17680298&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Crawford MW, Shichor T, Engelhardt T, Adamson G, Bell D, Carmichael FJ, Kim PC. The Novel Hemoglobin-based Oxygen Carrier HRC 101 Improves Survival in Murine Sickle Cell Disease. Anesthesiology. 2007 Aug;107(2):281-287. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17667573&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Zimmerman SA, Schultz WH, Burgett S, Mortier NA, Ware RE. Hydroxyurea therapy lowers transcranial Doppler flow velocities in children with sickle cell anemia. Blood. 2007 Aug 1;110(3):1043-7. Epub 2007 Apr 11. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17429008&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Austin H, Key NS, Benson JM, Lally C, Dowling NF, Whitsett C, Hooper WC. Sickle cell trait and the risk of venous thromboembolism among blacks. Blood. 2007 Aug 1;110(3):908-12. Epub 2007 Apr 4. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17409269&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
July 2007
Knox-Macaulay HH, Ahmed MM, Gravell D, Al-Kindi S, Ganesh A. Sickle cell-haemoglobin E (HbSE) compound heterozygosity: a clinical and haematological study.Int J Lab Hematol. 2007 Aug;29(4):292-301. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17617080&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Valrie CR, Gil KM, Redding-Lallinger R, Daeschner C. Brief report: sleep in children with sickle cell disease: an analysis of daily diaries utilizing multilevel models.J Pediatr Psychol. 2007 Aug;32(7):857-61. Epub 2007 Mar 30. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17400602&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Rahimi Z, Vaisi-Raygani A, Nagel RL, Muniz A. Thrombophilic mutations among Southern Iranian patients with sickle cell disease: high prevalence of factor V Leiden. J Thromb Thrombolysis. 2007 Jul 11; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17619828&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
van Beers EJ, van Tuijn CF, Nieuwkerk PT, Friederich PW, Vranken JH, Biemond BJ. Patient-controlled analgesia versus continuous infusion of morphine during vaso-occlusive crisis in sickle cell disease, a randomized controlled trial.Am J Hematol. 2007 Jul 6; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17617790&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Howe AS, Boden BP. Heat-Related Illness in Athletes.Am J Sports Med. 2007 Jul 3; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17609528&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Bernaudin F, Socie G, Kuentz M, Chevret S, Duval M, Bertrand Y, Vannier JP,Yakouben K, Thuret I, Bordigoni P, Fischer A, Lutz P, Stephan JL, Dhedin N, Plouvier E, Margueritte G, Bories D, Verlhac S, Esperou H, Coic L, Vernant JP,Gluckman E. Long-term results of related, myeloablative stem cell transplantation to cure sickle cell disease.Blood. 2007 Jul 2; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17606762&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Telfer P, Coen P, Chakravorty S, Wilkey O, Evans J, Newell H, Smalling B, Amos R, Stephens A, Rogers D, Kirkham F. Clinical outcomes in children with sickle cell disease living in England: a neonatal cohort in East London. Haematologica. 2007 Jul;92(7):905-12. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17606440&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Niebanck AE, Pollock AN, Smith-Whitley K, Raffini LJ, Zimmerman RA, Ohene-Frempong K, Kwiatkowski JL. Headache in children with sickle cell disease: prevalence and associated factors. J Pediatr. 2007 Jul;151(1):67-72, 72.e1. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17586193&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Ejindu VC, Hine AL, Mashayekhi M, Shorvon PJ, Misra RR. Musculoskeletal manifestations of sickle cell disease.Radiographics. 2007 Jul-Aug;27(4):1005-21. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17620464&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
June 2007
Dyson, SM; Cochran, F; Culley, LA; Dyson, SE, Kennefick, A; Kirkham, M; Morris, P; Sutton, F; and Squire, P (2007) Observation and Interview Findings from the Ethnicity Questions and Antenatal Screening for Sickle Cell/Thalassaemia [EQUANS] Study. Critical Public Health 17 (1): 31-43. ISSN 0958-1596 http://www.informaworld.com/smpp/content~content=a773302146~db=all~order=page
Tubman VN, Bennett CM, Luo HY, Chui DH, Heeney MM. Sickle cell disease caused by Hb
S/Quebec-CHORI: Treatment with hydroxyurea and
response. Pediatr Blood Cancer. 2007 Aug;49(2):207-10. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17551985&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Aprelev A, Weng W, Zakharov M, Rotter M, Yosmanovich D, Kwong S, Briehl RW, Ferrone FA. Metastable polymerization of sickle hemoglobin in droplets. J Mol Biol. 2007 Jun 22;369(5):1170-4. Epub 2007 Apr 19. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17493634&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Anthi A, Machado RF, Jison ML, Taveira-Dasilva AM, Rubin
LJ, Hunter L, Hunter
CJ, Coles W, Nichols J, Avila NA, Sachdev V, Chen CC, Gladwin MT.
