[Banner Image]

[Home][What's New][Products & Services][Contents][Feedback][Search]

 Sickle Cell Medical Articles[Dividing Line Image]

Articles in the Medical Literature

See NLM- Medline articles about sickle cell disease for the past 6 months

February 2010

Increased levels of the inflammatory biomarker C-reactive protein at baseline are associated with childhood sickle cell vasocclusive crises.

Krishnan S, Setty Y, Betal SG, Vijender V, Rao K, Dampier C, Stuart M.

Br J Haematol. 2009 Dec 8.

.

Sickle cell disease at the dawn of the molecular era.

 

Abboud MR, Musallam KM.

 

Hemoglobin. 2009;33 Suppl 1:S93-S106.

 

.

Pathophysiology of transfusional iron overload: contrasting patterns in thalassemia major and sickle cell disease.

 

Porter JB.

 

Hemoglobin. 2009;33 Suppl 1:S37-45.

 

 

Steps toward the prevention of hemoglobinopathies in the kingdom of saudi arabia.

 

Al-Shahrani M.

 

Hemoglobin. 2009;33 Suppl 1:S21-4.

 

.

Prevention of hemoglobinopathies in egypt.

 

El-Beshlawy A, Youssry I.

 

Hemoglobin. 2009;33 Suppl 1:S14-20.

 

.

Current understanding in the management of sickle cell disease.

 

Inati A, Chabtini L, Mounayar M, Taher A.

 

Hemoglobin. 2009;33 Suppl 1:S107-15.

 

.

Hydroxyurea for children with sickle cell disease.

 

Heeney MM, Ware RE.

 

Hematol Oncol Clin North Am. 2010 Feb;24(1):199-214.

 

.

Effects of a single sickling event on the mechanical fragility of sickle cell trait erythrocytes.

 

Presley TD, Perlegas AS, Bain LE, Ballas SK, Nichols JS, Sabio H, Gladwin MT, Kato GJ, Kim-Shapiro DB.

 

Hemoglobin. 2010;34(1):24-36.

 

.

Hemoglobinopathies in North Africa: a review.

 

Haj Khelil A, Denden S, Leban N, Daimi H, Lakhdhar R, Lefranc G, Ben Chibani J, Perrin P.

 

Hemoglobin. 2010;34(1):1-23.

 

.

Burden of influenza-related hospitalizations among children with sickle cell disease.

 

Bundy DG, Strouse JJ, Casella JF, Miller MR.

 

Pediatrics. 2010 Feb;125(2):234-43. Epub 2010 Jan 25.

 

.

Blood transfusions for treating acute chest syndrome in people with sickle cell disease.

 

Alhashimi D, Fedorowicz Z, Alhashimi F, Dastgiri S.

 

Cochrane Database Syst Rev. 2010 Jan 20;(1):CD007843.

 

.

Drugs for preventing red blood cell dehydration in people with sickle cell disease.

 

Nagalla S, Ballas SK.

 

Cochrane Database Syst Rev. 2010 Jan 20;(1):CD003426. Review.

 
January 2010

Pain, coping and health care utilization in younger and older adults with sickle cell disease.

Sanders KA, Labott SM, Molokie R, Shelby SR, Desimone JJ   Health Psychol. 2010 Jan;15(1):131-7

Acute human parvovirus B19 infection and nephrotic syndrome in patients with sickle cell disease.

Quek L, Sharpe C, Dutt N, Height S, Allman M, Awogbade M, Rees DC, Zuckerman M, Thein SL.Br J Haematol. 2010 Jan 7

High Prevalence of Sickle Cell Trait in African Americans with ESRD.

Derebail VK, Nachman PH, Key NS, Ansede H, Falk RJ, Kshirsagar AV.J Am Soc Nephrol. 2010 Jan 7.

The HDAC inhibitors trichostatin A and suberoylanilide hydroxamic acid exhibit multiple modalities of benefit for the vascular pathobiology of sickle transgenic mice.

Hebbel RP, Vercellotti GM, Pace BS, Solovey AN, Kollander R, Abanonu CF, Nguyen J, Vineyard JV, Belcher JD, Abdulla F, Osifuye S, Eaton JW, Kelm RJ Jr, Slungaard A.

Blood. 2010 Jan 6

Delayed Hemolytic Transfusion Reaction in Sickle Cell Disease.

Scheunemann LP, Ataga KI. Am J Med Sci. 2009 Dec 31.

Inpatient use of laxatives during opioid administration in children with sickle cell disease.

O'Brien SH, Fan L, Kelleher KJ. Pediatr Blood Cancer. 2010 Jan 4.

Respiratory symptoms and acute painful episodes in sickle cell disease.

Jacob E, Sockrider MM, Dinu M, Acosta M, Mueller BU.J Pediatr Oncol Nurs. 2010 Jan-Feb;27(1):33-9.

Placenta growth factor in sickle cell disease: association with hemolysis and inflammation.

Brittain JE, Hulkower B, Jones SK, Strayhorn D, De Castro L, Telen MJ, Orringer EP, Hinderliter A, Ataga KI.

Blood. 2009 Dec 29.

Genetic modifiers of the severity of sickle cell anemia identified through a genome-wide association study.

Sebastiani P, Solovieff N, Hartley SW, Milton JN, Riva A, Dworkis DA, Melista E, Klings ES, Garrett ME, Telen MJ, Ashley-Koch A, Baldwin CT, Steinberg MH.

Am J Hematol. 2010 Jan;85(1):29-35.

Cardiopulmonary complications leading to premature deaths in adult patients with sickle cell disease.

Fitzhugh CD, Lauder N, Jonassaint JC, Telen MJ, Zhao X, Wright EC, Gilliam FR, De Castro LM.

Am J Hematol. 2010 Jan;85(1):36-40.PMID: 20029950

Open heart surgery in patients with sickle cell hemoglobinopathy.

Yousafzai SM, Ugurlucan M, Al Radhwan OA, Al Otaibi AL, Canver CC. Circulation. 2010 Jan 5;121(1):14-9.

Relationships between Somatic Growth and Cognitive Functioning in Young Children with Sickle Cell Disease.

Puffer ES, Schatz JC, Roberts CW.J Pediatr Psychol. 2009 Dec 21.

December 2009

American Society of Hematology (ASH) meeting was held December 5 - 8, 2009 in New Orleans. There were over 130 abstracts published related to sickle cell disease showing the robust research efforts world wide by the hematology community. All the sickle cell related abstracts can be viewed at  http://ash.confex.com/ash/2009/webprogram/start.html#srch=words|sickle|method|and|pge|1   A selection of some of the titles and links are:

Safety and Efficacy of Sildenafil Therapy for Doppler-Defined Pulmonary Hypertension in Patients with Sickle Cell Disease: Preliminary Results of the Walk-PHaSST Clinical Trial http://ash.confex.com/ash/2009/webprogram/Paper24394.html

Elevated Systolic Blood Pressure and Low Fetal Hemoglobin Are Risk Factors for Silent Cerebral Infarcts in Children with Sickle Cell Anemia http://ash.confex.com/ash/2009/webprogram/Paper24452.html

Development of a Decision Support Tool to Guide Management of Adults with Sickle Cell Disease: The Emergency Department Sickle Cell Assessment of Strengths and Needs (ED-SCANS) http://ash.confex.com/ash/2009/webprogram/Paper22716.html

Sickle Cell Leg Ulcers Are Associated with Hyperuricemia, Hemolysis, Pulmonary Hypertension and Death  http://ash.confex.com/ash/2009/webprogram/Paper19572.html

Neuropathic Vs. Nociceptive Pain in Adolescent Sickle Cell Disease (SCD) Evaluated by a Computer-Based Self-Assessment Pain Tool http://ash.confex.com/ash/2009/webprogram/Paper25367.html

The Number of People with Sickle Cell Disease in the United States: National and Individual State Estimates http://ash.confex.com/ash/2009/webprogram/Paper17835.html

Emergency Department Follow-up for Adults with Sickle Cell Disease http://ash.confex.com/ash/2009/webprogram/Paper22777.html

Arginine Therapy for Vaso-Occlusive Pain Episodes in Sickle Cell Disease http://ash.confex.com/ash/2009/webprogram/Paper21015.html

Morphine Pharmacokinetics in Sickle Cell Disease: Implications for Pain Management http://ash.confex.com/ash/2009/webprogram/Paper22904.html

Hydroxyurea in Children with Sickle Cell Disease:  Practice Patterns and Barriers to Utilization http://ash.confex.com/ash/2009/webprogram/Paper18831.html

Increased Severity of Pandemic H1N1 Influenza in Children and Young Adults with Sickle Cell Disease http://ash.confex.com/ash/2009/webprogram/Paper24266.html

NT-Pro Brain Natriuretic Peptide Levels and the Risk of Stroke and Death in the Cooperative Study of Sickle Cell Disease http://ash.confex.com/ash/2009/webprogram/Paper24868.html

Health Care Disparities in Sickle Cell Disease : A Population-Based Study of Los Angeles County http://ash.confex.com/ash/2009/webprogram/Paper18061.html

National Burden of Emergency Department Care for Sickle Disease: Impact of Age, Insurance Status, Income, Hospital Type and Location On Subsequent Hospital Admission  http://ash.confex.com/ash/2009/webprogram/Paper25506.html

Definition of the Responder to Hydroxyurea Therapy: Revisited http://ash.confex.com/ash/2009/webprogram/Paper18381.html

November 2009
Walter PB, Harmatz P, Vichinsky E. Iron metabolism and iron chelation in sickle cell disease. 
Acta Haematol. 2009;122(2-3):174-83. Epub 2009 Nov 10.
 This review highlights recent advances in iron metabolism that are relevant to
sickle cell disease (SCD). SCD is a common hemoglobinopathy that results in
chronic inflammation. Improved understanding of how iron metabolism is controlled
by proteins such as hepcidin, ferroportin, hypoxia-inducible factor 1, and growth
differentiation factor 15 have revealed how they are involved in the organ
toxicity of SCD. SCD patients have lower levels of non-transferrin-bound iron
(NTBI) relative to other hemoglobinopathies, such as thalassemia. Care for SCD
now commonly uses transfusion that results in iron overload and necessitates the 
need for chelation. New oral chelation therapy using deferasirox (Exjade/ICL670) 
appears to be safe and may even lower the amount of toxic free NTBI and enhance
patient compliance. Finally, we suggest that iron metabolism and trafficking is
different in SCD compared to other hemoglobinopathies. The high levels of
inflammatory cytokines in SCD may enhance macrophage/reticuloendothelial cell
iron and/or renal cell iron retention. This makes the tissues that retain iron
different in SCD, and thus the organs that fail in SCD are different from those
of other hemoglobinopathies, such as the cardiomyopathy or endocrinopathies of
thalassemia. Copyright 2009 S. Karger AG, Basel. 
 
Cappellini MD, Taher A. Deferasirox (Exjade) for the treatment of iron overload.
Acta Haematol. 2009;122(2-3):165-73. Epub 2009 Nov 10.
 Deferasirox is a once-daily oral iron chelator with established dose-dependent
efficacy in both adult and pediatric patients with transfusional iron overload.
The clinical development program has demonstrated the efficacy of deferasirox for
up to 4.5 years of treatment in patients with various underlying anemias,
including beta-thalassemia, myelodysplastic syndromes, sickle cell disease,
aplastic anemia, and other rare anemias. In addition to reducing key indicators
of total body iron levels (serum ferritin, liver iron concentration, and toxic
labile plasma iron), deferasirox has also demonstrated the ability to remove
cardiac iron and prevent future cardiac iron accumulation. Emerging long-term
data confirm the tolerability profile of deferasirox, and data on patient
compliance render deferasirox a suitable therapeutic option for patients with
chronic conditions requiring ongoing iron chelation therapy. Data continue to
accumulate in a wide range of patient groups, including those with
non-transfusion-dependent anemias such as hereditary hemochromatosis. 
 
Voskaridou E, Christoulas D, Bilalis A, Plata E, Varvagiannis K, Stamatopoulos G,
Sinopoulou K, Balassopoulou A, Loukopoulos D, Terpos E.
The effect of prolonged administration of hydroxyurea on morbidity and mortality 
in adult patients with sickle-cell syndromes: results of a 17-year, single center
trial (LaSHS).  Blood. 2009 Nov 10.  
The aim of this prospective study was to evaluate the long-term efficacy and
safety of hydroxyurea (HU) in sickle-cell disease (SCD). Thirty-four patients
with sickle-cell anemia (HbS/HbS), 131 with HbS/beta(0)-thal and 165 with
HbS/beta(+)-thal were participated into this trial. HU was given to 131 patients,
while 199 patients were conventionally treated. The median follow-up period was 8
years for HU patients and 5 years for non-HU patients. HU produced a dramatic
reduction of the frequency of severe painful crises, transfusion requirements,
hospital admissions, and incidence of acute chest syndrome. The probability of
10-year survival was 86% and 65% for HU and non-HU patients, respectively
(p=0.001), although HU patients had more severe form of SCD. The 10-year
probability of survival for HbS/HbS, HbS/beta(0)-thal, and HbS/IVSI-110 patients 
was 100%, 87% and 82%, respectively for HU patients and 10%, 54% and 66%, for
non-HU patients. The multivariate analysis showed that HbF values at baseline and
percentage change of LDH between baseline and 6-month were independently
predicted for survival in the HU group. These results highlight the beneficial
effect of HU which seems to modify the natural history of SCD and raise the issue
of expanding its use in all SCD patients.
 
 
Ballas SK, Lieff S, Benjamin LJ, Dampier CD, Heeney MM, Hoppe C, Johnson CS,
Rogers ZR, Smith-Whitley K, Wang WC, Telen MJ; on Behalf of the Investigators at 
the Comprehensive Sickle Cell Centers. Definitions of the phenotypic manifestations of sickle cell disease.  Am J Hematol. 2009 Sep 24. 
 
Sickle cell disease (SCD) is a pleiotropic genetic disorder of hemoglobin that
has profound multiorgan effects. The low prevalence of SCD ( approximately
100,000/US) has limited progress in clinical, basic, and translational research. 
Lack of a large, readily accessible population for clinical studies has
contributed to the absence of standard definitions and diagnostic criteria for
the numerous complications of SCD and inadequate understanding of SCD
pathophysiology. In 2005, the Comprehensive Sickle Cell Centers initiated a
project to establish consensus definitions of the most frequently occurring
complications. A group of clinicians and scientists with extensive expertise in
research and treatment of SCD gathered to identify and categorize the most common
complications. From this group, a formal writing team was formed that further
reviewed the literature, sought specialist input, and produced definitions in a
standard format. This article provides an overview of the process and describes
12 body system categories and the most prevalent or severe complications within
these categories. A detailed Appendix provides standardized definitions for all
complications identified within each system. This report proposes use of these
definitions for studies of SCD complications, so future studies can be comparably
robust and treatment efficacy measured. Use of these definitions will support
greater accuracy in genotype-phenotype studies, thereby achieving a better
understanding of SCD pathophysiology. This should nevertheless be viewed as a
dynamic rather than final document; phenotype descriptions should be reevaluated 
and revised periodically to provide the most current standard definitions as
etiologic factors are better understood, and new diagnostic options are
developed. Am. J. Hematol. 2009. (c) 2009 Wiley-Liss, Inc.
 
Makani JK, Komba AN, Cox SE, Oruo J, Mwamtemi K, Kitundu J, Magesa P, Rwezaula S,
Meda E, Mgaya J, Pallangyo K, Okiro E, Muturi D, Newton CR, Fegan G, Marsh K,
Williams TN.Malaria in patients with sickle cell anemia: burden, risk factors and outcome at 
outpatient clinic and during hospitalization. Blood. 2009 Nov 9. 
 
Approximately 280,000 children are born with sickle cell anemia (SCA) in Africa
annually yet few survive beyond childhood. Falciparum malaria is considered a
significant cause of this mortality. We conducted a 5-year prospective
surveillance study for malaria parasitemia, clinical malaria and severe malarial 
anemia (SMA) in Dar-es-Salaam, Tanzania between 2004 and 2009. We recorded 10,491
visits to the outpatient clinic among 1,808 patients with SCA and 773 visits
among 679 patients without SCA. Similarly, we recorded 691 hospital admissions
among 497 patients with SCA and 2,017 in non-SCA patients. Overall, the
prevalence of parasitemia was lower in SCA than in non-SCA patients both at
clinic (0.7% versus 1.6%; OR 0.53, 95% confidence interval 0.32-0.86; p=0.008)
and during hospitalization (3.0% versus 5.6%; 0.46; 0.25-0.94; 0.01).
Furthermore, SCA patients had higher rates of malaria during hospitalization than
at clinic, the ORs being 4.29 (2.63-7.01; p<0.001) for parasitemia, 17.66
(5.92-52.71; p<0.001) for clinical malaria, and 21.11 (8.46-52.67; p<0.001) for
SMA respectively. Although malaria was rare among patients with SCA, parasitemia 
during hospitalization was associated with both severe anemia and death.
Effective treatment for malaria during severe illness episodes and further
studies to determine the role chemoprophylaxis are required.
 
 
Asare K, Gee BE, Stiles JK, Wilson NO, Driss A, Quarshie A, Adams RJ, Kutlar A,
Hibbert JM. Plasma interleukin-1beta concentration is associated with stroke in sickle cell
disease. Cytokine. 2009 Nov 7.
 
The pathogenesis of sickle cell disease (HbSS), which has numerous complications 
including stroke, involves inflammation resulting in alteration of plasma
inflammatory protein concentration. We investigated HbSS children with abnormal
cerebral blood flow detected by trans-cranial Doppler ultrasound (TCD) who
participated in the multi-center stroke prevention (STOP) study, to determine if 
plasma inflammatory protein concentration is associated with the outcome of
stroke. Thirty-nine plasma samples from HbSS participants with elevated TCD who
had no stroke, HbSS-NS (n=13) or had stroke, HbSS-S (n=13), HbSS steady-state
controls (n=7) and controls with normal hemoglobin, HbAA (n=6), were analyzed
simultaneously for 27 circulating inflammatory proteins. Logistic regression and 
receiver operating characteristics curve analysis of stroke on plasma
inflammatory mediator concentration, adjusted for age and gender, demonstrated
that interleukin-1beta (IL-1beta) was protective against stroke development
(HbSS-NS=19, 17-23, HbSS-S=17, 16-19pg/mL, median and 25th-75th percentile; odds 
ratio=0.59, C.I.=0.36-0.96) and was a good predictor of stroke (area under
curve=0.852). This result demonstrates a strong association of systemic
inflammation with stroke development in HbSS via moderately increased plasma
IL-1beta concentration, which is furthermore associated with a decreased
likelihood of stroke in HbSS.
 
 
Doulton DM. Cradle to Commencement: Transitioning Adolescents With Sickle Cell Disease to
Adult Providers. J Pediatr Oncol Nurs. 2009 Nov 6.
 
Children with sickle cell disease (SCD) are surviving past childhood and well
into adulthood. Concerns are raised as to who is going to care for these children
as they reach adulthood. We have developed a 2-part transition program. We have
transitioned 20 of our 18- to 27-year-old patients to adult providers recognizing
that early preparation is essential. At the newborn's initial visit or transfer
from another clinic the transition program is explained to the family. At age 13 
years, all our patients are given a "Preparation for Transition" binder. This
binder is reviewed in detail with the patient and parent on a regular basis. At
18 years of age, coordinating with the milestone of graduating from high school
and depending on developmental age, the transition is completed. The goal is a
continuum of care in the transition process.
 
McPherson ME, Anderson AR, Castillejo MI, Hillyer CD, Bray RA, Gebel HM,
Josephson CD.HLA alloimmunization is associated with RBC antibodies in multiply transfused
patients with sickle cell disease. Pediatr Blood Cancer. 2009 Nov 3.
 
BACKGROUND: Alloimmunization to minor red blood cell (RBC) antigens occurs
commonly in sickle cell disease (SCD). Patients with alloimmunization demonstrate
increased risk for new alloantibody formation with subsequent transfusion.
Alloimmunization to human leukocyte antigens (HLA) can occur with RBC transfusion
and may result in graft rejection during stem cell or organ transplantation. The 
prevalence and risk factors for HLA alloimmunization in multiply transfused
pediatric SCD patients are unknown. PROCEDURE: A cross-sectional study of HLA
alloimmunization in SCD patients aged 3-21 years with a history of >/=3 RBC
transfusions was performed to test the hypothesis that HLA alloimmunization is
associated with RBC alloimmunization. Antibodies to class I and class II HLA were
measured by Flow Panel Reactive Antibody (FlowPRA(R)). RESULTS: Seventy-three SCD
patients (30 with RBC antibodies) were tested. HLA antibodies were detected in
25/73 (34%) patients; class I HLA antibodies occurred in 24/73 (33%) and class II
HLA antibodies occurred in 3 (4%). Among patients with RBC antibodies, 16/30
(53%) had HLA antibodies, while 9/43 (21%) patients without RBC antibodies had
HLA antibodies (OR 4.32 [1.6-12.1]). In a multivariate analysis, antibodies to
RBC antigens were an independent predictor of HLA alloimmunization (P = 0.041).
The association of RBC and HLA immunization was strongest among patients with no 
history of chronic transfusion therapy. CONCLUSIONS: This analysis is the first
description of HLA alloimmunization in pediatric SCD patients who receive
primarily leukoreduced RBC transfusions and demonstrates that HLA
alloimmunization tendency is associated with antibodies to RBC antigens. Pediatr 
Blood Cancer. (c) 2009 Wiley-Liss, Inc.
 
October 2009
Velasquez MP, Mariscalco MM, Goldstein SL, Airewele GE. Erythrocytapheresis in
children with sickle cell disease and acute chest syndrome. Pediatr Blood Cancer.
2009 Dec;53(6):1060-3. http://www.ncbi.nlm.nih.gov/pubmed/19637317?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Smith WR, Bauserman RL, Ballas SK, McCarthy WF, Steinberg MH, Swerdlow PS,
Waclawiw MA, Barton BA; The Investigators of the Multicenter Study of Hydroxyurea
in Sickle Cell Anemia. Climatic and geographic temporal patterns of pain in the
Multicenter Study of Hydroxyurea. Pain. 2009 Nov;146(1-2):91-98. http://www.ncbi.nlm.nih.gov/pubmed/19683393?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Thein SL, Menzel S, Lathrop M, Garner C. Control of fetal hemoglobin: new
insights emerging from genomics and clinical implications. Hum Mol Genet. 2009
Oct 15;18(R2):R216-23. PubMed PMID: 19808799; http://www.ncbi.nlm.nih.gov/pubmed/19808799?ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Walters MC, Hardy K, Edwards S, Adamkiewicz T, Barkovich J, Bernaudin F,
Buchanan GR, Bunin N, Dickerhoff R, Giller R, Haut PR, Horan J, Hsu LL, Kamani N,
Levine JE, Margolis D, Ohene-Frempong K, Patience M, Redding-Lallinger R, Roberts
IA, Rogers ZR, Sanders JE, Scott JP, Sullivan KM. Pulmonary, Gonadal and Central 
Nervous System Status after Bone Marrow Transplantation for Sickle Cell Disease. 
Biol Blood Marrow Transplant. 2009 Oct 9. http://www.ncbi.nlm.nih.gov/pubmed/19822218?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Buchanan G, Vichinsky E, Krishnamurti L, Shenoy S. Severe sickle cell disease 
- pathophysiology and therapy. Biol Blood Marrow Transplant. 2009 Oct 8. http://www.ncbi.nlm.nih.gov/pubmed/19819341?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
van Beers EJ, Schaap MC, Berckmans RJ, Nieuwland R, Sturk A, van Doormaal FF, 
Meijers JC, Biemond BJ; on behalf of the CURAMA study group*. Circulating
erythrocyte-derived microparticles are associated with coagulation activation in 
sickle cell disease. Haematologica. 2009 Oct 8. http://www.ncbi.nlm.nih.gov/pubmed/19815831?ordinalpos=15&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Odey F, Okomo U, Oyo-Ita A. Vaccines for preventing invasive salmonella
infections in people with sickle cell disease. Cochrane Database Syst Rev. 2009
Oct 7;(4):CD006975. http://www.ncbi.nlm.nih.gov/pubmed/19821392?ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Miller FA, Paynter M, Hayeems RZ, Little J, Carroll JC, Wilson BJ, Allanson J,
Bytautas JP, Chakraborty P. Understanding sickle cell carrier status identified
through newborn screening: a qualitative study. Eur J Hum Genet. 2009 Oct 7.
http://www.ncbi.nlm.nih.gov/pubmed/19809482?ordinalpos=18&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Pavlakis SG, Rees RC, Huang X, Brown RC, Casella JF, Iyer RV, Kalpatthi R,
Luden J, Miller ST, Rogers ZR, Thornburg CD, Wang WC, Adams RJ; for the BABY HUG 
Investigators. Transcranial doppler ultrasonography (TCD) in infants with sickle 
cell anemia: Baseline data from the BABY HUG trial. Pediatr Blood Cancer. 2009
Oct 7. http://www.ncbi.nlm.nih.gov/pubmed/19813252?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Dowling MM, Quinn CT, Rogers ZR, Buchanan GR. Acute silent cerebral
infarction in children with sickle cell anemia. Pediatr Blood Cancer. 2009 Oct 7.
http://www.ncbi.nlm.nih.gov/pubmed/19813251?ordinalpos=20&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Roberts L, O'Driscoll S, Dick MC, Height SE, Deane C, Goss DE, Pohl K, Rees
DC. Stroke prevention in the young child with sickle cell anaemia. Ann Hematol.
2009 Oct;88(10):943-6. http://www.ncbi.nlm.nih.gov/pubmed/19455330?ordinalpos=27&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 
Verduzco LA, Nathan DG. Sickle cell disease and stroke. Blood. 2009 Oct 1.
http://www.ncbi.nlm.nih.gov/pubmed/19797523?ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
September 2009