Hemodynamic and functional assessment of patients with sickle cell disease and pulmonary hypertension.
Am J Respir Crit Care Med. 2007 Jun 15;175(12):1272-9. Epub 2007 Mar 22. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17379852&ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hankins J, Hinds P, Day S, Carroll Y, Li CS, Garvie P, Wang W. Therapy preference and decision-making among patients with severe sickle cell
anemia and their families. Pediatr Blood Cancer. 2007 Jun 15;48(7):705-10. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=16732581&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Odhiambo A, Perlman DH, Huang H, Costello CE, Farber HW, Steinberg MH, McComb
ME, Klings ES. Identification of oxidative post-translational modification of serum albumin in
patients with idiopathic pulmonary arterial hypertension and pulmonary hypertension of sickle cell anemia.
Rapid Commun Mass Spectrom. 2007 Jun 14;21(14):2195-2203 [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17569101&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Zhu J, Kren BT, Park CW, Bilgim R, Wong
PY, Steer CJ. Erythroid-Specific Expression of beta-Globin by the Sleeping Beauty Transposon
for Sickle Cell Disease. Biochemistry. 2007 Jun 12;46(23):6844-58. Epub 2007 May 18.
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Hankins JS, Helton KJ, McCarville MB, Li CS, Wang WC, Ware RE. Preservation of spleen and brain function in children with sickle cell anemia
treated with hydroxyurea. Pediatr Blood Cancer. 2007 Jun 6; [Epub ahead of print]
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Graham JK, Mosunjac M, Hanzlick RL, Mosunjac M. Sickle Cell Lung Disease and Sudden Death: A Retrospective/Prospective Study of
21 Autopsy Cases and Literature Review. Am J Forensic Med Pathol. 2007 Jun;28(2):168-172.
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Adewoye AH, Nolan V, McMahon L, Ma Q, Steinberg MH. Effectiveness of a dedicated day hospital for management of acute sickle cell
pain. Haematologica. 2007 Jun;92(6):854-5. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17550862&ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
May 2007
Hankins J, Hinds P, Day S, Carroll Y, Li CS, Garvie P, Wang W. Therapy
preference and decision-making among patients with severe sickle cell
anemia and their families&. Pediatr Blood Cancer. 2007 Jun 15;48(7):705-10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16732581&query_hl=1&itool=pubmed_DocSum
Zilberman MV, Du W, Das S, Sarnaik SA. Evaluation of left ventricular
diastolic function in pediatric sickle cell
disease patients.Am J Hematol. 2007 Jun;82(6):433-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17266053&query_hl=1&itool=pubmed_DocSum
Panepinto JA, Walters MC, Carreras J, Marsh J, Bredeson CN, Gale RP, Hale GA,
Horan J, Hows JM, Klein JP, Pasquini R, Roberts I, Sullivan K, Eapen M, Ferster
A; On behalf of the Non-Malignant Marrow Disorders Working Committee,
Center for International Blood and Marrow Transplant Research.
Matched-related donor transplantation for sickle cell disease: report from
the Center for International Blood and Transplant Research.
Br J Haematol. 2007 Jun;137(5):479-85. Epub 2007 Apr 24. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17459050&query_hl=1&itool=pubmed_DocSum
Halasa NB, Shankar SM, Talbot TR, Arbogast PG, Mitchel EF, Wang WC,Schaffner
W, Craig AS, Griffin MR.
Incidence of invasive pneumococcal disease among individuals with sickle
cell disease before and after the introduction of the pneumococcal conjugate
vaccine.Clin Infect Dis. 2007 Jun 1;44(11):1428-33. Epub 2007 Apr 18. Full
Text http://www.journals.uchicago.edu/CID/journal/issues/v44n11/41426/41426.html
Koumbourlis AC, Lee DJ, Lee A. Longitudinal changes in lung function and somatic
growth in children with
sickle cell disease.Pediatr Pulmonol. 2007 Jun;42(6):483-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17469146&query_hl=1&itool=pubmed_DocSum
Akgul F, Yalcin F, Seyfeli E, Ucar E, Karazincir S, Balci A, Gali E.
Pulmonary Hypertension in Sickle-Cell Disease: Comorbidities and
Echocardiographic Findings. Acta Haematol. 2007 May 14;118(1):53-60 [Epub ahead
of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17505130&query_hl=1&itool=pubmed_DocSum
Marlin L, Sara F, Antoine-Jonville S, Connes P, Etienne-Julan M, Hue O.
Ventilatory and Lactic Thresholds in Subjects with Sickle Cell Trait.
Int J Sports Med. 2007 May 11; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17497586&query_hl=1&itool=pubmed_DocSum
Yu J, Heck S, Yazdanbakhsh K. Prevention of red cell alloimmunization
by CD25 regulatory T cells in mouse
models. Am J Hematol. 2007 May 9; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17492644&query_hl=1&itool=pubmed_DocSum
Rivera A. Reduced sickle erythrocyte dehydration in vivo by
endothelin-1 receptor antagonists.
Am J Physiol Cell Physiol. 2007 May 9; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17494628&query_hl=1&itool=pubmed_DocSum
Finnegan EM, Barabino GA, Liu XD, Chang HY, Jonczyk A, Kaul DK.
Small-Molecule Cyclic {alpha}V{beta}3 Antagonists Inhibit Sickle Red Cell
Adhesion to Vascular Endothelium and Vaso-Occlusion. Am J Physiol Heart Circ
Physiol. 2007 May 4; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17483236&query_hl=1&itool=pubmed_DocSum
Goers T, Panepinto J, Debaun M, Blinder M, Foglia R, Oldham KT, Field JJ.
Laparoscopic versus open abdominal surgery in children with sickle cell disease
is associated with a shorter hospital stay. Pediatr Blood Cancer. 2007 May 4; [Epub
ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17480009&query_hl=1&itool=pubmed_DocSum
Tanabe P, Myers R, Zosel A, Brice J, Ansari AH, Evans J, Martinovich Z, Todd
KH, Paice JA.
Emergency department management of acute pain episodes in sickle cell
disease. Acad Emerg Med. 2007 May;14(5):419-25. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17389246&query_hl=1&itool=pubmed_DocSum
Mitchell MJ, Lemanek K, Palermo TM, Crosby LE, Nichols A, Powers SW.
Parent perspectives on pain management, coping, and family functioning in
pediatric sickle cell disease. Clin Pediatr (Phila). 2007 May;46(4):311-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17475988&query_hl=1&itool=pubmed_DocSum
Gustafson SL, Gettig EA, Watt-Morse M, Krishnamurti L. Health beliefs
among African American women regarding genetic testing and
counseling for sickle cell disease.Genet Med. 2007 May;9(5):303-310. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17505208&query_hl=1&itool=pubmed_DocSum
Kawchak DA, Schall JI, Zemel BS, Ohene-Frempong K, Stallings VA.
Adequacy of dietary intake declines with age in children with sickle cell
disease.J Am Diet Assoc. 2007 May;107(5):843-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17467383&query_hl=1&itool=pubmed_DocSum
Nelson SC, Adade BB, McDonough EA, Moquist KL, Hennessy JM. High
Prevalence of Pulmonary Hypertension in Children With Sickle Cell Disease.
J Pediatr Hematol Oncol. 2007 May;29(5):334-337. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17483714&query_hl=1&itool=pubmed_DocSum
April 2007
1: Wang WC. The pathophysiology, prevention, and treatment of stroke in sickle cell
disease.Curr Opin Hematol. 2007 May;14(3):191-197. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17414206&query_hl=12&itool=pubmed_DocSum
2: Howard SC, Wilimas JA, Flores A, Pacheco C, de Reyes G, Machin S, Svarch E,
Navarrete M, Nieves R, Rodriguez H, Masera G. Treatment for children with severe aplastic anemia and sickle cell disease in
low income countries in Latin America: A report on the recent meetings of the
Monza International School of Pediatric Hematology/Oncology (MISPHO): Part III.