Abern MR, Levine LA. Ketoconazole and prednisone to prevent recurrent ischemic priapism. J Urol. 2009 Oct;182(4):1401-6. Epub 2009 Aug 15. http://www.ncbi.nlm.nih.gov/pubmed/19683289?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Rhodes M, Akohoue SA, Shankar SM, Fleming I, Qi An A, Yu C, Acra S, Buchowski  MS. Growth patterns in children with sickle cell anemia during puberty. Pediatr Blood Cancer. 2009 Oct;53(4):635-41. http://www.ncbi.nlm.nih.gov/pubmed/19544390?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Mvundura M, Amendah D, Kavanagh PL, Sprinz PG, Grosse SD. Health care utilization and expenditures for privately and publicly insured children with sickle cell disease in the United States. Pediatr Blood Cancer. 2009 Oct;53(4):642-6. http://www.ncbi.nlm.nih.gov/pubmed/19492318?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Alvarez O, Rodriguez-Cortes H, Robinson N, Lewis N, Pow Sang CD, Lopez-Mitnik  G, Paley C. Adherence to Deferasirox in Children and Adolescents With Sickle Cell Disease During 1-year of Therapy. J Pediatr Hematol Oncol. 2009 Sep 3. http://www.ncbi.nlm.nih.gov/pubmed/19734806?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Thompson BW, Miller ST, Rogers ZR, Rees RC, Ware RE, Waclawiw MA, Iyer RV, Casella JF, Luchtman-Jones L, Rana S, Thornburg CD, Kalpatthi RV, Barredo JC, Brown RC, Sarnaik S, Howard TH, Luck L, Wang WC. The pediatric hydroxyurea phase  III clinical trial (BABY HUG): Challenges of study design. Pediatr Blood Cancer.  2009 Sep 3. http://www.ncbi.nlm.nih.gov/pubmed/19731330?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Hijmans CT, Grootenhuis MA, Oosterlaan J, Last BF, Heijboer H, Peters M, Fijnvandraat K. Behavioral and emotional problems in children with sickle cell disease and healthy siblings: Multiple informants, multiple measures. Pediatr Blood Cancer. 2009 Sep 3. http://www.ncbi.nlm.nih.gov/pubmed/19731327?ordinalpos=15&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Dham N, Ensing G, Minniti C, Campbell A, Arteta M, Rana S, Darbari D, Nouraie  M, Onyekwere O, Lasota M, Kato GJ, Gladwin MT, Castro O, Gordeuk V, Sable C. Prospective echocardiography assessment of pulmonary hypertension and its potential etiologies in children with sickle cell disease. Am J Cardiol. 2009 Sep 1;104(5):713-20. http://www.ncbi.nlm.nih.gov/pubmed/19699350?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Rogovik AL, Li Y, Kirby MA, Friedman JN, Goldman RD. Admission and length of  stay due to painful vasoocclusive crisis in children. Am J Emerg Med. 2009 Sep;27(7):797-801 http://www.ncbi.nlm.nih.gov/pubmed/19683107?ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Strouse JJ, Jordan LC, Lanzkron S, Casella JF. The excess burden of stroke in hospitalized adults with sickle cell disease. Am J Hematol. 2009 Sep;84(9):548-52. http://www.ncbi.nlm.nih.gov/pubmed/19623672?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Hardie R, King L, Fraser R, Reid M. Prevalence of pneumococcal polysaccharide vaccine administration and incidence of invasive pneumococcal disease in children in Jamaica aged over 4 years with sickle cell disease diagnosed by newborn screening. Ann Trop Paediatr. 2009 Sep;29(3):197-202. http://www.ncbi.nlm.nih.gov/pubmed/19689861?ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Shaz BH, Demmons DG, Hillyer KL, Jones RE, Hillyer CD. Racial differences in  motivators and barriers to blood donation among blood donors. Arch Pathol LabMed. 2009 Sep;133(9):1444-7 http://www.ncbi.nlm.nih.gov/pubmed/19722753?ordinalpos=24&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Sadarangani M, Makani J, Komba AN, Ajala-Agbo T, Newton CR, Marsh K, Williams TN. An observational study of children with sickle cell disease in Kilifi, Kenya. Br J Haematol. 2009 Sep;146(6):675-82. http://www.ncbi.nlm.nih.gov/pubmed/19650883?ordinalpos=27&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Subbannan K, Ustun C, Natarajan K, Clair B, Daitch L, Fields S, Kutlar F, Kutlar A. Acute splenic complications and implications of splenectomy in hemoglobin SC disease. Eur J Haematol. 2009 Sep;83(3):258-60. http://www.ncbi.nlm.nih.gov/pubmed/19459924?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 McClish DK, Smith WR, Dahman BA, Levenson JL, Roberts JD, Penberthy LT, Aisiku IP, Roseff SD, Bovbjerg VE. Pain site frequency and location in sickle cell disease: the PiSCES project. Pain. 2009 Sep;145(1-2):246-51 http://www.ncbi.nlm.nih.gov/pubmed/19631468?ordinalpos=37&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

  Lieberman L, Kirby M, Ozolins L, Mosko J, Friedman J. Initial presentation of unscreened children with sickle cell disease: the Toronto experience. Pediatr Blood Cancer. 2009 Sep;53(3):397-400. http://www.ncbi.nlm.nih.gov/pubmed/19405139?ordinalpos=40&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 McPherson ME, Anderson AR, Haight AE, Jessup P, Castillejo MI, Hillyer CD, Josephson CD. Transfusion management of sickle cell patients during bone marrow transplantation with matched sibling donor. Transfusion. 2009 Sep;49(9):1977-86.  http://www.ncbi.nlm.nih.gov/pubmed/19453984?ordinalpos=45&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Adamkiewicz TV, Abboud MR, Paley C, Olivieri N, Kirby-Allen M, Vichinsky E, Casella JF, Alvarez OA, Barredo JC, Lee MT, Iyer RV, Kutlar A, McKie KM, McKie V, Odo N, Gee B, Kwiatkowski JL, Woods GM, Coates T, Wang W, Adams RJ. Serum ferritin level changes in children with sickle cell disease on chronic blood transfusion are non-linear, and are associated with iron load and liver injury. Blood. 2009 Aug 31. http://www.ncbi.nlm.nih.gov/pubmed/19721013?ordinalpos=47&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Bartolucci P, El Murr T, Roudot-Thoraval F, Habibi A, Santin A, Renaud B, Noel V, Michel M, Bachir D, Galacteros F, Godeau B. A randomized, controlled clinical trial of ketoprofen for sickle-cell disease vaso-occlusive crises in adults. Blood. 2009 Aug 28 http://www.ncbi.nlm.nih.gov/pubmed/19717646?ordinalpos=49&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Zempsky WT, Loiselle KA, McKay K, Lee BH, Hagstrom JN, Schechter NL. Do children with sickle cell disease receive disparate care for pain in the emergency department?J Emerg Med. 2009 Aug 22. http://www.ncbi.nlm.nih.gov/pubmed/19703740?ordinalpos=53&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

August 2009

Frei-Jones MJ, Field JJ, DeBaun MR. Multi-modal intervention and prospective implementation of standardized sickle cell pain admission orders reduces 30-day
readmission rate. Pediatr Blood Cancer. 2009 Sep;53(3):401-5. PubMed PMID:
19422031; http://www.ncbi.nlm.nih.gov/pubmed/19422031?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum


Brandão RA, de Carvalho GT, Reis BL, Bahia E, de Souza AA. Intracranial aneurysms in sickle cell patients: report of 2 cases and review of the
literature. Surg Neurol. 2009 Sep;72(3):296-9; discussion 299. Epub 2008 Jul 9.
http://www.ncbi.nlm.nih.gov/pubmed/18614211?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum


Lou TF, Singh M, Mackie A, Li W, Pace BS. Hydroxyurea Generates Nitric Oxide in Human Erythroid Cells: Mechanisms for {gamma}-Globin Gene Activation. Exp Biol Med (Maywood). 2009 Aug 5. http://www.ncbi.nlm.nih.gov/pubmed/19657070?ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum


Brandow AM, Brousseau DC, Pajewski NM, Panepinto JA. Vaso-occlusive painful events in sickle cell disease: Impact on child well-being. Pediatr Blood Cancer.
2009 Aug 3. [Epub ahead of print] http://www.ncbi.nlm.nih.gov/pubmed/19653296?ordinalpos=21&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Ghugre NR, Gonzalez-Gomez I, Butensky E, Noetzli L, Fischer R, Williams R, Harmatz P, Coates TD, Wood JC. Patterns of hepatic iron distribution in patients
with chronically transfused thalassemia and sickle cell disease. Am J Hematol. 2009 Aug;84(8):480-3. http://www.ncbi.nlm.nih.gov/pubmed/19536851?ordinalpos=25&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Brousse V, Hertz-Pannier L, Consigny Y, Bresson JL, Girot R, Mirre E, Lenoir G, de Montalembert M. Does regular blood transfusion prevent progression of
cerebrovascular lesions in children with sickle cell disease? Ann Hematol. 2009 Aug;88(8):785-8. Epub 2008 Dec 24. http://www.ncbi.nlm.nih.gov/pubmed/19107481?ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Lee MT, Small T, Khan MA, Rosenzweig EB, Barst RJ, Brittenham GM. Doppler-defined pulmonary hypertension and the risk of death in children with
sickle cell disease followed for a mean of three years. Br J Haematol. 2009 Aug;146(4):437-41. Epub 2009 Jun 25. http://www.ncbi.nlm.nih.gov/pubmed/19563512?ordinalpos=30&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Kwiatkowski JL, Zimmerman RA, Pollock AN, Seto W, Smith-Whitley K, Shults J, Blackwood-Chirchir A, Ohene-Frempong K. Silent infarcts in young children with
sickle cell disease. Br J Haematol. 2009 Aug;146(3):300-5. Epub 2009 Jun 4.
http://www.ncbi.nlm.nih.gov/pubmed/19500105?ordinalpos=32&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Howard J, Thomas VJ, Rawle HM. Pain management and quality of life in sickle cell disease. Expert Rev Pharmacoecon Outcomes Res. 2009 Aug;9(4):347-52. http://www.ncbi.nlm.nih.gov/pubmed/19670995?ordinalpos=34&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Imran F, Phatak P. Pharmacoeconomic benefits of deferasirox in the management of iron overload syndromes. Expert Rev Pharmacoecon Outcomes Res. 2009
Aug;9(4):297-304. http://www.ncbi.nlm.nih.gov/pubmed/19670988?ordinalpos=35&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Crosby LE, Modi AC, Lemanek KL, Guilfoyle SM, Kalinyak KA, Mitchell MJ. Perceived barriers to clinic appointments for adolescents with sickle cell
disease. J Pediatr Hematol Oncol. 2009 Aug;31(8):571-6. http://www.ncbi.nlm.nih.gov/pubmed/19636266?ordinalpos=40&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

July 2009
1: Brousse V, Hertz-Pannier L, Consigny Y, Bresson JL, Girot R, Mirre E, 
Lenoir G, de Montalembert M. Does regular blood transfusion prevent progression 
of 
cerebrovascular lesions in children with sickle cell disease? Ann Hematol. 2009 Aug;88(8):785-8. Epub 2008 Dec 24.
http://www.ncbi.nlm.nih.gov/pubmed/19107481?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

2: Brousseau DC, Mukonje T, Brandow AM, Nimmer M, Panepinto JA. Dissatisfaction with hospital care for children with sickle cell disease not due only to race and
chronic disease. Pediatr Blood Cancer. 2009 Aug;53(2):174-8.
http://www.ncbi.nlm.nih.gov/pubmed/19350642?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

3: Dowling MM, Quinn CT, Rogers ZR, Journeycake JM. Stroke in sickle cell anemia: alternative etiologies. Pediatr Neurol. 2009 Aug;41(2):124-6.

http://www.ncbi.nlm.nih.gov/pubmed/19589461?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

4: Martí-Carvajal AJ, Solà I, Agreda-Pérez LH. Treatment for avascular necrosis of bone in people with sickle cell disease. Cochrane Database Syst Rev. 2009 Jul
8;(3):
http://www.ncbi.nlm.nih.gov/pubmed/19588352?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

5: Conran N, Costa FF. Hemoglobinopathies and Endothelial Cell Interactions. Clin Biochem. 2009 Jul 3. .
http://www.ncbi.nlm.nih.gov/pubmed/19580799?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

6: Strijbos MH, Landburg PP, Nur E, Teerlink T, Leebeek FW, Rijneveld AW, Biemond BJ, Sleijfer S, Gratama JW, Duits AJ, Schnog JJ; CURAMA study group. Circulating
endothelial cells: a potential parameter of organ damage in sickle cell anemia? Blood Cells Mol Dis. 2009 Jul-Aug;43(1):63-7. Epub 2009 Apr 7.
http://www.ncbi.nlm.nih.gov/pubmed/19356955?ordinalpos=23&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSumJune 2009
Shord SS, Cavallari LH, Gao W, Jeong HY, Deyo K, Patel SR, Camp JR, Labott SM, Molokie RE. The pharmacokinetics of codeine and its metabolites in Blacks with
sickle cell disease. Eur J Clin Pharmacol. 2009 Jul;65(7):651-8. Epub 2009 Apr 9.
http://www.ncbi.nlm.nih.gov/pubmed/19357842?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
McPherson M, Thaniel L, Minniti CP. Transition of patients with sickle cell disease from pediatric to adult care: Assessing patient readiness. Pediatr Blood 
Cancer. 2009 Jul;52(7):838-41. http://www.ncbi.nlm.nih.gov/pubmed/19229973?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Liem RI, Young LT, Thompson AA. Prolonged QTc interval in children and young adults with sickle cell disease at steady state. Pediatr Blood Cancer. 2009
Jul;52(7):842-6. http://www.ncbi.nlm.nih.gov/pubmed/19229972?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Komba AN, Makani J, Sadarangani M, Ajala-Agbo T, Berkley JA, Newton CR, Marsh K, Williams TN. Malaria as a Cause of Morbidity and Mortality in Children with
Homozygous Sickle Cell Disease on the Coast of Kenya. Clin Infect Dis. 2009 Jun
10. http://www.ncbi.nlm.nih.gov/pubmed/19514855?ordinalpos=15&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Fitzhugh CD, Hsieh MM, Bolan CD, Saenz C, Tisdale JF. Granulocyte colony-stimulating factor (G-CSF) administration in individuals with sickle cell 
disease: time for a moratorium? Cytotherapy. 2009 Jun 9:1-8. 
http://www.ncbi.nlm.nih.gov/pubmed/19513902?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Kwiatkowski JL, Zimmerman RA, Pollock AN, Seto W, Smith-Whitley K, Shults J,Blackwood-Chirchir A, Ohene-Frempong K. Silent infarcts in young children with
sickle cell disease. Br J Haematol. 2009 Jun 4.
http://www.ncbi.nlm.nih.gov/pubmed/19500105?ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Naoman SG, Nouraie M, Castro OL, Nwokolo C, Fadojutimi-Akinsiku M, Diaz S,Willie-Carnegie G, Andrews N, Gordeuk VR. Echocardiographic findings in patients 
with sickle cell disease. Ann Hematol. 2009 Jun 2. 
http://www.ncbi.nlm.nih.gov/pubmed/19488751?ordinalpos=24&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Booth C, Inusa B, Obaro SK. Infection in sickle cell disease: A review. Int J
Infect Dis. 2009 Jun 2. http://www.ncbi.nlm.nih.gov/pubmed/19497774?ordinalpos=26&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Mvundura M, Amendah D, Kavanagh PL, Sprinz PG, Grosse SD. Health care utilization and expenditures for privately and publicly insured children with
sickle cell disease in the United States. Pediatr Blood Cancer. 2009 Jun 2.
http://www.ncbi.nlm.nih.gov/pubmed/19492318?ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Scheinin L, Wetli CV. Sudden death and sickle cell trait: medicolegal
considerations and implications. Am J Forensic Med Pathol. 2009 Jun;30(2):204-8. 
http://www.ncbi.nlm.nih.gov/pubmed/19465821?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Flanagan JM, Steward S, Hankins JS, Howard TM, Neale G, Ware RE. Microarray analysis of liver gene expression in iron overloaded patients with sickle cell
anemia and beta-thalassemia. Am J Hematol. 2009 Jun;84(6):328-34. 
http://www.ncbi.nlm.nih.gov/pubmed/19384939?ordinalpos=34&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Kauf TL, Coates TD, Huazhi L, Mody-Patel N, Hartzema AG. The cost of health care for children and adults with sickle cell disease. Am J Hematol. 2009
Jun;84(6):323-7. http://www.ncbi.nlm.nih.gov/pubmed/19358302?ordinalpos=35&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Austin H, Lally C, Benson JM, Whitsett C, Hooper WC, Key NS. Hormonal contraception, sickle cell trait, and risk for venous thromboembolism among
African American women. Am J Obstet Gynecol. 2009 Jun;200(6):620.e1-3. 
http://www.ncbi.nlm.nih.gov/pubmed/19306959?ordinalpos=38&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Testa U. Fetal hemoglobin chemical inducers for treatment of hemoglobinopathies. Ann Hematol. 2009 Jun;88(6):505-28. Epub 2008 Nov 15. 
http://www.ncbi.nlm.nih.gov/pubmed/19011856?ordinalpos=39&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

May 2009

Simon K, Barakat LP, Patterson CA, Dampier C. Symptoms of depression and anxiety in adolescents with sickle cell disease: the role of intrapersonal
characteristics and stress processing variables. Child Psychiatry Hum Dev. 2009
Jun;40(2):317-30. http://www.ncbi.nlm.nih.gov/pubmed/19169810?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Mitchell MJ, Carpenter GJ, Crosby LE, Bishop CT, Hines J, Noll J. Growth status in children and adolescents with sickle cell disease. Pediatr Hematol
Oncol. 2009 Jun;26(4):202-15. http://www.ncbi.nlm.nih.gov/pubmed/19437323?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Lukusa AK, Vermylen C, Vanabelle B, Curaba M, Brichard B, Chantrain C, Dupont  S, Ferrant A, Wyns C. Bone marrow transplantation or hydroxyurea for sickle cell 
anemia: long-term effects on semen variables and hormone profiles. Pediatr
Hematol Oncol. 2009 Jun;26(4):186-94. http://www.ncbi.nlm.nih.gov/pubmed/19437321?ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Frei-Jones MJ, Field JJ, Debaun MR. Multi-modal intervention and prospective implementation of standardized sickle cell pain admission orders reduces 30-day
readmission rate. Pediatr Blood Cancer. 2009 May 6. 
http://www.ncbi.nlm.nih.gov/pubmed/19422031?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Yates AM, Hankins JS, Mortier NA, Aygun B, Ware RE. Simultaneous acute splenic sequestration and transient aplastic crisis in children with sickle cell disease.
Pediatr Blood Cancer. 2009 May 5. http://www.ncbi.nlm.nih.gov/pubmed/19418550?ordinalpos=18&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Aisiku IP, Smith WR, McClish DK, Levenson JL, Penberthy LT, Roseff SD, Bovbjerg VE, Roberts JD. Comparisons of high versus low emergency department
utilizers in sickle cell disease. Ann Emerg Med. 2009 May;53(5):587-93. Epub 2008
Oct 16. http://www.ncbi.nlm.nih.gov/pubmed/18926599?ordinalpos=27&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Aygun B, McMurray MA, Schultz WH, Kwiatkowski JL, Hilliard L, Alvarez O, Heeney M, Kalinyak K, Lee MT, Miller S, Helms RW, Ware RE; SWiTCH Trial
Investigators. Chronic transfusion practice for children with sickle cell anaemia and stroke. Br J Haematol. 2009 May;145(4):524-8. Epub 2008 Mar 13. 
http://www.ncbi.nlm.nih.gov/pubmed/19344396?ordinalpos=34&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Cotton S, Grossoehme D, Rosenthal SL, McGrady ME, Roberts YH, Hines J, Yi MS, Tsevat J. Religious/Spiritual coping in adolescents with sickle cell disease: a
pilot study. J Pediatr Hematol Oncol. 2009 May;31(5):313-8. 
http://www.ncbi.nlm.nih.gov/pubmed/19415008?ordinalpos=40&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Brown K, Subramony C, May W, Megason G, Liu H, Bishop P, Walker T, Nowicki MJ. Hepatic iron overload in children with sickle cell anemia on chronic
transfusion therapy. J Pediatr Hematol Oncol. 2009 May;31(5):309-12. 
http://www.ncbi.nlm.nih.gov/pubmed/19415007?ordinalpos=41&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Thornburg CD, Dixon N, Burgett S, Mortier NA, Schultz WH, Zimmerman SA, Bonner M, Hardy KK, Calatroni A, Ware RE. A pilot study of hydroxyurea to prevent
chronic organ damage in young children with sickle cell anemia. Pediatr Blood Cancer. 2009 May;52(5):609-15. http://www.ncbi.nlm.nih.gov/pubmed/19061213?ordinalpos=45&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Turner JM, Kaplan JB, Cohen HW, Billett HH. Exchange versus simple transfusion for acute chest syndrome in sickle cell anemia adults. Transfusion.
2009 May;49(5):863-8. Epub 2009 May 1. http://www.ncbi.nlm.nih.gov/pubmed/19309475?ordinalpos=52&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Lieberman L, Kirby M, Ozolins L, Mosko J, Friedman J. Initial presentation of unscreened children with sickle cell disease: The Toronto experience. Pediatr
Blood Cancer. 2009 Apr 29. http://www.ncbi.nlm.nih.gov/pubmed/19405139?ordinalpos=53&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Chadebech P, Habibi A, Nzouakou R, Bachir D, Meunier-Costes N, Bonin P, Rodet M, Chami B, Galacteros F, Bierling P, Noizat-Pirenne F. Delayed hemolytic
transfusion reaction in sickle cell disease patients: evidence of an emerging syndrome with suicidal red blood cell death. Transfusion. 2009 Apr 28. http://www.ncbi.nlm.nih.gov/pubmed/19413729?ordinalpos=55&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Tsaras G, Owusu-Ansah A, Boateng FO, Amoateng-Adjepong Y. Complications Associated with Sickle Cell Trait: A Brief Narrative Review. Am J Med. 2009 Apr
24. http://www.ncbi.nlm.nih.gov/pubmed/19393983?ordinalpos=58&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Abo-Zenah H, Moharram M, El Nahas AM. Cardiorenal Risk Prevalence in Sickle Cell Hemoglobinopathy. Nephron Clin Pract. 2009 Apr 23;112(2):c98-c106 http://www.ncbi.nlm.nih.gov/pubmed/19390209?ordinalpos=60&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

April 2009

McPherson M, Thaniel L, Minniti CP. Transition of patients with sickle cell
disease from pediatric to adult care: Assessing patient readiness. Pediatr Blood Cancer.
2009 Jul;52(7):838-41.
http://www.ncbi.nlm.nih.gov/pubmed/19229973?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Liem RI, Young LT, Thompson AA. Prolonged QTc interval in children and young
adults with sickle cell disease at steady state. Pediatr Blood Cancer. 2009
Jul;52(7):842-6.
http://www.ncbi.nlm.nih.gov/pubmed/19229972?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Raphael JL, Bernhardt MB, Mahoney DH, Mueller BU. Oral iron chelation and the
treatment of iron overload in a pediatric hematology center. Pediatr Blood
Cancer. 2009 May;52(5):616-20.
http://www.ncbi.nlm.nih.gov/pubmed/19148949?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Issaivanan M, Ahmed R, Shekher M, Esernio-Jenssen D, Manwani D. Sickle cell
disease and plumbism in children. Pediatr Blood Cancer. 2009 May;52(5):653-6.
http://www.ncbi.nlm.nih.gov/pubmed/19127571?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Thornburg CD, Dixon N, Burgett S, Mortier NA, Schultz WH, Zimmerman SA, Bonner
M, Hardy KK, Calatroni A, Ware RE. A pilot study of hydroxyurea to prevent
chronic organ damage in young children with sickle cell anemia. Pediatr Blood
Cancer. 2009 May;52(5):609-15.
http://www.ncbi.nlm.nih.gov/pubmed/19061213?ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Panepinto JA, Hoffmann RG, Pajewski NM. A psychometric evaluation of the
PedsQL Family Impact Module in parents of children with sickle cell disease.
Health Qual Life Outcomes. 2009 Apr 16;7(1):32. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/19371442?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Martí-Carvajal AJ, Agreda-Pérez LH, Cortés-Jofré M. Antibiotics for treating
osteomyelitis in people with sickle cell disease. Cochrane Database Syst Rev.
2009 Apr 15;(2):CD007175.
http://www.ncbi.nlm.nih.gov/pubmed/19370676?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Eccleston C, Palermo TM, Williams AC, Lewandowski A, Morley S. Psychological
therapies for the management of chronic and recurrent pain in children and
adolescents. Cochrane Database Syst Rev. 2009 Apr 15;(2):CD003968.
http://www.ncbi.nlm.nih.gov/pubmed/19370592?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Armstrong-Wells J, Grimes B, Sidney S, Kronish D, Shiboski SC, Adams RJ,
Fullerton HJ. Utilization of TCD screening for primary stroke prevention in
children with sickle cell disease. Neurology. 2009 Apr 14;72(15):1316-21.
http://www.ncbi.nlm.nih.gov/pubmed/19365052?ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Strijbos MH, Landburg PP, Nur E, Teerlink T, Leebeek FW, Rijneveld AW,
Biemond BJ, Sleijfer S, Gratama JW, Duits AJ, Schnog JJ; on behalf of the CURAMA study
group. Circulating endothelial cells: A potential parameter of organ damage
in sickle cell anemia?. Blood Cells Mol Dis. 2009 Apr 6.
http://www.ncbi.nlm.nih.gov/pubmed/19356955?ordinalpos=23&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Brousseau DC, Mukonje T, Brandow AM, Nimmer M, Panepinto JA. Dissatisfaction with
hospital care for children with sickle cell disease not due only to race and
chronic disease. Pediatr Blood Cancer. 2009 Apr 6.
[http://www.ncbi.nlm.nih.gov/pubmed/19350642?ordinalpos=24&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Morris CR. Asthma management: reinventing the wheel in sickle cell disease.
Am J Hematol. 2009 Apr;84(4):234-41. Review. PubMed PMID: 19229984.
http://www.ncbi.nlm.nih.gov/pubmed/19229984?ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Yanni E, Grosse SD, Yang Q, Olney RS. Trends in pediatric sickle cell
disease-related mortality in the United States, 1983-2002. J Pediatr. 2009
Apr;154(4):541-5. Epub 2008 Nov 22. PubMed PMID: 19028391.
http://www.ncbi.nlm.nih.gov/pubmed/19028391?ordinalpos=37&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 