Pediatr Blood Cancer. 2007 May;48(5):598-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16883599&query_hl=12&itool=pubmed_DocSum
3: Le Gallais D, Lonsdorfer J, Bogui P, Fattoum S, Connes P, Hardy-Dessources
MD, Hue O. Point-Counterpoint: Sickle cell trait should/should not be considered
asymptomatic and as a benign condition during physical activity.
J Appl Physiol. 2007 Apr 19; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17395764&query_hl=12&itool=pubmed_DocSum
4: Manchikanti A, Grimes D, Lopez L, Schulz K. Steroid hormones for contraception in women with sickle cell disease.
Cochrane Database Syst Rev. 2007 Apr 18;2:CD006261. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443618&query_hl=12&itool=pubmed_DocSum
5: Al Hajeri A, Fedorowicz Z, Omran A, Tadmouri G. Piracetam for reducing the incidence of painful sickle cell disease crises.
Cochrane Database Syst Rev. 2007 Apr 18;(2):CD006111. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443614&query_hl=12&itool=pubmed_DocSum
6: Marti-Carvajal A, Conterno L, Knight-Madden J. Antibiotics for treating acute chest syndrome in people with sickle cell
disease.Cochrane Database Syst Rev. 2007 Apr 18;(2):CD006110. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443613&query_hl=12&itool=pubmed_DocSum
7: Okomo U, Meremikwu M. Fluid replacement therapy for acute episodes of pain in people with sickle cell
disease.Cochrane Database Syst Rev. 2007 Apr 18;(2):CD005406. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443589&query_hl=12&itool=pubmed_DocSum
8: Zimmerman SA, Schultz WH, Burgett S, Mortier NA, Ware RE.
Hydroxyurea therapy lowers transcranial doppler flow velocities in children
with sickle cell anemia.Blood. 2007 Apr 11; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17429008&query_hl=12&itool=pubmed_DocSum
9: Thompson J, Reid M, Hambleton I, Serjeant GR. Albuminuria and renal function in homozygous sickle cell disease: observations
from a cohort study.Arch Intern Med. 2007 Apr 9;167(7):701-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17420429&query_hl=12&itool=pubmed_DocSum
10: Austin H, Key NS, Benson JM, Lally C, Dowling NF, Whitsett C, Hooper WC.
Sickle-cell trait and the risk of venous thromboembolism among African
Americans.Blood. 2007 Apr 4; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17409269&query_hl=12&itool=pubmed_DocSum
11: Citero VD, Levenson JL, McClish DK, Bovbjerg VE, Cole PL, Dahman BA,
Penberthy LT, Aisiku IP, Roseff SD, Smith WR. The role of catastrophizing in sickle cell disease - The PiSCES project.
Pain. 2007 Apr 2; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17408858&query_hl=12&itool=pubmed_DocSum
12: Fung EB, Harmatz P, Milet M, Ballas SK, De Castro L, Hagar W, Owen W,
Olivieri N, Smith-Whitley K, Darbari D, Wang W, Vichinsky E. Morbidity and mortality in chronically transfused subjects with thalassemia and
sickle cell disease: A report from the multi-center study of iron overload.
Am J Hematol. 2007 Apr;82(4):255-65. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17094096&query_hl=12&itool=pubmed_DocSum
13: Benton TD, Ifeagwu JA, Smith-Whitley K. Anxiety and Depression in Children and Adolescents with Sickle Cell Disease.
Curr Psychiatry Rep. 2007 Apr;9(2):114-121. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17389120&query_hl=12&itool=pubmed_DocSum
14: Givens M, Rutherford C, Joshi G, Delaney K. Impact of an emergency department pain management protocol on the pattern of
visits by patients with sickle cell disease.J Emerg Med. 2007 Apr;32(3):239-43. Epub 2007 Feb 7.
http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17394984&query_hl=12&itool=pubmed_DocSum
March 2007
Chakrabarti S, Bareford D. A survey on patient
perception of reduced-intensity transplantation in adults
with sickle cell disease. Bone Marrow Transplant. 2007 Mar 5; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17334383&query_hl=4&itool=pubmed_DocSum
Yallop D, Duncan ER, Norris E, Fuller GW, Thomas N, Walters J, Dick MC,Height SE, Thein SL, Rees DC. The associations between air quality and the number of hospital admissions for acute pain and sickle-cell disease in an urban environment.Br J Haematol. 2007 Mar;136(6):844-848. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17341271&query_hl=4&itool=pubmed_DocSum
Couillard S, Benkerrou M, Girot R, Brousse V, Ferster A,
Bader-Meunier B. Steroid treatment in children with sickle-cell disease.
Haematologica. 2007 Mar;92(3):425-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17339198&query_hl=4&itool=pubmed_DocSum
Pence L, Valrie CR, Gil KM, Redding-Lallinger R, Daeschner
C. Optimism Predicting Daily Pain Medication Use in Adolescents with
Sickle Cell
Disease.J Pain Symptom Manage. 2007 Mar;33(3):302-309. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17349499&query_hl=4&itool=pubmed_DocSum
McKie KT, Hanevold CD, Hernandez C, Waller JL, Ortiz L,
McKie KM. Prevalence, Prevention, and Treatment of Microalbuminuria and
Proteinuria in
Children With Sickle Cell Disease.J Pediatr Hematol Oncol. 2007
Mar;29(3):140-144. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17356390&query_hl=4&itool=pubmed_DocSum
Sylvester KP, Patey RA, Rafferty GF, Rees D, Thein SL, Greenough
A. Airway hyperresponsiveness and acute chest syndrome in children
with sickle
cell anemia. Pediatr Pulmonol. 2007 Mar;42(3):272-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17262858&query_hl=1&itool=pubmed_DocSum
Grassineau D, Papa K, Ducourneau A, Duboz P, Boetsch G, Chiaroni
J. Improving minority blood donation: anthropologic approach in a
migrant
community. Transfusion. 2007 Mar;47(3):402-9. PMID: 17319819 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17319819&query_hl=1&itool=pubmed_DocSum
Au WY, Leung WC. Challenges and pitfalls in prenatal screening in
pregnancies involving allogeneic stem cell transplantation recipients.
Bone Marrow Transplant. 2007 Feb 19; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17310136&query_hl=1&itool=pubmed_DocSum
February 2007
Kass NE, Medley AM, Natowicz MR, Hull SC, Faden RR, Plantinga L, Gostin LO. Access to health insurance: Experiences and attitudes of those with genetic versus non-genetic medical conditions. Am J Med Genet A. 2007 Feb 8; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17290434&query_hl=0&itool=pubmed_docsum
Frempong T, Pearson HA. Newborn screening coupled with comprehensive follow-up reduced early mortality of sickle cell disease in Connecticut. Conn Med. 2007 Jan;71(1):9-12. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17288099&query_hl=0&itool=pubmed_docsum
Serjeant GR, Higgs DR, Hambleton IR. Elderly survivors with homozygous sickle cell disease. N Engl J Med. 2007 Feb 8;356(6):642-3. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17287491&query_hl=0&itool=pubmed_docsum
Jacob E, Miaskowski C, Savedra M, Beyer JE, Treadwell M, Styles L. Quantification of analgesic use in children with sickle cell disease. Clin J Pain. 2007 Jan;23(1):8-14. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17277639&query_hl=0&itool=pubmed_docsum
Sachdev V, Machado RF, Shizukuda Y, Rao YN, Sidenko S, Ernst I, St Peter M, Coles WA, Rosing DR, Blackwelder WC, Castro O, Kato GJ, Gladwin MT. Diastolic dysfunction is an independent risk factor for death in patients with sickle cell disease. J Am Coll Cardiol. 2007 Jan 30;49(4):472-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17258093&query_hl=0&itool=pubmed_docsum
Joiner CH, Kirk Rettig R, Jiang M, Risinger M, Franco RS. Urea stimulation of KCl cotransport induces abnormal volume reduction in sickle reticulocytes.Blood. 2007 Feb 15;109(4):1728-35. Epub 2006 Oct 5. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17023583&query_hl=0&itool=pubmed_docsum
Miller ML, Gao G, Pestina T, Persons D, Tuomanen E. Hypersusceptibility to invasive pneumococcal infection in experimental sickle cell disease involves platelet-activating factor receptor.J Infect Dis. 2007 Feb 15;195(4):581-4. Epub 2007 Jan 8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17230418&query_hl=0&itool=pubmed_docsum
Koduri PR. Acute splenic sequestration crisis in adults with sickle cell anemia.Am J Hematol. 2007 Feb;82(2):174-5. No abstract available.