March 2009

Simon K, Barakat LP, Patterson CA, Dampier C.
 Symptoms of depression and anxiety in adolescents with sickle cell disease: the role of intrapersonal characteristics and stress processing variables.
Child Psychiatry Hum Dev. 2009 Jun;40(2):317-30. Epub 2009 Jan 24.
http://www.ncbi.nlm.nih.gov/pubmed/19169810?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Okoli K, Irani F, Horvath W.
 Pathophysiologic considerations for the interactions between obstructive sleep apnea and sickle hemoglobinopathies.
Med Hypotheses. 2009 May;72(5):578-80. Epub 2009 Jan 12.
http://www.ncbi.nlm.nih.gov/pubmed/19138828?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Little JA, Hauser KP, Martyr SE, Harris A, Maric I, Morris CR, Suh JH, Taylor  J, Castro O, Machado R, Kato G, Gladwin MT.
 Hematologic, biochemical, and cardiopulmonary effects of L-arginine supplementation or phosphodiesterase 5 inhibition in patients with sickle cell
disease who are on hydroxyurea therapy.
Eur J Haematol. 2009 Apr;82(4):315-21. Epub 2008 Feb 10.
http://www.ncbi.nlm.nih.gov/pubmed/19215288?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Michlitsch J, Azimi M, Hoppe C, Walters MC, Lubin B, Lorey F, Vichinsky E.
 Newborn screening for hemoglobinopathies in California.
Pediatr Blood Cancer. 2009 Apr;52(4):486-90.
http://www.ncbi.nlm.nih.gov/pubmed/19061217?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 Frei-Jones MJ, Field JJ, DeBaun MR.
 Risk factors for hospital readmission within 30 days: a new quality measure for children with sickle cell disease.
Pediatr Blood Cancer. 2009 Apr;52(4):481-5.
http://www.ncbi.nlm.nih.gov/pubmed/19058209?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Lemanek KL, Ranalli M, Lukens C.
 A Randomized Controlled Trial of Massage Therapy in Children with Sickle Cell Disease.
J Pediatr Psychol. 2009 Mar 12. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/19282374?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Al Jama FE, Gasem T, Burshaid S, Rahman J, Al Suleiman SA, Rahman MS.
 Pregnancy outcome in patients with homozygous sickle cell disease in a university hospital, Eastern Saudi Arabia.
Arch Gynecol Obstet. 2009 Mar 7. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/19271230?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Berger E, Saunders N, Wang L, Friedman JN.
 Sickle cell disease in children: Differentiating osteomyelitis from vaso-occlusive crisis.
Arch Pediatr Adolesc Med. 2009 Mar;163(3):251-5.
http://www.ncbi.nlm.nih.gov/pubmed/19255393?ordinalpos=26&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Raghupathy R, Billett HH.  Promising therapies in sickle cell disease.
Cardiovasc Hematol Disord Drug Targets. 2009 Mar;9(1):1-8.
http://www.ncbi.nlm.nih.gov/pubmed/19275572?ordinalpos=30&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Morrissey LK, Shea JO, Kalish LA, Weiner DL, Branowicki P, Heeney MM.
 Clinical practice guideline improves the treatment of sickle cell disease vasoocclusive pain.
Pediatr Blood Cancer. 2009 Mar;52(3):369-72.
http://www.ncbi.nlm.nih.gov/pubmed/19023890?ordinalpos=38&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

February 2009

Brandow AM, Brousseau DC, Panepinto JA.  Postdischarge pain, functional limitations and impact on caregivers of children
with sickle cell disease treated for painful events. Br J Haematol. 2009 Mar;144(5):782-8. Epub 2008 Dec 1.
http://www.ncbi.nlm.nih.gov/pubmed/19055663?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Khademian Z, Speller-Brown B, Nouraie SM, Minniti CP.  Reversible posterior leuko-encephalopathy in children with sickle cell disease.
Pediatr Blood Cancer. 2009 Mar;52(3):373-5.
http://www.ncbi.nlm.nih.gov/pubmed/19003906?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Prohovnik I, Hurlet-Jensen A, Adams R, De Vivo D, Pavlakis SG.  Hemodynamic etiology of elevated flow velocity and stroke in sickle-cell disease.
J Cereb Blood Flow Metab. 2009 Feb 11. http://www.ncbi.nlm.nih.gov/pubmed/19209182?ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Boyd JH, Debaun MR, Morgan WJ, Mao J, Strunk RC.  Lower airway obstruction is associated with increased morbidity in children with 
sickle cell disease. Pediatr Pulmonol. 2009 Feb 9. 
http://www.ncbi.nlm.nih.gov/pubmed/19205057?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Trompeter S, Roberts I. Haemoglobin F modulation in childhood sickle cell disease.
Br J Haematol. 2009 Feb;144(3):308-16. Epub 2008 Nov 20.
http://www.ncbi.nlm.nih.gov/pubmed/19036119?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Sedrak A, Rao SP, Miller ST, Hekmat V, Rao M. A prospective appraisal of pulmonary hypertension in children with sickle cell
disease. J Pediatr Hematol Oncol. 2009 Feb;31(2):97-100.
http://www.ncbi.nlm.nih.gov/pubmed/19194191?ordinalpos=31&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Scheinman JI.  Sickle cell disease and the kidney.
Nat Clin Pract Nephrol. 2009 Feb;5(2):78-88. Epub 2008 Dec 2.
http://www.ncbi.nlm.nih.gov/pubmed/19048000?ordinalpos=33&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Raphael JL, Dietrich CL, Whitmire D, Mahoney DH, Mueller BU, Giardino AP.
 Healthcare utilization and expenditures for low income children with sickle cell 
disease. Pediatr Blood Cancer. 2009 Feb;52(2):263-7.
http://www.ncbi.nlm.nih.gov/pubmed/18837428?ordinalpos=35&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Panepinto JA, Pajewski NM, Foerster LM, Sabnis S, Hoffmann RG.
 Impact of family income and sickle cell disease on the health-related quality of 
life of children. Qual Life Res. 2009 Feb;18(1):5-13. Epub 2008 Nov 7.
http://www.ncbi.nlm.nih.gov/pubmed/18989755?ordinalpos=38&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Simon K, Barakat LP, Patterson CA, Dampier C.  Symptoms of Depression and Anxiety in Adolescents with Sickle Cell Disease: The
Role of Intrapersonal Characteristics and Stress Processing Variables.
Child Psychiatry Hum Dev. 2009 Jan 24. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/19169810?ordinalpos=42&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Oringanje C, Nemecek E, Oniyangi O.  Hematopoietic stem cell transplantation for children with sickle cell disease.
Cochrane Database Syst Rev. 2009 Jan 21;(1):CD007001.
http://www.ncbi.nlm.nih.gov/pubmed/19160312?ordinalpos=45&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Martí-Carvajal AJ, Peña-Martí GE, Comunián-Carrasco G, Martí-Peña AJ.
 Interventions for treating painful sickle cell crisis during pregnancy.
Cochrane Database Syst Rev. 2009 Jan 21;(1):CD006786.
http://www.ncbi.nlm.nih.gov/pubmed/19160301?ordinalpos=46&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

January 2009

Morrissey LK, Shea JO, Kalish LA, Weiner DL, Branowicki P, Heeney MM.
 Clinical practice guideline improves the treatment of sickle cell disease vasoocclusive pain.
Pediatr Blood Cancer. 2009 Mar;52(3):369-72.
http://www.ncbi.nlm.nih.gov/pubmed/19023890?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Raphael JL, Dietrich CL, Whitmire D, Mahoney DH, Mueller BU, Giardino AP.
 Healthcare utilization and expenditures for low income children with sickle cell disease.
Pediatr Blood Cancer. 2009 Feb;52(2):263-7.
http://www.ncbi.nlm.nih.gov/pubmed/18837428?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Okoli K, Irani F, Horvath W.  Pathophysiologic considerations for the interactions between obstructive sleep
apnea and sickle hemoglobinopathies.
Med Hypotheses. 2009 Jan 10. 
http://www.ncbi.nlm.nih.gov/pubmed/19138828?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Hassell K, Pace B, Wang W, Kulkarni R, Luban N, Johnson CS, Eckman J, Lane P,  Woods WG.
 Sickle cell disease summit: from clinical and research disparity to action.
Am J Hematol. 2009 Jan;84(1):39-45. Full Text PDF
http://www3.interscience.wiley.com/cgi-bin/fulltext/121461964/PDFSTART

Bader-Meunier B, Verlhac S, Elmaleh-Bergès M, Ithier G, Sellami F, Faid S, Missud F, Ducrocq R, Alberti C, Zaccaria I, Baruchel A, Benkerrou M.
 Effect of transfusion therapy on cerebral vasculopathy in children with sickle-cell anemia.
Haematologica. 2009 Jan;94(1):123-6. Epub 2008 Dec 4.
http://www.ncbi.nlm.nih.gov/pubmed/19059938?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
McLeod C, Fleeman N, Kirkham J, Bagust A, Boland A, Chu P, Dickson R, Dundar Y, Greenhalgh J, Modell B, Olujohungbe A, Telfer P, Walley T.
 Deferasirox for the treatment of iron overload associated with regular blood transfusions (transfusional haemosiderosis) in patients suffering with chronic
anaemia: a systematic review and economic evaluation.
Health Technol Assess. 2009 Jan;13(1):iii-iv, ix-xi, 1-121.
http://www.ncbi.nlm.nih.gov/pubmed/19068191?ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Rahimy MC, Gangbo A, Ahouignan G, Alihonou E.
 Newborn screening for sickle cell disease in the Republic of Benin.
J Clin Pathol. 2009 Jan;62(1):46-8.
http://www.ncbi.nlm.nih.gov/pubmed/19103860?ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Kafando E, Nacoulma E, Ouattara Y, Ayéroué J, Cotton F, Sawadogo M, Gulbis B.
 Neonatal haemoglobinopathy screening in Burkina Faso.
J Clin Pathol. 2009 Jan;62(1):39-41.
http://www.ncbi.nlm.nih.gov/pubmed/19103858?ordinalpos=24&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Tshilolo L, Aissi LM, Lukusa D, Kinsiama C, Wembonyama S, Gulbis B, Vertongen F.
 Neonatal screening for sickle cell anaemia in the Democratic Republic of the Congo: experience from a pioneer project on 31 204 newborns.
J Clin Pathol. 2009 Jan;62(1):35-8.
http://www.ncbi.nlm.nih.gov/pubmed/19103857?ordinalpos=25&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Dickerhoff R, Genzel-Boroviczeny O, Kohne E.  Haemoglobinopathies and newborn haemoglobinopathy screening in Germany.
J Clin Pathol. 2009 Jan;62(1):34.
http://www.ncbi.nlm.nih.gov/pubmed/19103856?ordinalpos=26&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Bardakdjian-Michau J, Bahuau M, Hurtrel D, Godart C, Riou J, Mathis M, Goossens M.
 Neonatal screening for sickle cell disease in France. J Clin Pathol. 2009 Jan;62(1):31-3.
http://www.ncbi.nlm.nih.gov/pubmed/19103855?ordinalpos=27&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Streetly A, Latinovic R, Hall K, Henthorn J. Implementation of universal newborn bloodspot screening for sickle cell disease
and other clinically significant haemoglobinopathies in England: screening results for 2005-7.
J Clin Pathol. 2009 Jan;62(1):26-30.
http://www.ncbi.nlm.nih.gov/pubmed/19103854?ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Mañú Pereira M, Corrons JL.  Neonatal haemoglobinopathy screening in Spain.
J Clin Pathol. 2009 Jan;62(1):22-5.
http://www.ncbi.nlm.nih.gov/pubmed/19103853?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Khatib R, Rabah R, Sarnaik SA. The spleen in the sickling disorders: an update.
Pediatr Radiol. 2009 Jan;39(1):17-22. Epub 2008 Nov 11.
http://www.ncbi.nlm.nih.gov/pubmed/19002450?ordinalpos=39&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Steinberg MH. Sickle cell anemia, the first molecular disease: overview of molecular etiology, 
pathophysiology, and therapeutic approaches.ScientificWorldJournal. 2008 Dec 25;8:1295-324.
http://www.ncbi.nlm.nih.gov/pubmed/19112541?ordinalpos=48&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

December 2008

Gregory J. Kato, MD; Mark T. Gladwin, MD  Evolution of Novel Small-Molecule Therapeutics Targeting Sickle Cell Vasculopathy, JAMA. 2008;300(22):2638-2646. http://jama.ama-assn.org/cgi/content/short/300/22/2638

Sankaran VG, Menne TF, Xu J, Akie TE, Lettre G, Van Handel B, Mikkola HK,
Hirschhorn JN, Cantor AB, Orkin SH. Human Fetal Hemoglobin Expression Is Regulated by the Developmental
Stage-Specific Repressor BCL11A. Science. 2008 Dec 4. http://www.sciam.com/article.cfm?id=new-hope-for-sickle-cell-sufferers

Pestina TI, Hargrove PW, Jay D, Gray JT, Boyd KM, Persons DA.Correction of Murine Sickle Cell Disease Using gamma-Globin Lentiviral Vectors to Mediate High-level Expression of Fetal Hemoglobin. Mol Ther. 2008 Dec 2. http://www.ncbi.nlm.nih.gov/pubmed/19050697?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

McLeod C, Fleeman N, Kirkham J, Bagust A, Boland A, Chu P, Dickson R, Dundar Y, Greenhalgh J, Modell B, Olujohungbe A, Telfer P, Walley T.
 Deferasirox for the treatment of iron overload associated with regular blood transfusions (transfusional haemosiderosis) in patients suffering with chronic
anaemia: a systematic review and economic evaluation.
Health Technol Assess. 2009 Jan;13(1):1-144.
http://www.ncbi.nlm.nih.gov/pubmed/19068191?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Schwartz LA, Radcliffe J, Barakat LP.
 Associates of school absenteeism in adolescents with sickle cell disease.
Pediatr Blood Cancer. 2009 Jan;52(1):92-6.
http://www.ncbi.nlm.nih.gov/pubmed/19006248?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Michlitsch J, Azimi M, Hoppe C, Walters MC, Lubin B, Lorey F, Vichinsky E.
 Newborn screening for hemoglobinopathies in California.
Pediatr Blood Cancer. 2008 Dec 5. 
http://www.ncbi.nlm.nih.gov/pubmed/19061217?ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Thornburg CD, Dixon N, Burgett S, Mortier NA, Schultz WH, Zimmerman SA, Bonner M, Hardy KK, Calatroni A, Ware RE.
 A pilot study of hydroxyurea to prevent chronic organ damage in young children with sickle cell anemia.
Pediatr Blood Cancer. 2008 Dec 5.
http://www.ncbi.nlm.nih.gov/pubmed/19061213?ordinalpos=18&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Bader-Meunier B, Verlhac S, Elmaleh-Bergès M, Ithier G, Sellami F, Faid S, Missud F, Ducrocq R, Alberti C, Zaccaria I, Baruchel A, Benkerrou M.
 Effect of transfusion therapy on cerebral vasculopathy in children with sickle-cell anemia.
Haematologica. 2008 Dec 4. 
http://www.ncbi.nlm.nih.gov/pubmed/19059938?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Frei-Jones MJ, Field JJ, Debaun MR.
 Risk factors for hospital readmission within 30 days: A new quality measure for children with sickle cell disease.
Pediatr Blood Cancer. 2008 Dec 4
http://www.ncbi.nlm.nih.gov/pubmed/19058209?ordinalpos=20&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Pashankar FD, Carbonella J, Bazzy-Asaad A, Friedman A.
 Longitudinal follow up of elevated pulmonary artery pressures in children with sickle cell disease.
Br J Haematol. 2008 Dec 1.
http://www.ncbi.nlm.nih.gov/pubmed/19055665?ordinalpos=30&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Brandow AM, Brousseau DC, Panepinto JA.
 Postdischarge pain, functional limitations and impact on caregivers of children with sickle cell disease treated for painful events.
Br J Haematol. 2008 Dec 1. 
http://www.ncbi.nlm.nih.gov/pubmed/19055663?ordinalpos=31&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Wang WC.  The pharmacotherapy of sickle cell disease.
Expert Opin Pharmacother. 2008 Dec;9(17):3069-82.
http://www.ncbi.nlm.nih.gov/pubmed/19006479?ordinalpos=37&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Strouse JJ, Lanzkron S, Beach MC, Haywood C, Park H, Witkop C, Wilson RF, Bass EB, Segal JB.
 Hydroxyurea for sickle cell disease: a systematic review for efficacy and toxicity in children.
Pediatrics. 2008 Dec;122(6):1332-42.
http://www.ncbi.nlm.nih.gov/pubmed/19047254?ordinalpos=46&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Michel M, Habibi A, Godeau B, Bachir D, Lahary A, Galacteros F, Fifi-Mah A, Arfi S.
 Characteristics and outcome of connective tissue diseases in patients with sickle-cell disease: report of 30 cases.
Semin Arthritis Rheum. 2008 Dec;38(3):228-40. Epub 2008 Jan 4.
http://www.ncbi.nlm.nih.gov/pubmed/18177923?ordinalpos=47&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Price CL, Johnson MT, Lindsay T, Dalton D, Debaun MR.
 The Sickle Cell Sabbath: a community program increases first-time blood donors in the African American faith community.
Transfusion. 2008 Nov 25.
http://www.ncbi.nlm.nih.gov/pubmed/19040492?ordinalpos=56&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
McClellan CB, Schatz JC, Puffer E, Sanchez CE, Stancil MT, Roberts CW.
 Use of Handheld Wireless Technology for a Home-based Sickle Cell Pain Management  Protocol.
J Pediatr Psychol. 2008 Nov 23. 
http://www.ncbi.nlm.nih.gov/pubmed/19029141?ordinalpos=57&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Gladwin MT, Vichinsky E.  Pulmonary complications of sickle cell disease.
N Engl J Med. 2008 Nov 20;359(21):2254-65. Review. .
http://www.ncbi.nlm.nih.gov/pubmed/19020327?ordinalpos=63&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Gold JI, Treadwell M, Weissman L, Vichinsky E (2008)
An Expanded Transactional Stress and Coping Model for Siblings of Children with Sickle Cell Disease: Family Functioning and Sibling Coping, Self-Efficacy, and Perceived Social Support. Child: Care, Health & Development http://www.ncbi.nlm.nih.gov/pubmed/18485027?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Gold JI, Johnson CB, Treadwell MJ, Hans N, Vichinsky EP (2008)
Detection and assessment of stroke in patients with sickle cell disease: Neuropsychological functioning and magnetic resonance imaging. Pediatric Hematology and Oncology, 25, 409-421. http://www.ncbi.nlm.nih.gov/pubmed/18569843?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Gold JI, Mahrer NE, Treadwell MJ, Weissman L, Vichinsky EP
Psychosocial Outcomes in Children with Sickle Cell Disease and their Healthy Siblings. Journal of Behavioral Medicine. http://dx.doi.org/10.1007/s10865-008-9175-2.
http://www.ncbi.nlm.nih.gov/pubmed/18784995?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

November 2008

Lanaro C, Franco-Penteado CF, Albuqueque DM, Saad ST, Conran N, Costa FF. Altered levels of cytokines and inflammatory mediators in plasma and leukocytes of sickle cell anemia patients and effects of hydroxyurea therapy. J Leukoc Biol. 2008 Nov 12. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/19004988?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

 Khatib R, Rabah R, Sarnaik SA.The spleen in the sickling disorders: an update.Pediatr Radiol. 2008 Nov 11. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/19002450?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Khademian Z, Speller-Brown B, Nouraie SM, Minniti CP. Reversible posterior leuko-encephalopathy in children with sickle cell disease.
Pediatr Blood Cancer. 2008 Nov 10. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/19003906?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Panepinto JA, Pajewski NM, Foerster LM, Sabnis S, Hoffmann RG. Impact of family income and sickle cell disease on the health-related quality of 
life of children. Qual Life Res. 2008 Nov 7. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/18989755?ordinalpos=21&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
van Beers EJ, Nur E, Schaefer-Prokop CM, Mac Gillavry MR, van Esser JW, Brandjes DP, Kappers-Klunne MC, Duits AJ, Muskiet FA, Schnog JJ, Biemond BJ;
CURAMA Study Group. Cardiopulmonary imaging, functional and laboratory studies in sickle cell disease
associated pulmonary hypertension.Am J Hematol. 2008 Nov;83(11):850-4.
http://www.ncbi.nlm.nih.gov/pubmed/18819095?ordinalpos=23&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Krishnamurti L, Kharbanda S, Biernacki MA, Zhang W, Baker KS, Wagner JE, WuCJ. Stable long-term donor engraftment following reduced-intensity hematopoietic cell
transplantation for sickle cell disease.Biol Blood Marrow Transplant. 2008 Nov;14(11):1270-8.
http://www.ncbi.nlm.nih.gov/pubmed/18940682?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Nolan VG, Zhang Y, Lash T, Sebastiani P, Steinberg MH. Association between wind speed and the occurrence of sickle cell acute painful
episodes: results of a case-crossover study. Br J Haematol. 2008 Nov;143(3):433-8. Epub 2008 Aug 20.
http://www.ncbi.nlm.nih.gov/pubmed/18729854?ordinalpos=33&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Sadelain M, Boulad F, Lisowki L, Moi P, Riviere I. Stem cell engineering for the treatment of severe Hemoglobino-pathies.
Curr Mol Med. 2008 Nov;8(7):690-7.
http://www.ncbi.nlm.nih.gov/pubmed/18991654?ordinalpos=35&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Michlitsch JG, Walters MC. Recent advances in bone marrow transplantation in hemoglobinopathies.
Curr Mol Med. 2008 Nov;8(7):675-89.
http://www.ncbi.nlm.nih.gov/pubmed/18991653?ordinalpos=36&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 Singer ST, Ataga KI. Hypercoagulability in sickle cell disease and beta-thalassemia.
Curr Mol Med. 2008 Nov;8(7):639-45.
http://www.ncbi.nlm.nih.gov/pubmed/18991650?ordinalpos=38&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Morris CR, Gladwin MT, Kato GJ. Nitric oxide and arginine dysregulation: a novel pathway to pulmonary
hypertension in hemolytic disorders. Curr Mol Med. 2008 Nov;8(7):620-32.
http://www.ncbi.nlm.nih.gov/pubmed/18991648?ordinalpos=40&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Rund D, Fucharoen S.  Genetic modifiers in hemoglobinopathies.Curr Mol Med. 2008 Nov;8(7):600-8.
http://www.ncbi.nlm.nih.gov/pubmed/18991646?ordinalpos=42&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 McClellan CB, Schatz J, Sanchez C, Roberts CW. Validity of the Pediatric Quality Of Life Inventory for youth with sickle cell
disease.J Pediatr Psychol. 2008 Nov-Dec;33(10):1153-62. Epub 2008 Apr 9.
http://www.ncbi.nlm.nih.gov/pubmed/18400838?ordinalpos=53&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Wang WC, Pavlakis SG, Helton KJ, McKinstry RC, Casella JF, Adams RJ, Rees RC;
BABY HUG Investigators. MRI abnormalities of the brain in one-year-old children with sickle cell anemia.
Pediatr Blood Cancer. 2008 Nov;51(5):643-6.
http://www.ncbi.nlm.nih.gov/pubmed/18478575?ordinalpos=57&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Aisiku IP, Smith WR, McClish DK, Levenson JL, Penberthy LT, Roseff SD, Bovbjerg VE, Roberts JD.
 Comparisons of High Versus Low Emergency Department Utilizers in Sickle Cell Disease.
Ann Emerg Med. 2008 Oct 15.
http://www.ncbi.nlm.nih.gov/pubmed/18926599?ordinalpos=69&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

October 2008

Zennadi R, Chien A, Xu K, Batchvarova M, Telen MJ.
Sickle red cells induce adhesion of lymphocytes and monocytes to endothelium.
Blood. 2008 Oct 15;112(8):3474-83. Epub 2008 Jul 29.
http://www.ncbi.nlm.nih.gov/pubmed/18664622?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Shelat S. Thrombotic Thrombocytopenic Purpura and Sickle Cell Crisis.
Clin Appl Thromb Hemost. 2008 Oct 7. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/18840631?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Boemer F, Ketelslegers O, Minon JM, Bours V, Schoos R.
Newborn Screening for Sickle Cell Disease Using Tandem Mass Spectrometry.
Clin Chem. 2008 Oct 2. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/18832473?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Sidani CA, Ballourah W, El Dassouki M, Muwakkit S, Dabbous I, Dahoui H,
Al-Kutoubi A, Abboud MR.
Venous sinus thrombosis leading to stroke in a patient with sickle cell disease
on hydroxyurea and high hemoglobin levels: treatment with thrombolysis.
Am J Hematol. 2008 Oct;83(10):818-20.
http://www.ncbi.nlm.nih.gov/pubmed/18756541?ordinalpos=15&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Carpenter SL, Lieff S, Howard TA, Eggleston B, Ware RE.
UGT1A1 promoter polymorphisms and the development of hyperbilirubinemia and
gallbladder disease in children with sickle cell anemia.
Am J Hematol. 2008 Oct;83(10):800-3.
http://www.ncbi.nlm.nih.gov/pubmed/18756540?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Adam S, Jonassaint J, Kruger H, Kail M, Orringer EP, Eckman JR, Ashley-Koch A,
Telen MJ, De Castro LM.
Surgical and obstetric outcomes in adults with sickle cell disease.
Am J Med. 2008 Oct;121(10):916-21.
http://www.ncbi.nlm.nih.gov/pubmed/18823864?ordinalpos=18&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Moreira-Almeida A, Koenig HG.
Religiousness and spirituality in fibromyalgia and chronic pain patients.
Curr Pain Headache Rep. 2008 Oct;12(5):327-32.
http://www.ncbi.nlm.nih.gov/pubmed/18765136?ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Bernard AW, Lindsell CJ, Venkat A.
Derivation of a risk assessment tool for emergency department patients with
sickle cell disease.
Emerg Med J. 2008 Oct;25(10):635-9.
http://www.ncbi.nlm.nih.gov/pubmed/18843058?ordinalpos=23&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

Okumura MJ, Heisler M, Davis MM, Cabana MD, Demonner S, Kerr EA.
Comfort of general internists and general pediatricians in providing care for
young adults with chronic illnesses of childhood.
J Gen Intern Med. 2008 Oct;23(10):1621-7. Epub 2008 Jul 26.
http://www.ncbi.nlm.nih.gov/pubmed/18661191?ordinalpos=25&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 

September 2008

Raphael JL, Shetty PB, Liu H, Mahoney DH, Mueller BU.  A critical assessment of transcranial doppler screening rates in a large
pediatric sickle cell center: opportunities to improve healthcare quality. Pediatr Blood Cancer. 2008 Nov;51(5):647-51.
http://www.ncbi.nlm.nih.gov/pubmed/18623200?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
 Wang WC, Pavlakis SG, Helton KJ, McKinstry RC, Casella JF, Adams RJ, Rees RC; BABY HUG Investigators.
 MRI abnormalities of the brain in one-year-old children with sickle cell anemia. Pediatr Blood Cancer. 2008 Nov;51(5):643-6.
http://www.ncbi.nlm.nih.gov/pubmed/18478575?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Moreira-Almeida A, Koenig HG.  Religiousness and spirituality in fibromyalgia and chronic pain patients.
Curr Pain Headache Rep. 2008 Oct;12(5):327-32.
http://www.ncbi.nlm.nih.gov/pubmed/18765136?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Okumura MJ, Heisler M, Davis MM, Cabana MD, Demonner S, Kerr EA.  Comfort of general internists and general pediatricians in providing care for
young adults with chronic illnesses of childhood. J Gen Intern Med. 2008 Oct;23(10):1621-7. Epub 2008 Jul 26.
http://www.ncbi.nlm.nih.gov/pubmed/18661191?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Sonati MD, Costa FF.  The genetics of blood disorders: the hereditary hemoglobinopathies.
J Pediatr (Rio J). 2008 Sep 12;84(4 (Suppl)).
Full Text PDF http://www.jped.com.br/conteudo/AA_12908_A01/ing.pdf
Gold JI, Mahrer NE, Treadwell M, Weissman L, Vichinsky E.  Psychosocial and behavioral outcomes in children with sickle cell disease and
their healthy siblings. J Behav Med. 2008 Sep 11. 
http://www.ncbi.nlm.nih.gov/pubmed/18784995?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Mittal H, Roberts L, Fuller GW, O'Driscoll S, Dick MC, Height SE, Thein SL, Rees DC.  The effects of air quality on haematological and clinical parameters in children 
with sickle cell anaemia. Ann Hematol. 2008 Sep 4. 
http://www.ncbi.nlm.nih.gov/pubmed/18769920?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Ulug P, Vasavda N, Kumar R, Keir L, Awogbade M, Cunningham J, Rees DC, Menzel  S, Thein SL.
 Hydroxyurea therapy lowers circulating DNA levels in sickle cell anemia. Am J Hematol. 2008 Sep;83(9):714-6.
http://www.ncbi.nlm.nih.gov/pubmed/18615556?ordinalpos=21&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Koch J, Manworren R, Clark L, Quinn CT, Buchanan GR, Rogers ZR.  Pilot study of continuous co-infusion of morphine and naloxone in children with
sickle cell pain crisis. Am J Hematol. 2008 Sep;83(9):728-31.
http://www.ncbi.nlm.nih.gov/pubmed/18543345?ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Rovner AJ, Stallings VA, Kawchak DA, Schall JI, Ohene-Frempong K, Zemel BS.  High risk of vitamin d deficiency in children with sickle cell disease.
J Am Diet Assoc. 2008 Sep;108(9):1512-6.
http://www.ncbi.nlm.nih.gov/pubmed/18543345?ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum
Palermo TM, Riley CA, Mitchell BA.  Daily functioning and quality of life in children with sickle cell disease pain: 
relationship with family and neighborhood socioeconomic distress. J Pain. 2008 Sep;9(9):833-40. Epub 2008 Jun 12.
http://www.ncbi.nlm.nih.gov/pubmed/18550443?ordinalpos=35&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_DefaultReportPanel.Pubmed_RVDocSum

August 2008

Raphael JL, Kamdar A, Wang T, Liu H, Mahoney DH, Mueller BU.  
Day hospital versus inpatient management of uncomplicated vaso-occlusive crises in children with sickle cell disease. 
Pediatr Blood Cancer. 2008 Sep;51(3):398-401.
http://www.ncbi.nlm.nih.gov/pubmed/18300322?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 
 Payne KA, Rofail D, Baladi JF, Viala M, Abetz L, Desrosiers MP, Lordan N, Ishak K, Proskorovsky I.  
Iron chelation therapy: Clinical effectiveness, economic burden and quality of life in patients with iron overload. Adv Ther. 2008 Aug 14. 
http://www.ncbi.nlm.nih.gov/pubmed/18704280?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 
Barakat LP, Daniel LC, Patterson CA, Dampier C.  
Quality of life among adolescents with sickle cell disease: mediation of pain by  internalizing symptoms and parenting stress. 
Health Qual Life Outcomes. 2008 Aug 9;6(1):60. http://www.hqlo.com/content/6/1/60
  
Jennings JE, Ramkumar T, Mao J, Boyd J, Castro M, Field JJ, Strunk RC, DeBaun 
MR.  Elevated urinary leukotriene E4 levels are associated with hospitalization for
pain in children with sickle cell disease. Am J Hematol. 2008 Aug;83(8):640-3.
http://www.ncbi.nlm.nih.gov/pubmed/18506703?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 
Villers MS, Jamison MG, De Castro LM, James AH. 
Morbidity associated with sickle cell disease in pregnancy. Am J Obstet Gynecol. 2008 Aug;199(2):125.e1-5. 
http://www.ncbi.nlm.nih.gov/pubmed/18533123?ordinalpos=15&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 
 Newland JA.  Factors influencing independence in adolescents with sickle cell disease.
J Child Adolesc Psychiatr Nurs. 2008 Aug;21(3):177-85.
http://www.ncbi.nlm.nih.gov/pubmed/18667050?ordinalpos=20&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 
 Jenerette CM, Murdaugh C. Testing the theory of self-care management for sickle cell disease.  
Res Nurs Health. 2008 Aug;31(4):355-69.
http://www.ncbi.nlm.nih.gov/pubmed/18247376?ordinalpos=26&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 
Mali P, Ye Z, Hommond HH, Yu X, Lin J, Chen G, Zou J, Cheng L.  
Improved efficiency and pace of generating induced pluripotent stem cells from human adult and fetal fibroblasts. 
Stem Cells. 2008 Aug;26(8):1998-2005. Epub 2008 May 29.
http://stemcells.alphamedpress.org/cgi/content/full/26/8/1998
 
 Bao B, Prasad AS, Beck FW, Snell D, Suneja A, Sarkar FH, Doshi N, Fitzgerald JT, Swerdlow P.  
Zinc supplementation decreases oxidative stress, incidence of infection, and generation of inflammatory cytokines in sickle cell disease patients. 
Transl Res. 2008 Aug;152(2):67-80. Epub 2008 Jul 11. http://www.ncbi.nlm.nih.gov/pubmed/18674741?ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 
Strunk RC, Brown MS, Boyd JH, Bates P, Field JJ, Debaun MR.  
Methacholine challenge in children with sickle cell disease: A case series. Pediatr Pulmonol. 
2008 Jul 31. http://www.ncbi.nlm.nih.gov/pubmed/18671275?ordinalpos=30&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
  
 Mack AK, McGowan Ii VR, Tremonti CK, Ackah D, Barnett C, Machado RF, Gladwin  MT, Kato GJ.  
Sodium nitrite promotes regional blood flow in patients with sickle cell disease: a phase I/II study. 
Br J Haematol. 2008 Jul 30. http://www3.interscience.wiley.com/journal/121358451/abstract?CRETRY=1&SRETRY=0

July 2008

Adams-Graves P, Lamar K, Johnson C, Corley P. Development and validation of SIMS: an instrument for measuring quality of life
of adults with sickle cell disease. Am J Hematol. 2008 Jul;83(7):558-62. http://www3.interscience.wiley.com/journal/117873602/abstract?CRETRY=1&SRETRY=0

Streetly A, Clarke M, Downing M, Farrar L, Foo Y, Hall K, Kemp H, Newbold J, Walsh P, Yates J, Henthorn J.  Implementation of the newborn screening programme for sickle cell disease in England: results for 2003-2005. J Med Screen. 2008;15(1):9-13. http://www.ncbi.nlm.nih.gov/pubmed/18416948?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Zempsky WT, Loiselle KA, McKay K, Blake GL, Hagstrom JN, Schechter NL, Kain ZN. Retrospective evaluation of pain assessment and treatment for acute vasoocclusive episodes in children with sickle cell disease. Pediatr Blood Cancer. 2008 Aug;51(2):265-8. http://www.ncbi.nlm.nih.gov/pubmed/18386784?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Taori KB, Chaudhary RS, Attarde V, Dhakate S, Sheorain V, Nimbalkar P, Wasnik PN. Renal Doppler indices in sickle cell disease: early radiologic predictors of renovascular changes. AJR Am J Roentgenol. 2008 Jul;191(1):239-42. http://www.ncbi.nlm.nih.gov/pubmed/18562752?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Klings ES, Anton Bland D, Rosenman D, Princeton S, Odhiambo A, Li G, Bernard SA, Steinberg MH, Farber HW. Pulmonary arterial hypertension and left-sided heart disease in sickle celldisease: clinical characteristics and association with soluble adhesion molecule expression.cAm J Hematol. 2008 Jul;83(7):547-53. http://www.ncbi.nlm.nih.gov/pubmed/18383329?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Field JJ, Glassberg J, Gilmore A, Howard J, Patankar S, Yan Y, Davies SC, Debaun MR, Strunk RC. Longitudinal analysis of pulmonary function in adults with sickle cell disease. Am J Hematol. 2008 Jul;83(7):574-6. http://www.ncbi.nlm.nih.gov/pubmed/18383325?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Lanzkron S, Strouse JJ, Wilson R, Beach MC, Haywood C, Park H, Witkop C, Bass EB, Segal JB. Systematic review: Hydroxyurea for the treatment of adults with sickle cell disease. Ann Intern Med. 2008 Jun 17;148(12):939-55. Epub 2008 May 5. Full Text http://www.annals.org/cgi/content/full/148/12/939

Brawley OW, Cornelius LJ, Edwards LR, Gamble VN, Green BL, Inturrisi C, James AH, Laraque D, Mendez M, Montoya CJ, Pollock BH, Robinson L, Scholnik AP, Schori M. National Institutes of Health Consensus Development Conference statement: hydroxyurea treatment for sickle cell disease. Ann Intern Med. 2008 Jun 17;148(12):932-8. http://www.annals.org/cgi/content/full/148/12/932

Harban FM, Connor P, Crook R, Bingham R. Cardiopulmonary bypass for surgical correction of congenital heart disease in children with sickle cell disease: a case series. Anaesthesia. 2008 Jun;63(6):648-51. Epub 2008 Feb 29. http://www.ncbi.nlm.nih.gov/pubmed/18312603?ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Alvarez O, Lopez-Mitnik G, Zilleruelo G. Short-term follow-up of patients with sickle cell disease and albuminuria. Pediatr Blood Cancer. 2008 Jun;50(6):1236-9. http://www.ncbi.nlm.nih.gov/pubmed/18293385?ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Singh SA, Koumbourlis AC, Aygun B. Resolution of chronic hypoxemia in pediatric sickle cell patients after treatment with hydroxyurea. Pediatr Blood Cancer. 2008 Jun;50(6):1258-60. http://www.ncbi.nlm.nih.gov/pubmed/18293380?ordinalpos=18&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Dyson, SM; Abuateya, H; Atkin, K; Culley, LA; Dyson, SE; and Rowley, DT (2008) Local authorities and the education 
of young people with sickle cell disorders (SCD) in England International Studies in Sociology of Education 18 (1) 47-60. [
ISSN 0962-1214] doi:10.1080/09620210802196168 http://dx.doi.org/10.1080/09620210802196168

Abuateya, H; Atkin, K; Culley, LA; Dyson, SE and Dyson, SM (2008) Young People with Sickle Cell Disorder and Education: 
A Knowledge Review Diversity in Health and Social Care 5 (2): 123-135. [ISSN 1743-1913]

http://www.ingentaconnect.com/content/rmp/dhsc/2008/00000005/00000002/art00007

June 2008

Raphael JL, Kamdar A, Beavers MB, Mahoney DH, Mueller BU. Treatment of uncomplicated vaso-occlusive crises in children with sickle cell
disease in a day hospital. Pediatr Blood Cancer. 2008 Jul;51(1):82-5.
http://www.ncbi.nlm.nih.gov/pubmed/18383165?ordinalpos=1&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Panepinto JA. Health-related quality of life in sickle cell disease.
Pediatr Blood Cancer. 2008 Jul;51(1):5-9.
http://www.ncbi.nlm.nih.gov/pubmed/18338399?ordinalpos=2&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Aliyu ZY, Gordeuk V, Sachdev V, Babadoko A, Mamman AI, Akpanpe P, Attah E, Suleiman Y, Aliyu N, Yusuf J, Mendelsohn L, Kato GJ, Gladwin MT.
Prevalence and risk factors for pulmonary artery systolic hypertension among sickle cell disease patients in Nigeria.
Am J Hematol. 2008 Jun;83(6):485-90.
http://www.ncbi.nlm.nih.gov/pubmed/18306362?ordinalpos=3&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Barakat LP, Simon K, Schwartz LA, Radcliffe J. Correlates of pain-rating concordance for adolescents with sickle cell disease
and their caregivers. Clin J Pain. 2008 Jun;24(5):438-46.
http://www.ncbi.nlm.nih.gov/pubmed/18496309?ordinalpos=5&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Pannu R, Zhang J, Andraws R, Armani A, Patel P, Mancusi-Ungaro P. Acute Myocardial Infarction in Sickle Cell Disease: A Systematic Review.
Crit Pathw Cardiol. 2008 Jun;7(2):133-138.
http://www.ncbi.nlm.nih.gov/pubmed/18520531?ordinalpos=6&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Caboot JB, Allen JL. Pulmonary complications of sickle cell disease in children.
Curr Opin Pediatr. 2008 Jun;20(3):279-287.
http://www.ncbi.nlm.nih.gov/pubmed/18475096?ordinalpos=7&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Villavicencio K, Ivy D, Cole L, Nuss R. Symptomatic pulmonary hypertension in a child with sickle cell disease.
J Pediatr. 2008 Jun;152(6):879-81.
http://www.ncbi.nlm.nih.gov/pubmed/18492535?ordinalpos=8&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Rees DC, Dick MC, Height SE, O'Driscoll S, Pohl KR, Goss DE, Deane CR. A Simple Index Using Age, Hemoglobin, and Aspartate Transaminase Predicts
Increased Intracerebral Blood Velocity as Measured by Transcranial Doppler Scanning in Children With Sickle Cell Anemia.
Pediatrics. 2008 Jun;121(6):e1628-e1632. Epub 2008 May 19.
http://www.ncbi.nlm.nih.gov/pubmed/18490379?ordinalpos=11&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum
Cartron JP, Elion J. Erythroid adhesion molecules in sickle cell disease: Effect of hydroxyurea.
Transfus Clin Biol. 2008 May 30. [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/18515167?ordinalpos=12&itool=Email.EmailReport.Pubmed_ReportSelector.Pubmed_HVDocSum

May 2008

Alvarez O, Lopez-Mitnik G, Zilleruelo G.  Short-term follow-up of patients with sickle cell disease and albuminuria.
Pediatr Blood Cancer. 2008 Jun;50(6):1236-9.
http://www.ncbi.nlm.nih.gov/pubmed/18293385?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Singh SA, Koumbourlis AC, Aygun B.  Resolution of chronic hypoxemia in pediatric sickle cell patients after treatment
with hydroxyurea. Pediatr Blood Cancer. 2008 Jun;50(6):1258-60.
http://www.ncbi.nlm.nih.gov/pubmed/18293380?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Thein SL.  Genetic modifiers of the beta-haemoglobinopathies.
Br J Haematol. 2008 May;141(3):357-66.
http://www.ncbi.nlm.nih.gov/pubmed/18410570?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Lisowski L, Sadelain M.  Current status of globin gene therapy for the treatment of beta-thalassaemia. Br J Haematol. 2008 May;141(3):335-45.
http://www.ncbi.nlm.nih.gov/pubmed/18410569?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hagar W, Vichinsky E.  Advances in clinical research in sickle cell disease.
Br J Haematol. 2008 May;141(3):346-56. Epub 2008 Mar 12.
http://www.ncbi.nlm.nih.gov/pubmed/18341629?ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Pinto FO, Roberts I.  Cord blood stem cell transplantation for haemoglobinopathies.
Br J Haematol. 2008 May;141(3):309-24. Epub 2008 Feb 26.
http://www.ncbi.nlm.nih.gov/pubmed/18307566?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Ataga KI, Smith WR, De Castro LM, Swerdlow P, Saunthararajah Y, Castro O, Vichinsky E, Kutlar A, Orringer EP, Rigdon GC, Stocker JW; ICA-17043-05
Investigators.  Efficacy and safety of the Gardos channel blocker, senicapoc (ICA-17043), in
patients with sickle cell anemia. Blood. 2008 Apr 15;111(8):3991-7. Epub 2008 Jan 11. 
http://www.ncbi.nlm.nih.gov/pubmed/18192510?ordinalpos=37&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

April 2008

Strouse JJ, Takemoto CM, Keefer JR, Kato GJ, Casella JF.  Corticosteroids and increased risk of readmission after acute chest syndrome in
children with sickle cell disease. Pediatr Blood Cancer. 2008 May;50(5):1006-12.
http://www.ncbi.nlm.nih.gov/pubmed/17849474?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Wood KC, Hsu LL, Gladwin MT.  Sickle cell disease vasculopathy: A state of nitric oxide resistance. Free Radic Biol Med. 2008 Apr 15;44(8):1506-28. Epub 2008 Jan 26.
http://www.ncbi.nlm.nih.gov/pubmed/18261470?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 Zempsky WT, Loiselle KA, McKay K, Blake GL, Hagstrom JN, Schechter NL, Kain ZN.  Retrospective evaluation of pain assessment and treatment for acute vasoocclusive
episodes in children with sickle cell disease. Pediatr Blood Cancer. 2008 Apr 3; 
http://www.ncbi.nlm.nih.gov/pubmed/18386784?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Adewoye AH, Chen TC, Ma Q, McMahon L, Mathieu J, Malabanan A, Steinberg MH, Holick MF.  Sickle cell bone disease: Response to vitamin D and calcium.
Am J Hematol. 2008 Apr;83(4):271-4.
http://www.ncbi.nlm.nih.gov/pubmed/17924548?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Delea TE, Hagiwara M, Thomas SK, Baladi JF, Phatak PD, Coates TD.  Outcomes, utilization, and costs among thalassemia and sickle cell disease
patients receiving deferoxamine therapy in the United States. Am J Hematol. 2008 Apr;83(4):263-70.
http://www.ncbi.nlm.nih.gov/pubmed/17924547?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Saunthararajah Y, Molokie R, Saraf S, Sidhwani S, Gowhari M, Vara S, Lavelle D, DeSimone J.  Clinical effectiveness of decitabine in severe sickle cell disease.
Br J Haematol. 2008 Apr;141(1):126-9. 
http://www.ncbi.nlm.nih.gov/pubmed/18324975?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 Johnson C, Telen MJ.  Adhesion molecules and hydroxyurea in the pathophysiology of sickle cell disease. Haematologica. 2008 Apr;93(4):481-5. 
http://www.haematologica.org/cgi/content/full/93/4/481
Canalli AA, Franco-Penteado CF, Saad ST, Conran N, Costa FF.  Increased adhesive properties of neutrophils in sickle cell disease may be
reversed by pharmacological nitric oxide donation. Haematologica. 2008 Apr;93(4):605-9. Epub 2008 Mar 6.
http://www.ncbi.nlm.nih.gov/pubmed/18326523?ordinalpos=20&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Heeney MM, Ware RE.  Hydroxyurea for children with sickle cell disease. Pediatr Clin North Am. 2008 Apr;55(2):483-501.
http://www.ncbi.nlm.nih.gov/pubmed/18381097?ordinalpos=33&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Field JJ, Austin PF, An P, Yan Y, Debaun MR.  Enuresis Is a Common and Persistent Problem Among Children and Young Adults with  Sickle Cell Anemia.
Urology. 2008 Apr 1; 
http://www.ncbi.nlm.nih.gov/pubmed/18384865?ordinalpos=41&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 Platt OS.  Hydroxyurea for the treatment of sickle cell anemia. N Engl J Med. 2008 Mar 27;358(13):1362-9. Review. 
http://content.nejm.org/cgi/content/extract/358/13/1362
van Beers EJ, van Tuijn CF, Mac Gillavry MR, van der Giessen A, Schnog JJ, Biemond BJ; on behalf of the CURAMA study group. Sickle cell disease-related organ damage occurs irrespective of pain rate: implications for clinical practice.
Haematologica. 2008 Mar 26;
http://www.ncbi.nlm.nih.gov/pubmed/18367483?ordinalpos=48&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Raphael JL, Kamdar A, Beavers MB, Mahoney DH, Mueller BU.  Treatment of uncomplicated vaso-occlusive crises in children with sickle cell
disease in a day hospital. Pediatr Blood Cancer. 2008 Mar 26; 
http://www.ncbi.nlm.nih.gov/pubmed/18383165?ordinalpos=49&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

March 2008

Valrie CR, Gil KM, Redding-Lallinger R, Daeschner C. Brief report: daily mood as a mediator or moderator of the pain-sleep
relationship in children with sickle cell disease. J Pediatr Psychol. 2008 Apr;33(3):317-22. Epub 2007 Aug 8.
http://www.ncbi.nlm.nih.gov/pubmed/17690117?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 McCarville MB, Goodin GS, Fortner G, Li CS, Smeltzer MP, Adams R, Wang W. Evaluation of a comprehensive transcranial doppler screening program for children
with sickle cell anemia.Pediatr Blood Cancer. 2008 Apr;50(4):818-21.
http://www.ncbi.nlm.nih.gov/pubmed/18085672?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Mekontso Dessap A, Leon R, Habibi A, Nzouakou R, Roudot-Thoraval F, Adnot S,Godeau B, Galacteros F, Brun-Buisson C, Brochard L, Maitre B.
 Pulmonary hypertension and cor pulmonale during severe acute chest syndrome in sickle cell disease.
Am J Respir Crit Care Med. 2008 Mar 15;177(6):646-53. Epub 2008 Jan 3.
http://www.ncbi.nlm.nih.gov/pubmed/18174543?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
van den Tweel XW, Hatzmann J, Ensink E, van der Lee JH, Peters M, Fijnvandraat K, Grootenhuis M.
 Quality of life of female caregivers of children with sickle cell disease: a survey.
Haematologica. 2008 Mar 5; 
http://www.ncbi.nlm.nih.gov/pubmed/18322259?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Odièvre MH, Bony V, Benkerrou M, Lapouméroulie C, Alberti C, Ducrocq R, Jacqz-Aigrain E, Elion J, Cartron JP.
 Modulation of erythroid adhesion receptors expression by hydroxyurea in children with sickle cell disease.
Haematologica. 2008 Mar 5; 
http://www.ncbi.nlm.nih.gov/pubmed/18322255?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Lucarelli G, Gaziev J. Advances in the allogeneic transplantation for thalassemia.
Blood Rev. 2008 Mar;22(2):53-63. Epub 2007 Nov 26.
http://www.ncbi.nlm.nih.gov/pubmed/18039551?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 Locock L, Kai J. Parents' experiences of universal screening for haemoglobin disorders: implications for practice in a new genetics era.
Br J Gen Pract. 2008 Mar;58(548):161-8.
http://www.ncbi.nlm.nih.gov/pubmed/18318970?ordinalpos=21&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 Colombatti R, Dalla Pozza LV, Mazzucato M, Sainati L, Pierobon M, Facchin P.
 Hospitalization of children with sickle cell disease in a region with increasing  immigration rates.
Haematologica. 2008 Mar;93(3):463-4.
http://www.ncbi.nlm.nih.gov/pubmed/18310539?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 Geller AK, O'Connor MK.  The Sickle Cell Crisis: A Dilemma in Pain Relief.
Mayo Clin Proc. 2008 Mar;83(3):320-323.
http://www.mayoclinicproceedings.com/Abstract.asp?AID=4623&Abst=Abstract&UID=
Adamkiewicz TV, Silk BJ, Howgate J, Baughman W, Strayhorn G, Sullivan K, Farley MM.
 Effectiveness of the 7-valent pneumococcal conjugate vaccine in children with sickle cell disease in the first decade of life.
Pediatrics. 2008 Mar;121(3):562-9.
http://www.ncbi.nlm.nih.gov/pubmed/18310206?ordinalpos=38&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