Hofmann M, de Montalembert M, Beauquier-Maccotta B, de Villartay P, Golse B. Posttraumatic stress disorder in children affected by sickle-cell disease and their parents.Am J Hematol. 2007 Feb;82(2):171-2. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16924639&query_hl=0&itool=pubmed_docsum
Vichinsky E, Onyekwere O, Porter J, Swerdlow P, Eckman J, Lane P, Files B, Hassell K, Kelly P, Wilson F, Bernaudin F, Forni GL, Okpala I, Ressayre-Djaffer C, Alberti D, Holland J, Marks P, Fung E, Fischer R, Mueller BU, Coates T; Deferasirox in Sickle Cell Investigators. A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease. Br J Haematol. 2007 Feb;136(3):501-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17233848&query_hl=0&itool=pubmed_docsum
Krishnamurti L. Hematopoietic cell transplantation for sickle cell disease: state of the art.Expert Opin Biol Ther. 2007 Feb;7(2):161-72. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17250455&query_hl=0&itool=pubmed_docsum
Sylvester KP, Patey RA, Broughton S, Rafferty GF, Rees D, Thein SL, Greenough A. Temporal relationship of asthma to acute chest syndrome in sickle cell disease. Pediatr Pulmonol. 2007 Feb;42(2):103-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17186507&query_hl=0&itool=pubmed_docsum
January 2007
Platt A, Eckman J. Diagnosing Anemia. Clinician Reviews 2006 Dec;16 (12):43 - 50 Full text online at http://www.clinicianreviews.com/index.asp?show=lesson&page=courses/105417/lesson.htm&lsn_id=105417
Moheeb H, Wali YA, El-Sayed MS. Physical fitness indices and
anthropometrics profiles in schoolchildren with sickle cell trait/disease.
Am J Hematol. 2007
Feb;82(2):91-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16986131&query_hl=1&itool=pubmed_DocSum
Sylvester KP, Patey RA, Broughton S, Rafferty GF, Rees D, Thein SL, Greenough A. Temporal relationship of asthma to acute chest syndrome in sickle cell disease. Pediatr Pulmonol. 2007 Feb;42(2):103-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17186507&query_hl=1&itool=pubmed_DocSum
Eggleston B, Patience M, Edwards S, Adamkiewicz T, Buchanan GR, Davies SC, Dickerhoff R, Donfield S, Feig SA, Giller RH, Haight A, Horan J, Hsu LL, Kamani N, Lane P, Levine JE, Margolis D, Moore TB, Ohene-Frempong K, Redding-Lallinger R, Roberts IA, Rogers ZR, Sanders JE, Scott JP, Sleight B, Thompson AA, Sullivan KM, Walters MC; for the Multicenter Study of HCT for SCA*. Effect of myeloablative bone marrow transplantation on growth in children with sickle cell anaemia: results of the multicenter study of haematopoietic cell transplantation for sickle cell anaemia. Br J Haematol. 2007 Jan 11; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17223910&query_hl=1&itool=pubmed_DocSum
Saleem S, Rice L. Limb amputation in hemoglobin SC disease
after application of ice and elevation.
Am J Hematol. 2007
Jan;82(1):53-4. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16929537&query_hl=1&itool=pubmed_DocSum
Kizito ME, Mworozi E, Ndugwa C, Serjeant GR. Bacteraemia in
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Quinn CT, Shull EP, Ahmad N, Lee NJ, Rogers ZR, Buchanan GR. Prognostic significance of early vaso-occlusive complications in children with sickle cell anemia. Blood. 2007 Jan 1;109(1):40-5. Epub 2006 Aug 29 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16940426&query_hl=1&itool=pubmed_DocSum
Varganov Y, Amosova O, Fresco JR. Third strand-mediated psoralen-induced correction of the sickle cell mutation on a plasmid transfected into COS-7 cells. Gene Ther. 2007 Jan;14(2):173-9. Epub 2006 Aug 31 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16943853&query_hl=1&itool=pubmed_DocSum
Monchanin G, Serpero LD, Connes P, Tripette J, Wouassi D, Bezin L, Francina A, Ngongang J, de la Pena M, Massarelli R, Gozal D, Thiriet P, Martin C. Effects of progressive and maximal exercise on plasma levels of adhesion molecules in athletes with sickle cell trait with or without {alpha}-thalassemia. J Appl Physiol. 2007 Jan;102(1):169-173. Epub 2006 Aug 10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16902065&query_hl=1&itool=pubmed_DocSum
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December 2006