February 2008

Darbari DS, van Schaik RH, Capparelli EV, Rana S, McCarter R, van den Anker J. UGT2B7 promoter variant -840G>A contributes to the variability in hepatic clearance of morphine in patients with sickle cell disease. Am J Hematol. 2008 Mar;83(3):200-2. http://www.ncbi.nlm.nih.gov/pubmed/17724700?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Shord SS, Chew L, Villano J. Evaluation of opioid induced nausea and vomiting in sickle cell disease. Am J Hematol. 2008 Mar;83(3):196-9. http://www.ncbi.nlm.nih.gov/pubmed/17724690?ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Darbari DS, Minniti CP, Rana S, van den Anker J. Pharmacogenetics of morphine: Potential implications in sickle cell disease. Am J Hematol. 2008 Mar;83(3):233-6. http://www.ncbi.nlm.nih.gov/pubmed/17722074?ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum]

Appenzeller S, Fattori A, Saad ST, Costallat LT. Systemic lupus erythematosus in patients with sickle cell disease. Clin Rheumatol. 2008 Mar;27(3):359-64. Epub 2007 Nov 14. http://www.ncbi.nlm.nih.gov/pubmed/18000698?ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Lebensburger J, Persons DA. Progress toward safe and effective gene therapy for beta-thalassemia and sickle cell disease. Curr Opin Drug Discov Devel. 2008 Mar;11(2):225-32. http://www.ncbi.nlm.nih.gov/pubmed/18283610?ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

McNaughton-Smith GA, Burns JF, Stocker JW, Rigdon GC, Creech C, Arrington S, Shelton T, de Franceschi L. Novel inhibitors of the gardos channel for the treatment of sickle cell disease. J Med Chem. 2008 Feb 28;51(4):976-82. Epub 2008 Jan 31. http://www.ncbi.nlm.nih.gov/pubmed/18232633?ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Singh SA, Koumbourlis AC, Aygun B. Resolution of chronic hypoxemia in pediatric sickle cell patients after treatment with hydroxyurea.
Pediatr Blood Cancer. 2008 Feb 21; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/18293380?ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Jenerette CM, Murdaugh C. Testing the theory of self-care management for sickle cell disease. Res Nurs Health. 2008 Feb 4; http://www.ncbi.nlm.nih.gov/pubmed/18247376?ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Solomon LR. Treatment and prevention of pain due to vaso-occlusive crises in adults with sickle cell disease: an educational void. Blood. 2008 Feb 1;111(3):997-1003. Epub 2007 Oct 16. http://www.ncbi.nlm.nih.gov/pubmed/17940207?ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Frei-Jones MJ, Baxter AL, Rogers ZR, Buchanan GR. Vaso-occlusive episodes in older children with sickle cell disease: emergency department management and pain assessment. J Pediatr. 2008 Feb;152(2):281-5. Epub 2007 Oct 24.
http://www.ncbi.nlm.nih.gov/pubmed/18206703?ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hankins JS, Helton KJ, McCarville MB, Li CS, Wang WC, Ware RE. Preservation of spleen and brain function in children with sickle cell anemia treated with hydroxyurea. Pediatr Blood Cancer. 2008 Feb;50(2):293-7. http://www.ncbi.nlm.nih.gov/pubmed/17554794?ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hines P, Dover GJ, Resar LM. Pulsed-dosing with oral sodium phenylbutyrate increases hemoglobin F in a patient with sickle cell anemia.
Pediatr Blood Cancer. 2008 Feb;50(2):357-9. http://www.ncbi.nlm.nih.gov/pubmed/17253639?ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Levenson JL, McClish DK, Dahman BA, Bovbjerg VE, de A Citero V, Penberthy LT, Aisiku IP, Roberts JD, Roseff SD, Smith WR. Depression and anxiety in adults with sickle cell disease: the PiSCES project. Psychosom Med. 2008 Feb;70(2):192-6. Epub 2007 Dec 24. http://www.ncbi.nlm.nih.gov/pubmed/18158366?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

January 2008

King AA, Noetzel M, White DA, McKinstry RC, Debaun MR.  Blood transfusion therapy is feasible in a clinical trial setting in children
with sickle cell disease and silent cerebral infarcts. Pediatr Blood Cancer. 2008 Mar;50(3):599-602.
 http://www.ncbi.nlm.nih.gov/pubmed/17985350?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
 Halabi-Tawil M, Lionnet F, Girot R, Bachmeyer C, Lévy PP, Aractingi S. Sickle cell leg ulcers: a frequently disabling complication and a marker of
severity. Br J Dermatol. 2008 Feb;158(2):339-44. Epub 2007 Nov 28.
http://www.ncbi.nlm.nih.gov/pubmed/18047512?ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Hernigou P, Zilber S, Filippini P, Mathieu G, Poignard A, Galacteros F.  Total THA in Adult Osteonecrosis Related to Sickle Cell Disease.
Clin Orthop Relat Res. 2008 Feb;466(2):300-8. Epub 2008 Jan 10.
http://www.ncbi.nlm.nih.gov/pubmed/18196410?ordinalpos=14&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Frei-Jones MJ, Baxter AL, Rogers ZR, Buchanan GR.  Vaso-occlusive episodes in older children with sickle cell disease: emergency
department management and pain assessment. J Pediatr. 2008 Feb;152(2):281-5. Epub 2007 Oct 24.
http://www.ncbi.nlm.nih.gov/pubmed/18206703?ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Smiley D, Dagogo-Jack S, Umpierrez G. Therapy insight: metabolic and endocrine disorders in sickle cell disease.
Nat Clin Pract Endocrinol Metab. 2008 Feb;4(2):102-9.
http://www.ncbi.nlm.nih.gov/pubmed/18212812?ordinalpos=19&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Barnett CF, Hsue PY, Machado RF. Pulmonary hypertension: an increasingly recognized complication of hereditary
hemolytic anemias and HIV infection. JAMA. 2008 Jan 23;299(3):324-31. Review.
http://www.ncbi.nlm.nih.gov/pubmed/18212317?ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Kavanagh PL, Wang CJ, Therrell BL, Sprinz PG, Bauchner H. Communication of positive newborn screening results for sickle cell disease and
sickle cell trait: Variation across states.Am J Med Genet C Semin Med Genet. 2008 Jan 15;148C(1):15-22 [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/pubmed/18200513?ordinalpos=35&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Smith WR, Penberthy LT, Bovbjerg VE, McClish DK, Roberts JD, Dahman B, Aisiku IP, Levenson JL, Roseff SD.
 Daily assessment of pain in adults with sickle cell disease.Ann Intern Med. 2008 Jan 15;148(2):94-101.
http://www.ncbi.nlm.nih.gov/pubmed/18195334?ordinalpos=36&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

December 2007

Jastaniah W, Harmatz P, Pakbaz Z, Fischer R, Vichinsky E, Walters MC. Transfusional iron burden and liver toxicity after bone marrow transplantation
for acute myelogenous leukemia and hemoglobinopathies.Pediatr Blood Cancer. 2008 Feb;50(2):319-24.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17557314&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hankins JS, Helton KJ, McCarville MB, Li CS, Wang WC, Ware RE. Preservation of spleen and brain function in children with sickle cell anemiatre ated with hydroxyurea. Pediatr Blood Cancer. 2008 Feb;50(2):293-7.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17554794&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hines P, Dover GJ, Resar LM. Pulsed-dosing with oral sodium phenylbutyrate increases hemoglobin F in a patient with sickle cell anemia. Pediatr Blood Cancer. 2008 Feb;50(2):357-9.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17253639&ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Spivey JF, Uong EC, Strunk R, Boslaugh SE, DeBaun MR. Low daytime pulse oximetry reading is associated with nocturnal desaturation and obstructive sleep apnea in children with sickle cell anemia. Pediatr Blood Cancer. 2008 Feb;50(2):359-62.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17072857&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hagar RW, Michlitsch JG, Gardner J, Vichinsky EP, Morris CR. Clinical differences between children and adults with pulmonary hypertension and sickle cell disease. Br J Haematol. 2008 Jan;140(1):104-12. Epub 2007 Oct 3.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17916102&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Karam LB, Disco D, Jackson SM, Lewin D, McKie V, Baker RD, Baker SS, Laver JH, Nietert PJ, Abboud MR. Liver biopsy results in patients with sickle cell disease on chronic transfusions: poor correlation with ferritin levels. Pediatr Blood Cancer. 2008 Jan;50(1):62-5.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17457853&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Shankar SM, Arbogast PG, Mitchel E, Ding H, Wang WC, Griffin MR. Impact of proximity to comprehensive sickle cell center on utilization of healthcare services among children with sickle cell disease. Pediatr Blood Cancer. 2008 Jan;50(1):66-71.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=16998856&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Pawar SS, Panepinto JA, Brousseau DC. The effect of acute pain crisis on exhaled nitric oxide levels in children with sickle cell disease. Pediatr Blood Cancer. 2008 Jan;50(1):111-3.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=16619223&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Citero Vde A, Levenson JL, McClish DK, Bovbjerg VE, Cole PL, Dahman BA,Penberthy LT, Aisiku IP, Roseff SD, Smith WR. The role of catastrophizing in sickle cell disease--the PiSCES project. Pain. 2007 Dec 15;133(1-3):39-46. Epub 2007 Apr 3.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17408858&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hanna J, Wernig M, Markoulaki S, Sun CW, Meissner A, Cassady JP, Beard C, Brambrink T, Wu LC, Townes TM, Jaenisch R. Treatment of Sickle Cell Anemia Mouse Model with iPS Cells Generated from Autologous Skin. Science. 2007 Dec 6; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=18063756&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Bhatia M, Walters MC. Hematopoietic cell transplantation for thalassemia and sickle cell disease: past, present and future. Bone Marrow Transplant. 2007 Dec 3; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=18059330&ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

November 2007

Robert J. Adams, MS, MD Big Strokes in Small Persons Arch Neurol. 2007;64(11):1567-1574.  http://archneur.ama-assn.org/cgi/content/short/64/11/1567

Shawn M. Bediako, Annette R. Lavender and Zahida Yasin Racial Centrality and Health Care Use Among African American Adults With Sickle Cell Disease Journal of Black Psychology 2007; 33; 422  http://jbp.sagepub.com/cgi/content/abstract/33/4/422

Aslan M, Freeman BA. Redox-dependent impairment of vascular function in sickle cell disease.Free Radic Biol Med. 2007 Dec 1;43(11):1469-83. Epub 2007 Aug 31. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17964418&ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Inati A, Jradi O, Tarabay H, Moallem H, Rachkidi Y, El Accaoui R, Isma'eel H, Wehbe R, Mfarrej BG, Dabbous I, Taher A. Sickle cell disease: the Lebanese experience. Int J Lab Hematol. 2007 Dec;29(6):399-408. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17988293&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Ozbek OY, Malbora B, Sen N, Yazici AC, Ozyurek E, Ozbek N. Airway hyperreactivity detected by methacholine challenge in children with sickle
cell disease. Pediatr Pulmonol. 2007 Dec;42(12):1187-92. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17960821&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Appenzeller S, Fattori A, Saad ST, Costallat LT. Systemic lupus erythematosus in patients with sickle cell disease.Clin Rheumatol. 2007 Nov 14; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=18000698&ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hankins JS, Wynn LW, Brugnara C, Hillery CA, Li CS, Wang WC. Phase I study of magnesium pidolate in combination with hydroxycarbamide for children with sickle cell anaemia.Br J Haematol. 2007 Nov 7; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17991298&ordinalpos=16&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Shenoy S. Has stem cell transplantation come of age in the treatment of sickle cell disease? Bone Marrow Transplant. 2007 Nov;40(9):813-21. Epub 2007 Aug 20. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17704797&ordinalpos=22&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Tripette J, Hardy-Dessources MD, Sara F, Montout-Hedreville M, Saint-Martin C, Hue O, Connes P. Does Repeated and Heavy Exercise Impair Blood Rheology in Carriers of Sickle Cell Trait? Clin J Sport Med. 2007 Nov;17(6):465-470. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17993789&ordinalpos=25&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Marlin L, Sara F, Antoine-Jonville S, Connes P, Etienne-Julan M, Hue O. Ventilatory and lactic thresholds in subjects with sickle cell trait. Int J Sports Med. 2007 Nov;28(11):916-20. Epub 2007 May 11. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17497586&ordinalpos=28&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Lionnet F, Bachmeyer C, Sloma I, Rossier A, Thioliere B, Maier M, Grateau G, Girot R, Cadranel J. Tuberculosis in adult patients with sickle cell disease.
J Infect. 2007 Nov;55(5):439-44. Epub 2007 Aug 22. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17714789&ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Schatz J, Roberts CW. Neurobehavioral impact of sickle cell disease in early childhood. J Int Neuropsychol Soc. 2007 Nov;13(6):933-43. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17942011&ordinalpos=30&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Barakat LP, Patterson CA, Weinberger BS, Simon K, Gonzalez ER, Dampier C. A Prospective Study of the Role of Coping and Family Functioning in Health
Outcomes for Adolescents With Sickle Cell Disease. J Pediatr Hematol Oncol. 2007 Nov;29(11):752-760.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17984693&ordinalpos=33&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

October 2007

Dyson, SM; Atkin, K; Culley, LA and Dyson, SE (2007) The educational experiences of young people with sickle cell disorder: a commentary on existing literature. Disability and Society 22 (6): 581-594. http://www.informaworld.com/openurl?genre=article&issn=0968-7599&volume=22&issue=6&spage=581

Lee SP, Ataga KI, Zayed M, Manganello JM, Orringer EP, Phillips DR, Parise LV. Phase I study of eptifibatide in patients with sickle cell anaemia. Br J Haematol. 2007 Oct 3;  http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17916103&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Lavelle D, Chin J, Vaitkus K, Redkar S, Phiasivongsa P, Tang C, Will R, Hankewych M, Roxas B, Singh M, Saunthararajah Y, Desimone J. Oral decitabine reactivates expression of the methylated gamma-globin gene in Papio anubis. Am J Hematol. 2007 Nov;82(11):981-5. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17696208&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

van Beers EJ, van Tuijn CF, Nieuwkerk PT, Friederich PW, Vranken JH, Biemond BJ. Patient-controlled analgesia versus continuous infusion of morphine during vaso-occlusive crisis in sickle cell disease, a randomized controlled trial. Am J Hematol. 2007 Nov;82(11):955-60. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17617790&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Wu CJ, Gladwin M, Tisdale J, Hsieh M, Law T, Biernacki M, Rogers S, Wang X, Walters M, Zahrieh D, Antin JH, Ritz J, Krishnamurti L. Mixed haematopoietic chimerism for sickle cell disease prevents intravascular haemolysis. Br J Haematol. 2007 Nov;139(3):504-7. No abstract available. 

 McLeod BC. Evidence based therapeutic apheresis in autoimmune and other hemolytic anemias. Curr Opin Hematol. 2007 Nov;14(6):647-54. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17898570&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Klings ES. Pulmonary hypertension of sickle cell disease: More than just another lung disease. Am J Hematol. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17924550&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

H Adewoye A, C Chen T, Ma Q, McMahon L, Mathieu J, Malabanan A, H Steinberg M, F Holick M. Sickle cell bone disease: Response to vitamin D and calcium. Am J Hematol. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17924548&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Delea TE, Hagiwara M, Thomas SK, Baladi JF, Phatak PD, Coates TD. Outcomes, utilization, and costs among thalassemia and sickle cell disease patients receiving deferoxamine therapy in the United States. Am J Hematol. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17924547&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

 Deane C, Goss D, O'driscoll S, Melllor S, Pohl K, Dick MC, Height SE, Rees DC. Transcranial Doppler Scanning and the Assessment of Stroke Risk in Children with HbSC disease. Arch Dis Child. 2007 Oct 9; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17925326&ordinalpos=11&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

 Hagar RW, Michlitsch JG, Gardner J, Vichinsky EP, Morris CR. Clinical differences between children and adults with pulmonary hypertension and sickle cell disease. Br J Haematol. 2007 Oct 3; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17916102&ordinalpos=15&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Marlin L, Connes P, Antoine-Jonville S, Tripette J, Montout-Hedreville M, Sanouiller A, Etienne-Julan M, Hue O. Cardiorespiratory responses during three repeated incremental exercise tests in sickle cell trait carriers. Eur J Appl Physiol. 2007 Oct 2; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17909842&ordinalpos=17&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Quinn CT, Lee NJ, Shull EP, Ahmad N, Rogers ZR, Buchanan GR. Prediction of adverse outcomes in children with sickle cell anemia: a study of the Dallas Newborn Cohort. Blood. 2007 Oct 1; http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17909076&ordinalpos=21&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Bernaudin F, Socie G, Kuentz M, Chevret S, Duval M, Bertrand Y, Vannier JP, Yakouben K, Thuret I, Bordigoni P, Fischer A, Lutz P, Stephan JL, Dhedin N, Plouvier E, Margueritte G, Bories D, Verlhac S, Esperou H, Coic L, Vernant JP, Gluckman E; SFGM-TC. Long-term results of related myeloablative stem-cell transplantation to cure sickle cell disease. Blood. 2007 Oct 1;110(7):2749-56. Epub 2007 Jul 2. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17606762&ordinalpos=23&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Sebastiani P, Nolan VG, Baldwin CT, Abad-Grau MM, Wang L, Adewoye AH, McMahon LC, Farrer LA, Taylor JG 4th, Kato GJ, Gladwin MT, Steinberg MH. A network model to predict the risk of death in sickle cell disease. Blood. 2007 Oct 1;110(7):2727-35. Epub 2007 Jun 28. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17600133&ordinalpos=24&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Vasavda N, Ulug P, Kondaveeti S, Ramasamy K, Sugai T, Cheung G, Rees DC, Awogbade M, Bannister S, Cunningham J, Menzel S, Thein SL. Circulating DNA: a potential marker of sickle cell crisis. Br J Haematol. 2007 Oct;139(2):331-6. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17897311&ordinalpos=26&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Vekilov PG. Sickle-cell haemoglobin polymerization: is it the primary pathogenic event of sickle-cell anaemia? Br J Haematol. 2007 Oct;139(2):173-84. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17897293&ordinalpos=27&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

September 2007

The National Toxicology Program (NTP) Center for the Evaluation of Risks to Human Reproduction (CERHR) convened an expert panel on January 24–26, 2007, in Alexandria, Virginia to evaluate hydroxyurea. The report in full text is available at 
http://cerhr.niehs.nih.gov/chemicals/hydroxyurea/hydroxyurea-eval.html

Ataga KI, Cappellini MD, Rachmilewitz EA. beta-Thalassaemia and sickle cell anaemia as paradigms of hypercoagulability. Br J Haematol. 2007 Oct;139(1):3-13.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17854302&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Villagra J, Shiva S, Hunter LA, Machado RF, Gladwin MT, Kato GJ. Platelet activation in patients with sickle disease, hemolysis-associated pulmonary hypertension, and nitric oxide scavenging by cell-free hemoglobin.
Blood. 2007 Sep 15;110(6):2166-72. Epub 2007 May 29.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17536019&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Morris CR, Suh JH, Hagar W, Larkin S, Bland DA, Steinberg MH, Vichinsky EP,Shigenaga M, Ames B, Kuypers FA, Klings ES. Erythrocyte glutamine depletion, altered redox environment, and pulmonary
hypertension in sickle cell disease. Blood. 2007 Sep 11; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17848621&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Strouse JJ, Takemoto CM, Keefer JR, Kato GJ, Casella JF. Corticosteroids and increased risk of readmission after acute chest syndrome in children with sickle cell disease.
Pediatr Blood Cancer. 2007 Sep 11; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17849474&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Traina F, Jorge SG, Yamanaka A, de Meirelles LR, Costa FF, Saad ST. Chronic Liver Abnormalities in Sickle Cell Disease: A Clinicopathological Study
in 70 Living Patients.Acta Haematol. 2007 Sep 3;118(3):129-135 [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17785963&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Mazumdar M, Heeney MM, Sox CM, Lieu TA. Preventing Stroke Among Children With Sickle Cell Anemia: An Analysis of Strategies That Involve Transcranial Doppler Testing and Chronic Transfusion.
Pediatrics. 2007 Sep 3; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17768181&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Sylvester K, Patey R, Rafferty G, Rees D, Thein S, Greenough A.  Peak expiratory flow in Afro-Caribbean children with and without sickle cell
anaemia. Acta Paediatr. 2007 Sep;96(9):1308-10. Epub 2007 Jul 31.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17666101&ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Krejza J, Rudzinski W, Pawlak MA, Tomaszewski M, Ichord R, Kwiatkowski J, Gor D, Melhem ER.  Angle-Corrected Imaging Transcranial Doppler Sonography versus Imaging and
Nonimaging Transcranial Doppler Sonography in Children with Sickle Cell Disease. AJNR Am J Neuroradiol. 2007 Sep;28(8):1613-8.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17846223&ordinalpos=13&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Pakbaz Z, Fischer R, Fung E, Nielsen P, Harmatz P, Vichinsky E.  Serum ferritin underestimates liver iron concentration in transfusion independent
thalassemia patients as compared to regularly transfused thalassemia and sickle cell patients. Pediatr Blood Cancer. 2007 Sep;49(3):329-32.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17554789&ordinalpos=29&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Morris, C Hemolysis-Associated Pulmonary Hypertension in Sickle Cell Disease: Global Disruption of the Arginine-Nitric Oxide Pathway Current Hypertension Reviews, Volume 3, Number 3, August 2007 , pp. 223-230(8)  http://www.ingentaconnect.com/content/ben/chyr/2007/00000003/00000003/art00009

August 2007

 Galkin, O., Nagel, R. L. & Vekilov, P. G. (2007). The kinetics of nucleation and growth of sickle cell hemoglobin fibers. J. Mol. Biol. 365,
425-439.Full Text PDF 

Pan, W., Galkin, O., Filobelo, L., Nagel, R. L. & Vekilov, P. G. (2007). Metastable mesoscopic clusters in solutions of sickle cell hemoglobin.
Biophys. J. 92, 267-277. Full Text PDF  

Galkin, O., Pan, W., Filobelo, L., Hirsch, R. E., Nagel, R. L. & Vekilov, P. G. (2007). Two-step mechanism of homogeneous nucleation of sickle cell
hemoglobin polymers. Biophys. J. 92, 902-913. Full Text PDF 

Creary, M., Williamson, D, Kulkarni, R.  Journal of Women's Health. 2007, 16(5): 575-582. doi:10.1089/jwh.2007.CDC4. http://www.liebertonline.com/doi/abs/10.1089/jwh.2007.CDC4

Pakbaz Z, Fischer R, Fung E, Nielsen P, Harmatz P, Vichinsky E.  Serum ferritin underestimates liver iron concentration in transfusion independent
thalassemia patients as compared to regularly transfused thalassemia and sickle cell patients.
Pediatr Blood Cancer. 2007 Sep;49(3):329-32. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17554789&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Brambilla DJ, Miller ST, Adams RJ.  Intra-individual variation in blood flow velocities in cerebral arteries of children with sickle cell disease.
Pediatr Blood Cancer. 2007 Sep;49(3):318-22. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17243135&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
 Adamkiewicz TV, Szabolcs P, Haight A, Baker KS, Staba S, Kedar A, Chiang KY, Krishnamurti L, Boyer MW, Kurtzberg J, Wagner JE, Wingard JR, Yeager AM.
 Unrelated cord blood transplantation in children with sickle cell disease: Review of four-center experience. Pediatr Transplant. 2007 Sep;11(6):641-4.  
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17663687&ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Sylvester KP, Patey RA, Kassim Z, Rafferty GF, Rees D, Thein SL, Greenough A.  Lung gas transfer in children with sickle cell anaemia. Respir Physiol Neurobiol. 2007 Aug 15;158(1):70-4. Epub 2007 Apr 8.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17512804&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
 Hanchard N, Elzein A, Trafford C, Rockett K, Pinder M, Jallow M, Harding R,Kwiatkowski D, McKenzie C.  Classical beta-globin sickle haplotypes exhibit a high degree of long-range
haplotype similarity in African and Afro-Caribbean populations. BMC Genet. 2007 Aug 10;8(1):52 http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17688704&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Onyekwere OC, Campbell A, Teshome M, Onyeagoro S, Sylvan C, Akintilo A, Hutchinson S, Ensing G, Gaskin P, Kato G, Rana S, Kwagyan J, Gordeuk V, Williams 
J, Castro O.  Pulmonary Hypertension in Children and Adolescents with Sickle Cell Disease. Pediatr Cardiol. 2007 Aug 7; 
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17680298&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Crawford MW, Shichor T, Engelhardt T, Adamson G, Bell D, Carmichael FJ, Kim PC.  The Novel Hemoglobin-based Oxygen Carrier HRC 101 Improves Survival in Murine
Sickle Cell Disease. Anesthesiology. 2007 Aug;107(2):281-287.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17667573&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Zimmerman SA, Schultz WH, Burgett S, Mortier NA, Ware RE.  Hydroxyurea therapy lowers transcranial Doppler flow velocities in children with 
sickle cell anemia. Blood. 2007 Aug 1;110(3):1043-7. Epub 2007 Apr 11.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17429008&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline
Austin H, Key NS, Benson JM, Lally C, Dowling NF, Whitsett C, Hooper WC.  Sickle cell trait and the risk of venous thromboembolism among blacks.
Blood. 2007 Aug 1;110(3):908-12. Epub 2007 Apr 4.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17409269&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVMedline

July 2007

Knox-Macaulay HH, Ahmed MM, Gravell D, Al-Kindi S, Ganesh A. Sickle cell-haemoglobin E (HbSE) compound heterozygosity: a clinical and
haematological study.Int J Lab Hematol. 2007 Aug;29(4):292-301. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17617080&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Valrie CR, Gil KM, Redding-Lallinger R, Daeschner C. Brief report: sleep in children with sickle cell disease: an analysis of daily
diaries utilizing multilevel models.J Pediatr Psychol. 2007 Aug;32(7):857-61. Epub 2007 Mar 30.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17400602&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Rahimi Z, Vaisi-Raygani A, Nagel RL, Muniz A. Thrombophilic mutations among Southern Iranian patients with sickle cell disease:
high prevalence of factor V Leiden. J Thromb Thrombolysis. 2007 Jul 11;
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17619828&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
van Beers EJ, van Tuijn CF, Nieuwkerk PT, Friederich PW, Vranken JH, Biemond BJ. Patient-controlled analgesia versus continuous infusion of morphine during
vaso-occlusive crisis in sickle cell disease, a randomized controlled trial.Am J Hematol. 2007 Jul 6; [Epub ahead of print]
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17617790&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Howe AS, Boden BP. Heat-Related Illness in Athletes.Am J Sports Med. 2007 Jul 3;
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17609528&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Bernaudin F, Socie G, Kuentz M, Chevret S, Duval M, Bertrand Y, Vannier JP,Yakouben K, Thuret I, Bordigoni P, Fischer A, Lutz P, Stephan JL, Dhedin N,
Plouvier E, Margueritte G, Bories D, Verlhac S, Esperou H, Coic L, Vernant JP,Gluckman E. Long-term results of related, myeloablative stem cell transplantation to cure
sickle cell disease.Blood. 2007 Jul 2; 
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17606762&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Telfer P, Coen P, Chakravorty S, Wilkey O, Evans J, Newell H, Smalling B, Amos R, Stephens A, Rogers D, Kirkham F.
 Clinical outcomes in children with sickle cell disease living in England: a neonatal cohort in East London. Haematologica. 2007 Jul;92(7):905-12.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17606440&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Niebanck AE, Pollock AN, Smith-Whitley K, Raffini LJ, Zimmerman RA, Ohene-Frempong K, Kwiatkowski JL. Headache in children with sickle cell disease: prevalence and associated factors.
J Pediatr. 2007 Jul;151(1):67-72, 72.e1.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17586193&ordinalpos=9&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum
Ejindu VC, Hine AL, Mashayekhi M, Shorvon PJ, Misra RR. Musculoskeletal manifestations of sickle cell disease.Radiographics. 2007 Jul-Aug;27(4):1005-21.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17620464&ordinalpos=10&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

June 2007

Dyson, SM; Cochran, F; Culley, LA; Dyson, SE, Kennefick, A; Kirkham, M; Morris, P; Sutton, F; and Squire, P (2007) Observation and Interview Findings from the Ethnicity Questions and Antenatal Screening for Sickle Cell/Thalassaemia [EQUANS] Study. Critical Public Health 17 (1): 31-43. ISSN 0958-1596 http://www.informaworld.com/smpp/content~content=a773302146~db=all~order=page 

Tubman VN, Bennett CM, Luo HY, Chui DH, Heeney MM. Sickle cell disease caused by Hb S/Quebec-CHORI: Treatment with hydroxyurea and
response. Pediatr Blood Cancer. 2007 Aug;49(2):207-10. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17551985&ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Aprelev A, Weng W, Zakharov M, Rotter M, Yosmanovich D, Kwong S, Briehl RW, Ferrone FA. Metastable polymerization of sickle hemoglobin in droplets. J Mol Biol. 2007 Jun 22;369(5):1170-4. Epub 2007 Apr 19. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17493634&ordinalpos=2&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Anthi A, Machado RF, Jison ML, Taveira-Dasilva AM, Rubin LJ, Hunter L, Hunter CJ, Coles W, Nichols J, Avila NA, Sachdev V, Chen CC, Gladwin MT.
Hemodynamic and functional assessment of patients with sickle cell disease and pulmonary hypertension. Am J Respir Crit Care Med. 2007 Jun 15;175(12):1272-9. Epub 2007 Mar 22. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17379852&ordinalpos=3&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hankins J, Hinds P, Day S, Carroll Y, Li CS, Garvie P, Wang W. Therapy preference and decision-making among patients with severe sickle cell
anemia and their families. Pediatr Blood Cancer. 2007 Jun 15;48(7):705-10. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=16732581&ordinalpos=4&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Odhiambo A, Perlman DH, Huang H, Costello CE, Farber HW, Steinberg MH, McComb ME, Klings ES. Identification of oxidative post-translational modification of serum albumin in patients with idiopathic pulmonary arterial hypertension and pulmonary hypertension of sickle cell anemia.
Rapid Commun Mass Spectrom. 2007 Jun 14;21(14):2195-2203 [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17569101&ordinalpos=5&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Zhu J, Kren BT, Park CW, Bilgim R, Wong PY, Steer CJ. Erythroid-Specific Expression of beta-Globin by the Sleeping Beauty Transposon
for Sickle Cell Disease. Biochemistry. 2007 Jun 12;46(23):6844-58. Epub 2007 May 18. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17508724&ordinalpos=6&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Hankins JS, Helton KJ, McCarville MB, Li CS, Wang WC, Ware RE. Preservation of spleen and brain function in children with sickle cell anemia
treated with hydroxyurea. Pediatr Blood Cancer. 2007 Jun 6; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17554794&ordinalpos=7&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Graham JK, Mosunjac M, Hanzlick RL, Mosunjac M. Sickle Cell Lung Disease and Sudden Death: A Retrospective/Prospective Study of
21 Autopsy Cases and Literature Review. Am J Forensic Med Pathol. 2007 Jun;28(2):168-172.
http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17525572&ordinalpos=8&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

Adewoye AH, Nolan V, McMahon L, Ma Q, Steinberg MH. Effectiveness of a dedicated day hospital for management of acute sickle cell
pain. Haematologica. 2007 Jun;92(6):854-5. http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=ShowDetailView&TermToSearch=17550862&ordinalpos=12&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum

 

May 2007

Hankins J, Hinds P, Day S, Carroll Y, Li CS, Garvie P, Wang W.  Therapy preference and decision-making among patients with severe sickle cell
anemia and their families&. Pediatr Blood Cancer. 2007 Jun 15;48(7):705-10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16732581&query_hl=1&itool=pubmed_DocSum

Zilberman MV, Du W, Das S, Sarnaik SA.  Evaluation of left ventricular diastolic function in pediatric sickle cell
disease patients.Am J Hematol. 2007 Jun;82(6):433-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17266053&query_hl=1&itool=pubmed_DocSum

Panepinto JA, Walters MC, Carreras J, Marsh J, Bredeson CN, Gale RP, Hale GA, Horan J, Hows JM, Klein JP, Pasquini R, Roberts I, Sullivan K, Eapen M, Ferster A; On behalf of the Non-Malignant Marrow Disorders Working Committee,  Center for International Blood and Marrow Transplant Research. 
 Matched-related donor transplantation for sickle cell disease: report from the Center for International Blood and Transplant Research.
Br J Haematol. 2007 Jun;137(5):479-85. Epub 2007 Apr 24. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17459050&query_hl=1&itool=pubmed_DocSum

Halasa NB, Shankar SM, Talbot TR, Arbogast PG, Mitchel EF, Wang WC,Schaffner W, Craig AS, Griffin MR. 
 Incidence of invasive pneumococcal disease among individuals with sickle cell disease before and after the introduction of the pneumococcal conjugate vaccine.Clin Infect Dis. 2007 Jun 1;44(11):1428-33. Epub 2007 Apr 18. Full Text http://www.journals.uchicago.edu/CID/journal/issues/v44n11/41426/41426.html

Koumbourlis AC, Lee DJ, Lee A. Longitudinal changes in lung function and somatic growth in children with
sickle cell disease.Pediatr Pulmonol. 2007 Jun;42(6):483-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17469146&query_hl=1&itool=pubmed_DocSum

Akgul F, Yalcin F, Seyfeli E, Ucar E, Karazincir S, Balci A, Gali E.  Pulmonary Hypertension in Sickle-Cell Disease: Comorbidities and
Echocardiographic Findings. Acta Haematol. 2007 May 14;118(1):53-60 [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17505130&query_hl=1&itool=pubmed_DocSum

Marlin L, Sara F, Antoine-Jonville S, Connes P, Etienne-Julan M, Hue O.  Ventilatory and Lactic Thresholds in Subjects with Sickle Cell Trait.
Int J Sports Med. 2007 May 11; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17497586&query_hl=1&itool=pubmed_DocSum

Yu J, Heck S, Yazdanbakhsh K.  Prevention of red cell alloimmunization by CD25 regulatory T cells in mouse
models. Am J Hematol. 2007 May 9; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17492644&query_hl=1&itool=pubmed_DocSum

Rivera A.  Reduced sickle erythrocyte dehydration in vivo by endothelin-1 receptor antagonists.
Am J Physiol Cell Physiol. 2007 May 9; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17494628&query_hl=1&itool=pubmed_DocSum

Finnegan EM, Barabino GA, Liu XD, Chang HY, Jonczyk A, Kaul DK.  Small-Molecule Cyclic {alpha}V{beta}3 Antagonists Inhibit Sickle Red Cell
Adhesion to Vascular Endothelium and Vaso-Occlusion. Am J Physiol Heart Circ Physiol. 2007 May 4; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17483236&query_hl=1&itool=pubmed_DocSum

Goers T, Panepinto J, Debaun M, Blinder M, Foglia R, Oldham KT, Field JJ.  Laparoscopic versus open abdominal surgery in children with sickle cell disease
is associated with a shorter hospital stay. Pediatr Blood Cancer. 2007 May 4; [Epub ahead of print]  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17480009&query_hl=1&itool=pubmed_DocSum

Tanabe P, Myers R, Zosel A, Brice J, Ansari AH, Evans J, Martinovich Z, Todd KH, Paice JA. 
 Emergency department management of acute pain episodes in sickle cell disease. Acad Emerg Med. 2007 May;14(5):419-25. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17389246&query_hl=1&itool=pubmed_DocSum

Mitchell MJ, Lemanek K, Palermo TM, Crosby LE, Nichols A, Powers SW.  Parent perspectives on pain management, coping, and family functioning in
pediatric sickle cell disease. Clin Pediatr (Phila). 2007 May;46(4):311-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17475988&query_hl=1&itool=pubmed_DocSum

Gustafson SL, Gettig EA, Watt-Morse M, Krishnamurti L.  Health beliefs among African American women regarding genetic testing and
counseling for sickle cell disease.Genet Med. 2007 May;9(5):303-310. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17505208&query_hl=1&itool=pubmed_DocSum

Kawchak DA, Schall JI, Zemel BS, Ohene-Frempong K, Stallings VA.  Adequacy of dietary intake declines with age in children with sickle cell
disease.J Am Diet Assoc. 2007 May;107(5):843-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17467383&query_hl=1&itool=pubmed_DocSum

Nelson SC, Adade BB, McDonough EA, Moquist KL, Hennessy JM.  High Prevalence of Pulmonary Hypertension in Children With Sickle Cell Disease.
J Pediatr Hematol Oncol. 2007 May;29(5):334-337. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17483714&query_hl=1&itool=pubmed_DocSum

Josephson CD, Su LL, Hillyer KL, Hillyer CD. Transfusion in the patient with sickle cell disease: a critical review of the literature and transfusion guidelines.Transfus Med Rev. 2007 Apr;21(2):118-33  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17397762&query_hl=21&itool=pubmed_docsum

April 2007
1: Wang WC. The pathophysiology, prevention, and treatment of stroke in sickle cell
disease.Curr Opin Hematol. 2007 May;14(3):191-197. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17414206&query_hl=12&itool=pubmed_DocSum

2: Howard SC, Wilimas JA, Flores A, Pacheco C, de Reyes G, Machin S, Svarch E,
Navarrete M, Nieves R, Rodriguez H, Masera G. Treatment for children with severe aplastic anemia and sickle cell disease in
low income countries in Latin America: A report on the recent meetings of the
Monza International School of Pediatric Hematology/Oncology (MISPHO): Part III.
Pediatr Blood Cancer. 2007 May;48(5):598-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16883599&query_hl=12&itool=pubmed_DocSum

3: Le Gallais D, Lonsdorfer J, Bogui P, Fattoum S, Connes P, Hardy-Dessources
MD, Hue O. Point-Counterpoint: Sickle cell trait should/should not be considered
asymptomatic and as a benign condition during physical activity.
J Appl Physiol. 2007 Apr 19; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17395764&query_hl=12&itool=pubmed_DocSum

4: Manchikanti A, Grimes D, Lopez L, Schulz K. Steroid hormones for contraception in women with sickle cell disease.
Cochrane Database Syst Rev. 2007 Apr 18;2:CD006261. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443618&query_hl=12&itool=pubmed_DocSum

5: Al Hajeri A, Fedorowicz Z, Omran A, Tadmouri G. Piracetam for reducing the incidence of painful sickle cell disease crises.
Cochrane Database Syst Rev. 2007 Apr 18;(2):CD006111. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443614&query_hl=12&itool=pubmed_DocSum

6: Marti-Carvajal A, Conterno L, Knight-Madden J. Antibiotics for treating acute chest syndrome in people with sickle cell
disease.Cochrane Database Syst Rev. 2007 Apr 18;(2):CD006110. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443613&query_hl=12&itool=pubmed_DocSum

7: Okomo U, Meremikwu M. Fluid replacement therapy for acute episodes of pain in people with sickle cell
disease.Cochrane Database Syst Rev. 2007 Apr 18;(2):CD005406. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17443589&query_hl=12&itool=pubmed_DocSum

8: Zimmerman SA, Schultz WH, Burgett S, Mortier NA, Ware RE. 
Hydroxyurea therapy lowers transcranial doppler flow velocities in children
with sickle cell anemia.Blood. 2007 Apr 11; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17429008&query_hl=12&itool=pubmed_DocSum

9: Thompson J, Reid M, Hambleton I, Serjeant GR. Albuminuria and renal function in homozygous sickle cell disease: observations
from a cohort study.Arch Intern Med. 2007 Apr 9;167(7):701-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17420429&query_hl=12&itool=pubmed_DocSum

10: Austin H, Key NS, Benson JM, Lally C, Dowling NF, Whitsett C, Hooper WC. 
Sickle-cell trait and the risk of venous thromboembolism among African
Americans.Blood. 2007 Apr 4; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17409269&query_hl=12&itool=pubmed_DocSum

11: Citero VD, Levenson JL, McClish DK, Bovbjerg VE, Cole PL, Dahman BA,
Penberthy LT, Aisiku IP, Roseff SD, Smith WR. The role of catastrophizing in sickle cell disease - The PiSCES project.
Pain. 2007 Apr 2; [Epub ahead of print] http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17408858&query_hl=12&itool=pubmed_DocSum

12: Fung EB, Harmatz P, Milet M, Ballas SK, De Castro L, Hagar W, Owen W,
Olivieri N, Smith-Whitley K, Darbari D, Wang W, Vichinsky E. Morbidity and mortality in chronically transfused subjects with thalassemia and
sickle cell disease: A report from the multi-center study of iron overload.
Am J Hematol. 2007 Apr;82(4):255-65. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17094096&query_hl=12&itool=pubmed_DocSum

13: Benton TD, Ifeagwu JA, Smith-Whitley K. Anxiety and Depression in Children and Adolescents with Sickle Cell Disease.
Curr Psychiatry Rep. 2007 Apr;9(2):114-121. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17389120&query_hl=12&itool=pubmed_DocSum

14: Givens M, Rutherford C, Joshi G, Delaney K. Impact of an emergency department pain management protocol on the pattern of
visits by patients with sickle cell disease.J Emerg Med. 2007 Apr;32(3):239-43. Epub 2007 Feb 7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17394984&query_hl=12&itool=pubmed_DocSum

 

March 2007

Chakrabarti S, Bareford D.  A survey on patient perception of reduced-intensity transplantation in adults
with sickle cell disease. Bone Marrow Transplant. 2007 Mar 5; 
http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17334383&query_hl=4&itool=pubmed_DocSum

Yallop D, Duncan ER, Norris E, Fuller GW, Thomas N, Walters J, Dick MC,Height SE, Thein SL, Rees DC.  The associations between air quality and the number of hospital admissions for acute pain and sickle-cell disease in an urban environment.Br J Haematol. 2007 Mar;136(6):844-848.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17341271&query_hl=4&itool=pubmed_DocSum

Couillard S, Benkerrou M, Girot R, Brousse V, Ferster A, Bader-Meunier B.  Steroid treatment in children with sickle-cell disease.
Haematologica. 2007 Mar;92(3):425-6.  
http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17339198&query_hl=4&itool=pubmed_DocSum

Pence L, Valrie CR, Gil KM, Redding-Lallinger R, Daeschner C.  Optimism Predicting Daily Pain Medication Use in Adolescents with Sickle Cell
Disease.J Pain Symptom Manage. 2007 Mar;33(3):302-309. 
http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17349499&query_hl=4&itool=pubmed_DocSum

 McKie KT, Hanevold CD, Hernandez C, Waller JL, Ortiz L, McKie KM.  Prevalence, Prevention, and Treatment of Microalbuminuria and Proteinuria in
Children With Sickle Cell Disease.J Pediatr Hematol Oncol. 2007 Mar;29(3):140-144.
http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17356390&query_hl=4&itool=pubmed_DocSum

Sylvester KP, Patey RA, Rafferty GF, Rees D, Thein SL, Greenough A.   Airway hyperresponsiveness and acute chest syndrome in children with sickle
cell anemia. Pediatr Pulmonol. 2007 Mar;42(3):272-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17262858&query_hl=1&itool=pubmed_DocSum

Grassineau D, Papa K, Ducourneau A, Duboz P, Boetsch G, Chiaroni J.   Improving minority blood donation: anthropologic approach in a migrant
community. Transfusion. 2007 Mar;47(3):402-9.  PMID: 17319819 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17319819&query_hl=1&itool=pubmed_DocSum

Au WY, Leung WC.   Challenges and pitfalls in prenatal screening in pregnancies involving allogeneic stem cell transplantation recipients.
Bone Marrow Transplant. 2007 Feb 19; [Epub ahead of print]  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17310136&query_hl=1&itool=pubmed_DocSum

 

February 2007

Kass NE, Medley AM, Natowicz MR, Hull SC, Faden RR, Plantinga L, Gostin LO.   Access to health insurance: Experiences and attitudes of those with genetic
versus non-genetic medical conditions. Am J Med Genet A. 2007 Feb 8;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17290434&query_hl=0&itool=pubmed_docsum
 Frempong T, Pearson HA.  Newborn screening coupled with comprehensive follow-up reduced early mortality of sickle cell disease in Connecticut. Conn Med. 2007 Jan;71(1):9-12. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17288099&query_hl=0&itool=pubmed_docsum
 Serjeant GR, Higgs DR, Hambleton IR.  Elderly survivors with homozygous sickle cell disease.
N Engl J Med. 2007 Feb 8;356(6):642-3. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17287491&query_hl=0&itool=pubmed_docsum
 Jacob E, Miaskowski C, Savedra M, Beyer JE, Treadwell M, Styles L.  Quantification of analgesic use in children with sickle cell disease.
Clin J Pain. 2007 Jan;23(1):8-14. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17277639&query_hl=0&itool=pubmed_docsum
Sachdev V, Machado RF, Shizukuda Y, Rao YN, Sidenko S, Ernst I, St Peter M, Coles WA, Rosing DR, Blackwelder WC, Castro O, Kato GJ, Gladwin MT. 
 Diastolic dysfunction is an independent risk factor for death in patients with sickle cell disease. J Am Coll Cardiol. 2007 Jan 30;49(4):472-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17258093&query_hl=0&itool=pubmed_docsum
 Joiner CH, Kirk Rettig R, Jiang M, Risinger M, Franco RS.  Urea stimulation of KCl cotransport induces abnormal volume reduction in sickle
reticulocytes.Blood. 2007 Feb 15;109(4):1728-35. Epub 2006 Oct 5.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17023583&query_hl=0&itool=pubmed_docsum
 Miller ML, Gao G, Pestina T, Persons D, Tuomanen E.  Hypersusceptibility to invasive pneumococcal infection in experimental sickle
cell disease involves platelet-activating factor receptor.J Infect Dis. 2007 Feb 15;195(4):581-4. Epub 2007 Jan 8.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17230418&query_hl=0&itool=pubmed_docsum
  Koduri PR.  Acute splenic sequestration crisis in adults with sickle cell anemia.Am J Hematol. 2007 Feb;82(2):174-5. No abstract available. 
Hofmann M, de Montalembert M, Beauquier-Maccotta B, de Villartay P, Golse B.  Posttraumatic stress disorder in children affected by sickle-cell disease and
their parents.Am J Hematol. 2007 Feb;82(2):171-2. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16924639&query_hl=0&itool=pubmed_docsum
  Vichinsky E, Onyekwere O, Porter J, Swerdlow P, Eckman J, Lane P, Files B, Hassell K, Kelly P, Wilson F, Bernaudin F, Forni GL, Okpala I, Ressayre-Djaffer
C, Alberti D, Holland J, Marks P, Fung E, Fischer R, Mueller BU, Coates T; Deferasirox in Sickle Cell Investigators. 
 A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease. 
Br J Haematol. 2007 Feb;136(3):501-8.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17233848&query_hl=0&itool=pubmed_docsum
   Krishnamurti L.  Hematopoietic cell transplantation for sickle cell disease: state of the art.Expert Opin Biol Ther. 2007 Feb;7(2):161-72. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17250455&query_hl=0&itool=pubmed_docsum
  Sylvester KP, Patey RA, Broughton S, Rafferty GF, Rees D, Thein SL, Greenough A.  Temporal relationship of asthma to acute chest syndrome in sickle cell disease.
Pediatr Pulmonol. 2007 Feb;42(2):103-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17186507&query_hl=0&itool=pubmed_docsum

January 2007

Platt A, Eckman J. Diagnosing Anemia. Clinician Reviews  2006 Dec;16 (12):43 - 50  Full text online at  http://www.clinicianreviews.com/index.asp?show=lesson&page=courses/105417/lesson.htm&lsn_id=105417

Moheeb H, Wali YA, El-Sayed MS. Physical fitness indices and anthropometrics profiles in schoolchildren with sickle cell trait/disease.
Am J Hematol. 2007 Feb;82(2):91-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16986131&query_hl=1&itool=pubmed_DocSum

Sylvester KP, Patey RA, Broughton S, Rafferty GF, Rees D, Thein SL, Greenough A. Temporal relationship of asthma to acute chest syndrome in sickle cell disease.  Pediatr Pulmonol. 2007 Feb;42(2):103-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17186507&query_hl=1&itool=pubmed_DocSum

Eggleston B, Patience M, Edwards S, Adamkiewicz T, Buchanan GR, Davies SC, Dickerhoff R, Donfield S, Feig SA, Giller RH, Haight A, Horan J, Hsu LL, Kamani N, Lane P, Levine JE, Margolis D, Moore TB, Ohene-Frempong K, Redding-Lallinger R, Roberts IA, Rogers ZR, Sanders JE, Scott JP, Sleight B, Thompson AA, Sullivan KM, Walters MC; for the Multicenter Study of HCT for SCA*. Effect of myeloablative bone marrow transplantation on growth in children with sickle cell anaemia: results of the multicenter study of haematopoietic cell transplantation for sickle cell anaemia. Br J Haematol. 2007 Jan 11;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17223910&query_hl=1&itool=pubmed_DocSum   

Saleem S, Rice L. Limb amputation in hemoglobin SC disease after application of ice and elevation.
Am J Hematol. 2007 Jan;82(1):53-4. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16929537&query_hl=1&itool=pubmed_DocSum

Kizito ME, Mworozi E, Ndugwa C, Serjeant GR. Bacteraemia in homozygous sickle cell disease in Africa: is pneumococcal prophylaxis justified?
Arch Dis Child. 2007 Jan;92(1):21-3. Epub 2006 Mar 10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16531454&query_hl=1&itool=pubmed_DocSum