Sara Day, RN, MSN; and Elisabeth Chismark, RN, MSN The Cognitive and Academic Impact Of Sickle Cell Disease The Journal of School Nursing December 2006 Volume 22, Number 6 Full Text PDF
Neumayr LD, Aguilar C, Earles AN, Jergesen HE, Haberkern CM, Kammen BF, Nancarrow PA, Padua E, Milet M, Stulberg BN, Williams RA, Orringer EP, Graber N, Robertson SM, Vichinsky EP. Physical therapy alone compared with core decompression and physical therapy for femoral head osteonecrosis in sickle cell disease. Results of a multicenter study at a mean of three years after treatment. J Bone Joint Surg Am. 2006 Dec;88(12):2573-82. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17142406&query_hl=1&itool=pubmed_docsum
Hibbert JM, Creary MS, Gee BE, Buchanan ID, Quarshie A, Hsu LL. Erythropoiesis and myocardial energy requirements contribute to the hypermetabolism of childhood sickle cell anemia. J Pediatr Gastroenterol Nutr. 2006 Nov;43(5):680-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17130748&query_hl=1&itool=pubmed_docsum
Burnett AL, Bivalacqua TJ, Champion HC, Musicki B Feasibility of the use of phosphodiesterase type 5 inhibitors in a pharmacologic prevention program for recurrent priapism. J Sex Med. 2006 Nov;3(6):1077-84. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17100941&query_hl=1&itool=pubmed_DocSum
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Ataga KI, Orringer EP, Styles L, Vichinsky EP, Swerdlow P, Davis GA, Desimone
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Morris CR, Singer ST, Walters MC. Clinical hemoglobinopathies: iron, lungs and new blood. Curr Opin Hematol. 2006 Nov;13(6):407-418. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17053452&query_hl=4&itool=pubmed_DocSum
Mehta SH, Adams RJ. Treatment and prevention of stroke in children with sickle cell disease. Curr Treat Options Neurol. 2006 Nov;8(6):503-12. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17032571&query_hl=4&itool=pubmed_DocSum
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Mason P. Sickle cell disease in the perioperative setting. J Perioper Pract. 2006 Sep;16(9):443-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17001937&query_hl=2&itool=pubmed_docsum
Stein PD, Beemath A, Meyers FA, Skaf E, Olson RE. Deep venous thrombosis and pulmonary embolism in hospitalized patients with sickle cell disease. Am J Med. 2006 Oct;119(10):897.e7-11. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17000225&query_hl=2&itool=pubmed_docsum
Raj AB, O'brien LM, Bertolone SJ, Gozal D, Edmonds HL Jr. Cerebral oximetry improves detection of sickle cell patients at risk for nocturnal cerebral hypoxia. Pediatr Pulmonol. 2006 Sep 22;41(11):1088-1094 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16998929&query_hl=2&itool=pubmed_docsum
Shankar SM, Arbogast PG, Mitchel E, Ding H, Wang WC, Griffin MR. Impact of proximity to comprehensive sickle cell center on utilization of healthcare services among children with sickle cell disease. Pediatr Blood Cancer. 2006 Sep 22; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16998856&query_hl=2&itool=pubmed_docsum
Moheeb H, Wali YA, El-Sayed MS. Physical fitness indices and anthropometrics profiles in schoolchildren with sickle cell trait/disease. Am J Hematol. 2006 Sep 19; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16986131&query_hl=2&itool=pubmed_docsum
Chulamokha L, Scholand SJ, Riggio JM, Ballas SK, Horn D, Desimone JA. Bloodstream infections in hospitalized adults with sickle cell disease: A retrospective analysis. Am J Hematol. 2006 Oct;81(10):723-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16795063&query_hl=12&itool=pubmed_docsum
Raffini LJ, Niebanck AE, Hrusovsky J, Stevens A, Blackwood-Chirchir A, Ohene-Frempong K, Kwiatkowski JL. Prolongation of the prothrombin time and activated partial thromboplastin time in children with sickle cell disease. Pediatr Blood Cancer. 2006 Oct 15;47(5):589-93. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16123995&query_hl=14&itool=pubmed_docsum
September 2006
Kaye CI. Newborn screening fact sheets. Pediatrics. 2006 Sep;118(3):e934-63. Full Text at http://pediatrics.aappublications.org/cgi/content/full/118/3/1304
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