Quinn CT, Shull EP, Ahmad N, Lee NJ, Rogers ZR, Buchanan GR. Prognostic significance of early vaso-occlusive complications in children with sickle cell anemia. Blood. 2007 Jan 1;109(1):40-5. Epub 2006 Aug 29 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16940426&query_hl=1&itool=pubmed_DocSum

Varganov Y, Amosova O, Fresco JR. Third strand-mediated psoralen-induced correction of the sickle cell mutation on a plasmid transfected into COS-7 cells. Gene Ther. 2007 Jan;14(2):173-9. Epub 2006 Aug 31 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16943853&query_hl=1&itool=pubmed_DocSum

Monchanin G, Serpero LD, Connes P, Tripette J, Wouassi D, Bezin L, Francina A, Ngongang J, de la Pena M, Massarelli R, Gozal D, Thiriet P, Martin C. Effects of progressive and maximal exercise on plasma levels of adhesion molecules in athletes with sickle cell trait with or without {alpha}-thalassemia. J Appl Physiol. 2007 Jan;102(1):169-173. Epub 2006 Aug 10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16902065&query_hl=1&itool=pubmed_DocSum

Machado RF, Kyle Mack A, Martyr S, Barnett C, Macarthur P, Sachdev V, Ernst I, Hunter LA, Coles WA, Nichols JP, Kato GJ, Gladwin MT. Severity of pulmonary hypertension during vaso-occlusive pain crisis and exercise in patients with sickle cell disease. Br J Haematol. 2006 Dec 8; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17156401&query_hl=1&itool=pubmed_DocSum

December 2006

Sara Day, RN, MSN; and Elisabeth Chismark, RN, MSN  The Cognitive and Academic Impact Of Sickle Cell Disease The Journal of School Nursing December 2006 Volume 22, Number 6 Full Text PDF 

Neumayr LD, Aguilar C, Earles AN, Jergesen HE, Haberkern CM, Kammen BF, Nancarrow PA, Padua E, Milet M, Stulberg BN, Williams RA, Orringer EP, Graber N, Robertson SM, Vichinsky EP. Physical therapy alone compared with core decompression and physical therapy for femoral head osteonecrosis in sickle cell disease. Results of a multicenter study at a mean of three years after treatment. J Bone Joint Surg Am. 2006 Dec;88(12):2573-82. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17142406&query_hl=1&itool=pubmed_docsum

 Hernigou P, Habibi A, Bachir D, Galacteros F. The natural history of asymptomatic osteonecrosis of the femoral head in adults with sickle cell disease. J Bone Joint Surg Am. 2006 Dec;88(12):2565-72. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17142405&query_hl=1&itool=pubmed_docsum

Hibbert JM, Creary MS, Gee BE, Buchanan ID, Quarshie A, Hsu LL. Erythropoiesis and myocardial energy requirements contribute to the hypermetabolism of childhood sickle cell anemia. J Pediatr Gastroenterol Nutr. 2006 Nov;43(5):680-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17130748&query_hl=1&itool=pubmed_docsum

 Al-Salem AH. Indications and complications of splenectomy for children with sickle cell disease. J Pediatr Surg. 2006 Nov;41(11):1909-15.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17101369&query_hl=1&itool=pubmed_DocSum

Burnett AL, Bivalacqua TJ, Champion HC, Musicki B Feasibility of the use of phosphodiesterase type 5 inhibitors in a pharmacologic prevention program for recurrent priapism. J Sex Med. 2006 Nov;3(6):1077-84. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17100941&query_hl=1&itool=pubmed_DocSum

 Hulbert ML, Scothorn DJ, Panepinto JA, Scott JP, Buchanan GR, Sarnaik S, Fallon R, Chu JY, Wang W, Casella JF, Resar L, Berman B, Adamkiewicz T, Hsu LL, Smith-Whitley K, Mahoney D, Woods G, Watanabe M, DeBaun MR. Exchange blood transfusion compared with simple transfusion for first overt stroke is associated with a lower risk of subsequent stroke: a retrospective cohort study of 137 children with sickle cell anemia. J Pediatr. 2006 Nov;149(5):710-2. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17095350&query_hl=1&itool=pubmed_DocSum

 Uong EC, Boyd JH, DeBaun MR. Daytime pulse oximeter measurements do not predict incidence of pain and acute chest syndrome episodes in sickle cell anemia.  J Pediatr. 2006 Nov;149(5):707-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17095349&query_hl=1&itool=pubmed_DocSum

 Fung EB, Harmatz P, Milet M, Ballas SK, De Castro L, Hagar W, Owen W, Olivieri N, Smith-Whitley K, Darbari D, Wang W, Vichinsky E. Morbidity and mortality in chronically transfused subjects with thalassemia and sickle cell disease: A report from the multi-center study of iron overload. Am J Hematol. 2006 Nov 8; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17094096&query_hl=1&itool=pubmed_DocSum

 

November 2006

 Strouse JJ, Hulbert ML, DeBaun MR, Jordan LC, Casella JF. Primary hemorrhagic stroke in children with sickle cell disease is associated with recent transfusion and use of corticosteroids. Pediatrics. 2006 Nov;118(5):1916-24. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17079562&query_hl=4&itool=pubmed_docsum

Spivey JF, Uong EC, Strunk R, Boslaugh SE, Debaun MR. Low daytime pulse oximetry reading is associated with nocturnal desaturation and obstructive sleep apnea in children with sickle cell anemia. Pediatr Blood Cancer. 2006 Oct 27; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17072857&query_hl=4&itool=pubmed_docsum

Ataga KI, Orringer EP, Styles L, Vichinsky EP, Swerdlow P, Davis GA, Desimone PA, Stocker JW. Dose-Escalation Study of ICA-17043 in Patients with Sickle Cell Disease.
Pharmacotherapy. 2006 Nov;26(11):1557-64. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17064199&query_hl=4&itool=pubmed_docsum

Schatz J, McClellan CB. Sickle cell disease as a neurodevelopmental disorder.
Ment Retard Dev Disabil Res Rev. 2006;12(3):200-7.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17061284&query_hl=4&itool=pubmed_docsum

Oniyangi O, Omari AA. Malaria chemoprophylaxis in sickle cell disease. Cochrane Database Syst Rev. 2006 Oct 18;(4):CD003489. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17054173&query_hl=4&itool=pubmed_docsum

Morris CR, Singer ST, Walters MC. Clinical hemoglobinopathies: iron, lungs and new blood. Curr Opin Hematol. 2006 Nov;13(6):407-418. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17053452&query_hl=4&itool=pubmed_DocSum

Mehta SH, Adams RJ. Treatment and prevention of stroke in children with sickle cell disease. Curr Treat Options Neurol. 2006 Nov;8(6):503-12. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17032571&query_hl=4&itool=pubmed_DocSum

 

October 2006

Mason P. Sickle cell disease in the perioperative setting. J Perioper Pract. 2006 Sep;16(9):443-6.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17001937&query_hl=2&itool=pubmed_docsum

Stein PD, Beemath A, Meyers FA, Skaf E, Olson RE. Deep venous thrombosis and pulmonary embolism in hospitalized patients with sickle cell disease. Am J Med. 2006 Oct;119(10):897.e7-11. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=17000225&query_hl=2&itool=pubmed_docsum

Raj AB, O'brien LM, Bertolone SJ, Gozal D, Edmonds HL Jr. Cerebral oximetry improves detection of sickle cell patients at risk for nocturnal cerebral hypoxia. Pediatr Pulmonol. 2006 Sep 22;41(11):1088-1094 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16998929&query_hl=2&itool=pubmed_docsum

Shankar SM, Arbogast PG, Mitchel E, Ding H, Wang WC, Griffin MR. Impact of proximity to comprehensive sickle cell center on utilization of healthcare services among children with sickle cell disease. Pediatr Blood Cancer. 2006 Sep 22;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16998856&query_hl=2&itool=pubmed_docsum

Moheeb H, Wali YA, El-Sayed MS. Physical fitness indices and anthropometrics profiles in schoolchildren with sickle cell trait/disease. Am J Hematol. 2006 Sep 19; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16986131&query_hl=2&itool=pubmed_docsum

Chulamokha L, Scholand SJ, Riggio JM, Ballas SK, Horn D, Desimone JA. Bloodstream infections in hospitalized adults with sickle cell disease: A retrospective analysis. Am J Hematol. 2006 Oct;81(10):723-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16795063&query_hl=12&itool=pubmed_docsum

Raffini LJ, Niebanck AE, Hrusovsky J, Stevens A, Blackwood-Chirchir A, Ohene-Frempong K, Kwiatkowski JL. Prolongation of the prothrombin time and activated partial thromboplastin time in children with sickle cell disease. Pediatr Blood Cancer. 2006 Oct 15;47(5):589-93.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16123995&query_hl=14&itool=pubmed_docsum

September 2006

Kaye CI.  Newborn screening fact sheets. Pediatrics. 2006 Sep;118(3):e934-63. Full Text at http://pediatrics.aappublications.org/cgi/content/full/118/3/1304

Full text on the following  biotinidase deficiency • congenital adrenal
hyperplasia • congenital hearing loss • congenital hypothyroidism • cystic fibrosis • galactosemia • hemoglobinopathies • homocystinuria • maple syrup urine disease • medium-chain acyl-CoA dehydrogenase deficiency • phenylketonuria • sickle cell disease • tyrosinemia  at http://pediatrics.aappublications.org/cgi/content/full/118/3/e934

Ballas SK, Barton FB, Waclawiw MA, Swerdlow P, Eckman JR, Pegelow CH, Koshy M, Barton BA, Bonds DR, Msh IO.  Hydroxyurea and sickle cell anemia: Effect on quality of life. Health Qual Life Outcomes. 2006 Aug 31;4(1):59 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16942629&query_hl=3&itool=pubmed_docsum

Karimi M, Zekavat OR, Sharifzadeh S, Mosavizadeh K. Clinical response of patients with sickle cell anemia to cromolyn sodium nasal spray. Am J Hematol. 2006 Aug 29 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16941613&query_hl=3&itool=pubmed_docsum

Quinn CT, Shull EP, Ahmad N, Lee NJ, Rogers ZR, Buchanan GR. Prognostic significance of early vaso-occlusive complications in children with sickle cell anemia. Blood. 2006 Aug 29;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16940426&query_hl=3&itool=pubmed_docsum

Price CL, Boyd JH, Watkins AR, Fleming F, DeBaun MR. Mailing of a sickle cell disease educational packet increases blood donors within an African American community. Transfusion. 2006 Aug;46(8):1388-93. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16934076&query_hl=3&itool=pubmed_docsum

Montero-Huerta P, Hess DR, Head CA. Inhaled Nitric Oxide for Treatment of Sickle Cell Stroke. Anesthesiology. 2006 Sep;105(3):619-621 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16931997&query_hl=3&itool=pubmed_docsum

Saleem S, Rice L. Limb amputation in hemoglobin SC disease after application of ice and elevation. Am J Hematol. 2006 Aug 23 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16929537&query_hl=3&itool=pubmed_docsum

Ahmed S, Atkin K, Hewison J, Green J. The influence of faith and religion and the role of religious and community leaders in prenatal decisions for sickle cell disorders
and thalassaemia major. Prenat Diagn. 2006 Sep;26(9):801-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16927359&query_hl=3&itool=pubmed_docsum

Lanzkron S, Haywood C Jr, Segal JB, Dover GJ. Hospitalization rates and costs of care of patients with sickle-cell anemia in the state of Maryland in the era of hydroxyurea.
Am J Hematol. 2006 Aug 21 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16924648&query_hl=3&itool=pubmed_DocSum

Darbari DS, Kple-Faget P, Kwagyan J, Rana S, Gordeuk VR, Castro O. Circumstances of death in adult sickle cell disease patients. Am J Hematol. 2006 Aug 21 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16924640&query_hl=3&itool=pubmed_DocSum

Hofmann M, de Montalembert M, Beauquier-Maccotta B, de Villartay P, Golse B. Posttraumatic stress disorder in children affected by sickle-cell disease and their parents. Am J Hematol. 2006 Aug 21; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16924639&query_hl=3&itool=pubmed_DocSum

Valadi N, Silva GS, Bowman LS, Ramsingh D, Vicari P, Filho AC, Massaro AR, Kutlar A, Nichols FT, Adams RJ. Transcranial Doppler ultrasonography in adults with sickle cell disease. Neurology. 2006 Aug 22;67(4):572-4. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16924006&query_hl=3&itool=pubmed_DocSum

August 2006

Little JA, McGowan VR, Kato GJ, Partovi KS, Feld JJ, Maric I, Martyr S, Taylor JG 6th, Machado RF, Heller T, Castro O, Gladwin MT. Combination erythropoietin-hydroxyurea therapy in sickle cell disease: experience from the National Institutes of Health and a literature review. Haematologica. 2006 Aug;91(8):1076-83. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16885048&query_hl=1&itool=pubmed_docsum

Mehta SR, Afenyi-Annan A, Byrns PJ, Lottenberg R. Opportunities to improve outcomes in sickle cell disease. Am Fam Physician. 2006 Jul 15;74(2):303-10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16883928&query_hl=1&itool=pubmed_docsum

Howard SC, Wilimas JA, Flores A, Pacheco C, de Reyes G, Machin S, Svarch E, Navarrete M, Nieves R, Rodriguez H, Masera G. Treatment for children with severe aplastic anemia and sickle cell disease in low income countries in Latin America: A report on the recent meetings of the Monza International School of Pediatric Hematology/Oncology (MISPHO): Part III. Pediatr Blood Cancer. 2006 Aug 1 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16883599&query_hl=1&itool=pubmed_docsum

Lee MT, Piomelli S, Granger S, Miller ST, Harkness S, Brambilla DJ, Adams RJ; STOP Study Investigators. Stroke Prevention Trial in Sickle Cell Anemia (STOP): extended follow-up and final results. Blood. 2006 Aug 1;108(3):847-52. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16861341&query_hl=1&itool=pubmed_DocSum

Qureshi N, Joyce JJ, Qi N, Chang RK. Right ventricular abnormalities in sickle cell anemia: evidence of a progressive increase in pulmonary vascular resistance. J Pediatr. 2006 Jul;149(1):23-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16860121&query_hl=1&itool=pubmed_DocSum

Sylvester KP, Patey RA, Milligan P, Rafferty GF, Broughton S, Rees D, Thein SL,  Greenough A. Impact of acute chest syndrome on lung function of children with sickle cell disease. J Pediatr. 2006 Jul;149(1):17-22 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16860119&

July 2006
Marti-Carvajal A, Conterno L. Antibiotics for treating community acquired pneumonia in people with sickle cell disease. Cochrane Database Syst Rev. 2006 Jul 19;3 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16856106&query_hl=2&itool=pubmed_docsum

Machado RF, Anthi A, Steinberg MH, Bonds D, Sachdev V, Kato GJ, Taveira-DaSilva AM, Ballas SK, Blackwelder W, Xu X, Hunter L, Barton B, Waclawiw M, Castro O, Gladwin MT; MSH Investigators. N-terminal pro-brain natriuretic peptide levels and risk of death in sickle cell disease. JAMA. 2006 Jul 19;296(3):310-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16849664&query_hl=2&itool=pubmed_docsum

Kwiatkowski JL, Granger S, Brambilla DJ, Brown RC, Miller ST, Adams RJ; the STOP Trial Investigators*. Elevated blood flow velocity in the anterior cerebral artery and stroke risk in sickle cell disease: extended analysis from the STOP trial. Br J Haematol. 2006 Aug;134(3):333-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16848777&query_hl=2&itool=pubmed_docsum

Guasch A, Navarrete J, Nass K, Zayas CF. Glomerular Involvement in Adults with Sickle Cell Hemoglobinopathies: Prevalence and Clinical Correlates of Progressive Renal Failure. J Am Soc Nephrol. 2006 Jul 12 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16837635&query_hl=2&itool=pubmed_docsum

Akgul F, Yalcin F, Babayigit C, Seyfeli E, Seydaliyeva T, Gali E. Right Ventricular and Pulmonary Function in Sickle Cell Disease Patients with Pulmonary Hypertension. Pediatr Cardiol. 2006 Jul 11; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16835804&query_hl=2&itool=pubmed_docsum

Duits AJ, Rodriguez T, Schnog JJ; CURAMA Study Group. Serum levels of angiogenic factors indicate a pro-angiogenic state in adults with sickle cell disease. Br J Haematol. 2006 Jul;134(1):116-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16803577&query_hl=2&itool=pubmed_DocSum

Ataga KI, Moore CG, Jones S, Olajide O, Strayhorn D, Hinderliter A, Orringer EP. Pulmonary hypertension in patients with sickle cell disease: a longitudinal study.
Br J Haematol. 2006 Jul;134(1):109-15. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16803576&query_hl=2&itool=pubmed_DocSum

Chulamokha L, Scholand SJ, Riggio JM, Ballas SK, Horn D, Desimone JA. Bloodstream infections in hospitalized adults with sickle cell disease: A retrospective analysis. Am J Hematol. 2006 Jun 22;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=pubmed&cmd=Retrieve&dopt=AbstractPlus&list_uids=16795063&query_hl=2&itool=pubmed_DocSum

June 2006
Sylvester KP, Desai SR, Wells AU, Hansell DM, Awogbade M, Thein SL, Greenough A. Computed tomography and pulmonary function abnormalities in sickle cell disease.  Eur Respir J. 2006 May 31 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16737989&query_hl=2&itool=pubmed_docsum

Oneal PA, Gantt NM, Schwartz JD, Bhanu NV, Lee YT, Moroney JW, Reed CH, Schechter AN, Luban NL, Miller JL. Fetal hemoglobin silencing in humans. Blood. 2006 May 30;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16735596&query_hl=2&itool=pubmed_docsum

Hankins J, Hinds P, Day S, Carroll Y, Li CS, Garvie P, Wang W. Therapy preference and decision-making among patients with severe sickle cell anemia and their families& Pediatr Blood Cancer. 2006 May 26; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16732581&query_hl=2&itool=pubmed_docsum

 Goldstein LB, Adams R, Alberts MJ, Appel LJ, Brass LM, Bushnell CD, Culebras A, Degraba TJ, Gorelick PB, Guyton JR, Hart RG, Howard G, Kelly-Hayes M, Nixon JV, Sacco RL; American Heart Association/American Stroke Association Stroke Council; Atherosclerotic Peripheral Vascular Disease Interdisciplinary Working Group; Cardiovascular Nursing Council; Clinical Cardiology Council; Nutrition, Physical Activity, and Metabolism Council; Quality of Care and Outcomes Research Interdisciplinary Working Group; American Academy of Neurology.Primary prevention of ischemic stroke: a guideline from the American Heart Association/American Stroke Association Stroke Council: cosponsored by the Atherosclerotic Peripheral Vascular Disease Interdisciplinary Working Group; Cardiovascular Nursing Council; Clinical Cardiology Council; Nutrition, Physical Activity, and Metabolism Council; and the Quality of Care and Outcomes Research Interdisciplinary Working Group: the American Academy of Neurology affirms the value of this guideline. Stroke. 2006 Jun;37(6):1583-633. Epub 2006 May 4. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16675728&query_hl=2&itool=pubmed_DocSum

Kaul DK, Liu XD, Zhang X, Mankelow T, Parsons S, Spring F, An X, Narla M, Anstee D, Chasis JA. Peptides based on {alpha}V-Binding Domains of Erythrocyte ICAM-4 Inhibit Sickle Red Cell-endothelial Interactions and Vaso-Occlusion in the Microcirculation. Am J Physiol Cell Physiol. 2006 May 31; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16738001&query_hl=2&itool=pubmed_docsum

Alexy T, Pais E, Armstrong JK, Meiselman HJ, Johnson CS, Fisher TC.
Rheologic behavior of sickle and normal red blood cell mixtures in sickle plasma: implications for transfusion therapy. Transfusion. 2006 Jun;46(6):912-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16734807&query_hl=2&itool=pubmed_docsum

Scheinman JI. Tools to detect and modify sickle cell nephropathy. Kidney Int. 2006 Jun;69(11):1927-30. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16724088&query_hl=2&itool=pubmed_docsum


May 2006

Nolan VG, Adewoye A, Baldwin C, Wang L, Ma Q, Wyszynski DF, Farrell JJ, Sebastiani P, Farrer LA, Steinberg MH.Sickle cell leg ulcers: associations with haemolysis and SNPs in Klotho, TEK and genes of the TGF-beta/BMP pathway. Br J Haematol. 2006 Jun;133(5):570-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16681647&query_hl=2&itool=pubmed_docsum

 Structured telephone-based outreach using nonmedical personnel can improve adherence to comprehensive care in families of children with sickle cell disease.  Am J Hematol. 2006 May 5;81(6):462-464  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16680738&query_hl=2&itool=pubmed_docsum

 White DA, Moinuddin A, McKinstry RC, Noetzel M, Armstrong M, DeBaun M. Cognitive screening for silent cerebral infarction in children with sickle cell disease. J Pediatr Hematol Oncol. 2006 Mar;28(3):166-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16679942&query_hl=2&itool=pubmed_docsum

Bergmann S, Zheng D, Barredo J, Abboud MR, Jaffa AA. Renal kallikrein: a risk marker for nephropathy in children with sickle cell disease. J Pediatr Hematol Oncol. 2006 Mar;28(3):147-53. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16679937&query_hl=2&itool=pubmed_docsum

 Smith LA, Oyeku SO, Homer C, Zuckerman B .Sickle cell disease: a question of equity and quality. Pediatrics. 2006 May;117(5):1763-70. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16651336&query_hl=2&itool=pubmed_docsum

Sibinga EM, Shindell DL, Casella JF, Duggan AK, Wilson MH. Pediatric patients with sickle cell disease: use of complementary and alternative therapies. J Altern Complement Med. 2006 Apr;12(3):291-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16646728&query_hl=2&itool=pubmed_DocSum

Dauphin-McKenzie N, Gilles JM, Jacques E, Harrington T. Sickle cell anemia in the female patient. Obstet Gynecol Surv. 2006 May;61(5):343-52. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16635275&query_hl=2&itool=pubmed_DocSum

Dunlop R, Bennett K. Pain management for sickle cell disease. Cochrane Database Syst Rev. 2006 Apr 19;(2):CD003350. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16625580&query_hl=2&itool=pubmed_DocSum

Christine Anne Dumaplin" Avoiding Admission for Afebrile Pediatric Sickle Cell Pain: Pain Management Methods" , Journal of Pediatric Health Care (2005) Volume 20, Issue 2, 115-122 20. Full Text PDF

April 2006 Medline

Sadelain M. Recent advances in globin gene transfer for the treatment of beta-thalassemia and sickle cell anemia.
Curr Opin Hematol. 2006 May;13(3):142-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16567956&query_hl=2&itool=pubmed_DocSum
 
 Steinberg MH, Adewoye AH. Modifier genes and sickle cell anemia. Curr Opin Hematol. 2006 May;13(3):131-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16567954&query_hl=2&itool=pubmed_DocSum

Alvarez O, Zilleruelo G, Wright D, Montane B, Lopez-Mitnik G. Serum cystatin C levels in children with sickle cell disease. Pediatr Nephrol. 2006 Apr;21(4):533-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16491413&query_hl=2&itool=pubmed_DocSum 

Klings ES, Wyszynski DF, Nolan VG, Steinberg MH Abnormal Pulmonary Function in Adults with Sickle Cell Anemia. Am J Respir Crit Care Med. 2006 Mar 23; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16556694&query_hl=2&itool=pubmed_DocSum

 

Dyson SM, Culley L, Gill C, Hubbard S, Kennefick A, Morris P, Rees D, Sutton F, Squire P.thnicity Questions and Antenatal Screening for Sickle Cell/Thalassaemia [EQUANS] in England: A Randomised Controlled Trial of Two Questionnaires. Ethn Health. 2006 May;11(2):169-89. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16595318&query_hl=2&itool=pubmed_DocSum
 
Dykxhoorn DM, Schlehuber LD, London IM, Lieberman J. Determinants of specific RNA interference-mediated silencing of human beta-globin alleles differing by a single nucleotide polymorphism. Proc Natl Acad Sci U S A. 2006 Apr 11;103(15):5953-8. Epub 2006 Apr 3.
http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16585504&query_hl=2&itool=pubmed_DocSum
 
 Lee SP, Ataga KI, Orringer EP, Phillips DR, Parise LV. Biologically Active CD40 Ligand Is Elevated in Sickle Cell Anemia. Potential Role for Platelet-Mediated Inflammation. Arterioscler Thromb Vasc Biol. 2006 Apr 6;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16601237&query_hl=2&itool=pubmed_DocSum
 
Lee MT, Piomelli S, Granger S, Miller ST, Harkness S, Brambilla DJ, Adams RJ. Stroke Prevention Trial in Sickle Cell Anemia (STOP): Extended Follow-up and Final Results. Blood. 2006 Apr 6; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16601250&query_hl=2&itool=pubmed_DocSum
 
Miller RG, Segal JB, Ashar BH, Leung S, Ahmed S, Siddique S, Rice T, Lanzkron S. High prevalence and correlates of low bone mineral density in young adults with sickle cell disease. Am J Hematol. 2006 Apr;81(4):236-41. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16550513&query_hl=2&itool=pubmed_DocSum
 
Koduri PR, Nathan S. Acute splenic sequestration crisis in adults with hemoglobin S-C disease: a report of nine cases. Ann Hematol. 2006  Apr;85(4):239-43 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16463155&query_hl=2&itool=pubmed_DocSum  
 
 
 
 
 
 

 

March 2006 MedLine

  Koduri PR, Nathan S. Related Articles,
  Acute splenic sequestration crisis in adults with hemoglobin S-C disease: a report of nine cases.
Ann Hematol. 2006 Apr;85(4):239-43. Epub 2006 Feb 7.
PMID: 16463155 [PubMed - in process]
  Kato GJ, McGowan V, Machado RF, Little JA, Taylor J 6th, Morris CR, Nichols JS, Wang X, Poljakovic M, Morris SM Jr, Gladwin MT. Related Articles,  
  Lactate dehydrogenase as a biomarker of hemolysis-associated nitric oxide resistance, priapism, leg ulceration, pulmonary hypertension, and death in patients with sickle cell disease.
Blood. 2006 Mar 15;107(6):2279-85. Epub 2005 Nov 15.
PMID: 16291595 [PubMed - in process]
  Kmietowicz Z.  
  Sickle cell screening makes genetic counselling everybody's business.
BMJ. 2006 Mar 11;332(7541):570. No abstract available.
PMID: 16528080 [PubMed - in process]
  Cokic VP, Beleslin-Cokic BB, Tomic M, Stojilkovic SS, Noguchi CT, Schechter AN.  
  Hydroxyurea induces the eNOS-cGMP pathway in endothelial cells.
Blood. 2006 Mar 9; [Epub ahead of print]
PMID: 16527893 [PubMed - as supplied by publisher]
  Kratovil T, Bulas D, Driscoll MC, Speller-Brown B, McCarter R, Minniti CP. Related Articles,
  Hydroxyurea therapy lowers TCD velocities in children with sickle cell disease.
Pediatr Blood Cancer. 2006 Mar 8; [Epub ahead of print]
PMID: 16526051 [PubMed - as supplied by publisher]
  Connes P, Sara F, Hardy-Dessources MD, Marlin L, Etienne F, Larifla L, Saint-Martin C, Hue O. Related Articles,
  Effects of short supramaximal exercise on hemorheology in sickle cell trait carriers.
Eur J Appl Physiol. 2006 Feb 28; [Epub ahead of print]
PMID: 16506056 [PubMed - as supplied by publisher]
  Elander J, Marczewska M, Amos R, Thomas A, Tangayi S. Related Articles,
  Factors Affecting Hospital Staff Judgments About Sickle Cell Disease Pain.
J Behav Med. 2006 Feb 22; [Epub ahead of print]
PMID: 16496211 [PubMed - as supplied by publisher]

 

February 2006

Tarer V, Etienne-Julan M, Diara JP, Belloy MS, Mukizi-Mukaza M, Elion J, Romana M. Sickle cell anemia in Guadeloupean children: pattern and prevalence of acute clinical events. Eur J Haematol. 2006 Mar;76(3):193-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16451394&query_hl=2&itool=pubmed_DocSum
 
Brown RT, Connelly M, Rittle C, Clouse B.A longitudinal examination predicting emergency room use in children with sickle cell disease and their caregivers. J Pediatr Psychol. 2006 Mar;31(2):163-73. Epub 2005 Mar 3. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16467316&query_hl=2&itool=pubmed_DocSum
 
 Acute splenic sequestration crisis in adults with hemoglobin S-C disease: a report of nine cases. Ann Hematol. 2006 Feb 7;:1-5 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16463155&query_hl=2&itool=pubmed_DocSum
 
Thomas VJ, Cohn T. Communication skills and cultural awareness courses for healthcare professionals who care for patients with sickle cell disease. J Adv Nurs. 2006 Feb;53(4):480-488. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16448491&query_hl=2&itool=pubmed_DocSum

Wu CJ, Krishnamurti L, Kutok JL, Biernacki M, Rogers S, Zhang W, Antin JH,
Ritz J.   Evidence for ineffective erythropoiesis in severe sickle cell
disease.  Blood. 2005 Nov 15;106(10):3639-45. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16091448&query_hl=23&itool=pubmed_docsum

Dyson, SM and Boswell, G (2006) Sickle Cell Anaemia and Deaths in Custody in the UK and USA Howard Journal of Criminal Justice 45 (1): 14-28  http://www.blackwell-synergy.com/doi/abs/10.1111/j.1468-2311.2006.00401.x

Adamkiewicz, Thomas V MD, MsCR, FRCP(C) *; Boyer, Michael W MD +; Bray, Robert MD, PhD *; Haight, Ann MD *; Yeager, Andrew M MD Identification of Unrelated Cord Blood Units For Hematopoietic Stem Cell Transplantation in Children With Sickle Cell Disease. Journal of Pediatric Hematology/Oncology. 28(1):29-32, January 2006. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16394889&query_hl=21&itool=pubmed_docsum



January 2006

Judy C. Chang, Lin Ye, and Yuet Wai Kan Correction of the sickle cell mutation in embryonic stem cells
Proc Natl Acad Sci U S A. Published online 2006 January 11. doi: 10.1073/pnas.0510177103. Full Text at  http://www.pubmedcentral.gov/articlerender.fcgi?tool=pubmed&pubmedid=16407095
Morris CR. New Strategies for the Treatment of Pulmonary Hypertension in Sickle Cell Disease : The Rationale for Arginine Therapy. Treat Respir Med. 2006;5(1):31-45.
Full Text PDF Click Here
Adams RJ, Brambilla D; Optimizing Primary Stroke Prevention in Sickle Cell Anemia (STOP 2) Trial Investigators.Discontinuing prophylactic transfusions used to prevent stroke in sickle cell disease.N Engl J Med. 2005 Dec 29;353(26):2769-78. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16382063&query_hl=1&itool=pubmed_docsum
 
Amer J, Ghoti H, Rachmilewitz E, Koren A, Levin C, Fibach E. Red blood cells, platelets and polymorphonuclear neutrophils of patients with sickle cell disease exhibit oxidative stress that can be ameliorated by antioxidants. Br J Haematol. 2006 Jan;132(1):108-13. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16371026&query_hl=1&itool=pubmed_docsum
 
Wagner MC, Eckman JR, Wick TM. Histamine increases sickle erythrocyte adherence to endothelium. Br J Haematol. 2006 Feb;132(4):512-22. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16412024&query_hl=4&itool=pubmed_DocSum

 
Legardy JK, Curtis KM. Progestogen-only contraceptive use among women with sickle cell anemia: a systematic review. Contraception. 2006 Feb;73(2):195-204. Epub 2005 Nov 2. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16413850&query_hl=4&itool=pubmed_DocSum
 
Bank A. Regulation of human fetal hemoglobin: new players, new complexities. Blood. 2006 Jan 15;107(2):435-43. Epub 2005 Aug 18. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16109777&query_hl=4&itool=pubmed_DocSum

 
Hogan AM, Kirkham FJ, Prengler M, Telfer P, Lane R, Vargha-Khadem F, Haan M. An exploratory study of physiological correlates of neurodevelopmental delay in infants with sickle cell anaemia. Br J Haematol. 2006 Jan;132(1):99-107. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16371025&query_hl=4&itool=pubmed_DocSum

 
Samakoglu S, Lisowski L, Budak-Alpdogan T, Usachenko Y, Acuto S, Di Marzo R, Maggio A, Zhu P, Tisdale JF, Riviere I, Sadelain M. A genetic strategy to treat sickle cell anemia by coregulating globin transgene expression and RNA interference. Nat Biotechnol. 2006 Jan;24(1):89-94. Epub 2005 Dec 25. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16378095&query_hl=4&itool=pubmed_DocSum
 
Meyappan JD, Lampl M, Hsu LL.Parents' assessment of risk in sickle cell disease treatment with hydroxyurea. J Pediatr Hematol Oncol. 2005 Dec;27(12):644-50. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16344668&query_hl=1
 
Ballas SK, Marcolina MJ. Hyperhemolysis during the evolution of uncomplicated acute painful episodes in patients with sickle cell anemia. Transfusion. 2006 Jan;46(1):105-10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16398738&query_hl=4&itool=pubmed_DocSum
 

December 2005

 Okpala I. Leukocyte adhesion and the pathophysiology of sickle cell disease. Curr Opin Hematol. 2006 Jan;13(1):40-44. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16319686&query_hl=2

Lal A, Fung EB, Pakbaz Z, Hackney-Stephens E, Vichinsky EP. Bone mineral density in children with sickle cell anemia. Pediatr Blood Cancer. 2005 Nov 29 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16317761&query_hl=2

Asakura T, Asakura K, Obata K, Mattiello J, Ballas SK. Blood samples collected under venous oxygen pressure from patients with sickle cell disease contain a significant number of a new type of reversibly sickled cells: Constancy of the percentage of sickled cells in individual patients during steady state. Am J Hematol. 2005 Dec;80(4):249-56. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16315254&query_hl=2

Shankar SM, Arbogast PG, Mitchel E, Cooper WO, Wang WC, Griffin MR. Medical care utilization and mortality in sickle cell disease: A population-based study. Am J Hematol. 2005 Dec;80(4):262-70.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16315251&query_hl=2

Weatherall MW, Higgs DR, Weiss H, Weatherall DJ, Serjeant GR. Phenotype/genotype relationships in sickle cell disease: a pilot twin study. Clin Lab Haematol. 2005 Dec;27(6):384-90. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16307540&query_hl=2

Mark C. Walters  Stem Cell Therapy for Sickle Cell Disease: Transplantation and Gene Therapy The American Society of Hematology Full Text http://www.asheducationbook.org/cgi/content/full/2005/1/66

Richard Lottenberg and Kathryn L. Hassell  An Evidence-Based Approach to the Treatment of Adults with Sickle Cell Disease The American Society of Hematology  http://www.asheducationbook.org/cgi/content/full/2005/1/58

Gladwin MT, Kato GJ. Cardiopulmonary complications of sickle cell disease: role of nitric oxide and hemolytic anemia.Hematology (Am Soc Hematol Educ Program). 2005;:51-7.  http://www.asheducationbook.org/cgi/content/full/2005/1/51

Jenerette C, Funk M, Murdaugh C. Sickle cell disease: a stigmatizing condition that may lead to depression. Issues Ment Health Nurs. 2005 Dec;26(10):1081-101 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16284000&query_hl=2

November 2005

Are You Giving Poor Care to Sickle Cell Patients?  From ED Nursing | October 2005 http://www.ahcpub.com/hot_topics/?htid=1&httid=1648

Alvarez O, Montane B, Lopez G, Wilkinson J, Miller T. Early blood transfusions protect against microalbuminuria in children with sickle cell disease. Pediatr Blood Cancer. 2005 Oct 31; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16261557&query_hl=2

Fitzhugh CD, Wigfall DR, Ware RE. Enalapril and hydroxyurea therapy for children with sickle nephropathy.Pediatr Blood Cancer. 2005 Dec;45(7):982-5. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15704213&query_hl=2

Iyamu EW, Cecil R, Parkin L, Woods G, Ohene-Frempong K, Asakura T. Modulation of erythrocyte arginase activity in sickle cell disease patients during hydroxyurea therapy. Br J Haematol. 2005 Nov;131(3):389-94. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16225659&query_hl=2

Nolan VG, Wyszynski DF, Farrer LA, Steinberg MH. Hemolysis-associated priapism in sickle cell disease. Blood. 2005 Nov 1;106(9):3264-7. Epub 2005 Jun 28 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15985542&query_hl=12

September - October 2005

Buchanan ID, Woodward M, Reed GW.Opioid selection during sickle cell pain crisis and its impact on the development of acute chest syndrome. Pediatr Blood Cancer. 2005 Oct 15;45(5):716-24. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15926170&query_hl=2

Hankins JS, Ware RE, Rogers ZR, Wynn LW, Lane PA, Scott JP, Wang WC. Long-term hydroxyurea therapy for infants with sickle cell anemia: the HUSOFT extension study. Blood. 2005 Oct 1;106(7):2269-75. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16172253&query_hl=2

Downes SM, Hambleton IR, Chuang EL, Lois N, Serjeant GR, Bird AC. Incidence and Natural History of Proliferative Sickle Cell Retinopathy Observations from a Cohort Study. Ophthalmology. 2005 Sep 17;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16171867&query_hl=2

Vichinsky E, Butensky E, Fung E, Hudes M, Theil E, Ferrell L, Williams R, Louie L, Lee PD, Harmatz P. Comparison of organ dysfunction in transfused patients with SCD or beta thalassemia. Am J Hematol. 2005 Sep;80(1):70-4. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16138345&query_hl=2

Kosecki SM, Rodgers PT, Adams MB. Glycemic monitoring in diabetics with sickle cell plus beta-thalassemia hemoglobinopathy. Ann Pharmacother. 2005 Sep;39(9):1557-60 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16076916&query_hl=2

Serjeant GR, Hambleton I, Thame M. Fecundity and pregnancy outcome in a cohort with sickle cell-haemoglobin C disease followed from birth. BJOG. 2005 Sep;112(9):1308-14. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16101613&query_hl=2

 Kato GJ, Martyr S, Blackwelder WC, Nichols JS, Coles WA, Hunter LA, Brennan ML, Hazen SL, Gladwin MT. Levels of soluble endothelium-derived adhesion molecules in patients with sickle cell disease are associated with pulmonary hypertension, organ dysfunction, and mortality. Br J Haematol. 2005 Sep;130(6):943-53. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16156864&query_hl=2

Naprawa JT, Bonsu BK, Goodman DG, Ranalli MA. Serum biomarkers for identifying acute chest syndrome among patients who have sickle cell disease and present to the emergency department. Pediatrics. 2005 Sep;116(3):e420-5 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16099851&query_hl=2

McClish DK, Penberthy LT, Bovbjerg VE, Roberts JD, Aisiku IP, Levenson JL, Roseff SD, Smith WR. Health related quality of life in sickle cell patients: The PiSCES project.Health Qual Life Outcomes. 2005 Aug 29;3(1):50 Full Text http://www.hqlo.com/content/3/1/50

August 2005

Ballas SK, Lusardi M. Hospital readmission for adult acute sickle cell painful episodes: frequency, etiology, and prognostic significance. Am J Hematol. 2005 May;79(1):17-25 Full Text PDF click here Abstract: http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15849770&query_hl=3

Steinberg MH. Predicting clinical severity in sickle cell anaemia. Br J Haematol. 2005 May;129(4):465-81. Full Text PDF click here  Abstract: http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15877729&query_hl=5

Tavakkoli F et al. Effects of Hydroxyurea Treatment on Cerebral Oxygenation in Adult Patients with Sickle Cell Disease: An Open-Label Pilot Study Clinical Therapeutics Volume 27, Number 7 July 2005  Full Text PDF click here

Crandall M, Savedra M. Multidimensional assessment using the adolescent pediatric pain tool: a case report. J Spec Pediatr Nurs. 2005 Jul-Aug;10(3):115-23. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16083431&query_hl=13

Edwards CL, Scales MT, Loughlin C, Bennett GG, Harris-Peterson S, De Castro LM, Whitworth E, Abrams M, Feliu M, Johnson S, Wood M, Harrison O, Killough A. A brief review of the pathophysiology, associated pain, and psychosocial issues in sickle cell disease. Int J Behav Med. 2005;12(3):171-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16083320&query_hl=13

Kosecki SM, Rodgers PT, Adams MBGlycemic Monitoring in Diabetics with Sickle Cell Plus {beta}-Thalassemia Hemoglobinopathy (September).Ann Pharmacother. 2005 Aug 2 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16076916&query_hl=13

Blum A, Yeganeh S, Peleg A, Vigder F, Kryuger K, Khatib A, Khazim K, Dauerman H. Endothelial function in patients with sickle cell anemia during and after sickle cell crises. J Thromb Thrombolysis. 2005 Apr;19(2):83-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16052296&query_hl=13

Mohan JS, Lip GY, Bareford D, Blann AD. Platelet P-selectin and platelet mass, volume and component in sickle cell disease: Relationship to genotype. Thromb Res. 2005 Jul 26; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16051315&query_hl=13

Prengler M, Pavlakis SG, Boyd S, Connelly A, Calamante F, Chong WK, Saunders D, Cox T, Bynevelt M, Lane R, Laverty A, Kirkham FJ. Sickle cell disease: Ischemia and seizures.Ann Neurol. 2005 Aug;58(2):290-302  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16049936&query_hl=13

Kotila TR. Management of acute painful crises in sickle cell disease in Nigeria.Clin Lab Haematol. 2005 Aug;27(4):221-3 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16048488&query_hl=13

Niihara Y, Matsui NM, Shen YM, Akiyama DA, Johnson CS, Sunga MA, Magpayo J, Embury SH, Kalra VK, Cho SH, Tanaka KR. L-Glutamine therapy reduces endothelial adhesion of sickle red blood cells to human umbilical vein endothelial cells.BMC Blood Disord. 2005 Jul 25;5(1):4  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16042803&query_hl=13

 Machado RF, Martyr S, Kato GJ, Barst RJ, Anthi A, Robinson MR, Hunter L, Coles W, Nichols J, Hunter C, Sachdev V, Castro O, Gladwin MT. Sildenafil therapy in patients with sickle cell disease and pulmonary hypertension. Br J Haematol. 2005 Aug;130(3):445-53. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16042696&query_hl=13

Monchanin G, Connes P, Wouassi D, Francina A, Djoda B, Banga PE, Owona FX, Thiriet P, Massarelli R, Martin C. Hemorheology, sickle cell trait, and alpha-thalassemia in athletes: effects of exercise. Med Sci Sports Exerc. 2005 Jul;37(7):1086-92. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=16015123&query_hl=13

July 2005 

Claudia R. Morris, MD; Gregory J. Kato, MD; Mirjana Poljakovic, PhD; Xunde Wang, PhD; William C. Blackwelder, PhD; Vandana Sachdev, MD; Stanley L. Hazen, MD, PhD; Elliott P. Vichinsky, MD; Sidney M. Morris, Jr, PhD; Mark T. Gladwin, MD Dysregulated Arginine Metabolism, Hemolysis-Associated Pulmonary Hypertension, and Mortality in Sickle Cell Disease JAMA. 2005;294:81-90.  http://jama.ama-assn.org/cgi/content/abstract/294/1/81?lookupType=volpage&vol=294&fp=81&view=short

Neil Dalton R, Turner C, Dick M, Height SE, Awogbade M, Inusa B, Okpala I, O'driscoll S, Thein SL, Rees DC. The measurement of urinary hydroxyurea in sickle cell anaemia. Br J Haematol. 2005 Jul;130(1):138-144. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15982356&query_hl=2

Lindsey T, Watts-Tate N, Southwood E, Routhieaux J, Beatty J, Diane C, Phillips M, Lea G, Brown E, Debaun MRJ  Chronic blood transfusion therapy practices to treat strokes in children with sickle cell disease. Am Acad Nurse Pract. 2005 Jul;17(7):277-82. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15982248&query_hl=2

 Udezue E, Girshab AM Observations on the management of acute pain crisis in adult sickle cell disease in eastern Saudi Arabia. Ann Saudi Med. 2005 Mar-Apr;25(2):115-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15977688&query_hl=2

Newman JH. Centennial Article: Pulmonary Hypertension.Am J Respir Crit Care Med. 2005 Jun 30; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15994464&query_hl=2

Ahn H, Li CS, Wang W. Sickle cell hepatopathy: Clinical presentation, treatment, and outcome in pediatric and adult patients.Pediatr Blood Cancer. 2005 Aug;45(2):184-90 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15747337&query_hl=2

Chopra R, Al-Mulhim AR, Al-Baharani AT. Fibrocongestive splenomegaly in sickle cell disease: A distinct clinicopathological entity in the Eastern province of Saudi Arabia.Am J Hematol. 2005 Jul;79(3):180-6.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15981225&query_hl=2

Voskaridou E, Douskou M, Terpos E, Stamoulakatou A, Meletis J, Ourailidis A, Papassotiriou I, Loukopoulos D. Deferiprone as an oral iron chelator in sickle cell disease. Ann Hematol. 2005 Jul;84(7):434-40. Epub 2005 Apr 5.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15809885&query_hl=2

Kofi A Anie, PhD (UK), Joseph Telfair,DrPH, MSW/MPH (US) and the Sickle Cell Disease Transition Study Group (US/UK) Multi-site study of transition in adolescents with sickle cell disease in the United Kingdom and the United States  INTERNATIONAL JOURNAL OF ADOLESCENT MEDICINE AND HEALTH
Volume 17, No. 2 April - June 2005  (pages 169-78). http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15971736&query_hl=2

Baldwin C, Nolan VG, Wyszynski DF, Ma QL, Sebastiani P, Embury SH, Bisbee A, Farrell J, Farrer L, Steinberg MH. Association of klotho, bone morphogenic protein 6, and annexin A2 polymorphisms with sickle cell osteonecrosis. Blood. 2005 Jul 1;106(1):372-5. Epub 2005 Mar 22 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15784727&query_hl=2

June 2005

Hankins JS, Ware RE, Rogers ZR, Wynn LW, Lane PA, Scott JP, Wang WC.
 Long-term hydroxyurea therapy for infants with sickle cell anemia - the Husoft extension study.Blood. 2005 Jun 14;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15956277&query_hl=2

Anie KA. Psychological complications in sickle cell disease. Br J Haematol. 2005 Jun;129(6):723-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15952997&query_hl=2

Williams TN, Mwangi TW, Wambua S, Alexander ND, Kortok M, Snow RW, Marsh K. Sickle Cell Trait and the Risk of Plasmodium falciparum Malaria and Other Childhood Diseases.J Infect Dis. 2005 Jul 1;192(1):178-186. Epub 2005 May 3 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15942909&query_hl=2

Akinyanju OO, Otaigbe AI, Ibidapo MO. Outcome of holistic care in Nigerian patients with sickle cell anaemia. Clin Lab Haematol. 2005 Jun;27(3):195-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15938726&query_hl=2

Zumberg MS, Reddy S, Boyette RL, Schwartz RJ, Konrad TR, Lottenberg R.
 Hydroxyurea therapy for sickle cell disease in community-based practices: A survey of Florida and North Carolina hematologists/oncologists. Am J Hematol. 2005 Jun;79(2):107-13.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15929107&query_hl=2

Buchanan ID, Woodward M, Reed GW. Opioid selection during sickle cell pain crisis and its impact on the development of acute chest syndrome.Pediatr Blood Cancer. 2005 May 30; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15926170&query_hl=2

Steen RG, Fineberg-Buchner C, Hankins G, Weiss L, Prifitera A, Mulhern RK.Cognitive deficits in children with sickle cell disease.J Child Neurol. 2005 Feb;20(2):102-7 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15794173&query_hl=2

May 2005

Lewis L Hsu MD PhD, Brenda K Batts MPH RRT, and Joseph L Rau PhD RRT FAARC Positive Expiratory Pressure Device Acceptance by Hospitalized Children With Sickle Cell Disease Is Comparable to Incentive Spirometry RESPIRATORY CARE  MAY 2005 VOL 50 NO 5 Full  article PDF click here

Sheila Philpott, Jestina Mason and Imoigele P. Aisiku  Patient Satisfaction in the Emergency Department Management of Acute Sickle Cell Pain Academic Emergency Medicine Volume 12, Number 5 suppl 1 158, http://www.aemj.org/cgi/content/abstract/12/5_suppl_1/158-a

Simpson L, He X, Pins M, Huang X, Campbell SC, Yang XJ, Perlman EJ, Bergan RC.v RENAL MEDULLARY CARCINOMA AND ABL GENE AMPLIFICATION. J Urol. 2005 Jun;173(6):1883-1888 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15879768

Ren H, Obike I, Okpala I, Ghebremeskel K, Ugochukwu C, Crawford M. Steady-state haemoglobin level in sickle cell anaemia increases with an increase in erythrocyte membrane n-3 fatty acids.Prostaglandins Leukot Essent Fatty Acids. 2005 May 2;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15876528

Bryant R. Asthma in the pediatric sickle cell patient with acute chest syndrome.J Pediatr Health Care. 2005 May-Jun;19(3):157-62  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15867831

Jacob E, Beyer JE, Miaskowski C, Savedra M, Treadwell M, Styles L. Are There Phases to the Vaso-Occlusive Painful Episode in Sickle Cell Disease?J Pain Symptom Manage. 2005 Apr;29(4):392-400.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15857743

Ballas SK, Lusardi M. Hospital readmission for adult acute sickle cell painful episodes: frequency, etiology, and prognostic significance. Am J Hematol. 2005 May;79(1):17-25 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15849770

April 2005

Derchi G, Forni GL, Formisano F, Cappellini MD, Galanello R, D'Ascola G, Bina P,
Magnano C, Lamagna M. Efficacy and safety of sildenafil in the treatment of severe pulmonary hypertension in patients with hemoglobinopathies. Haematologica. 2005 Apr;90(4):452-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15820939

Voskaridou E, Douskou M, Terpos E, Stamoulakatou A, Meletis J, Ourailidis A,
Papassotiriou I, Loukopoulos D.eferiprone as an oral iron chelator in sickle cell disease.nn Hematol. 2005 Apr 5 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15809885

Harrison MO, Edwards CL, Koenig HG, Bosworth HB, Decastro L, Wood M.
 Religiosity/Spirituality and pain in patients with sickle cell disease. J Nerv Ment Dis. 2005 Apr;193(4):250-7 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15805821

Mohan JS, Lip GY, Wright J, Bareford D, Blann AD. Plasma levels of tissue factor and soluble E-selectin in sickle cell disease: relationship to genotype and to inflammation.Blood Coagul Fibrinolysis. 2005 Apr;16(3):209-14. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15795541

Eisenbach Ch, Pohl J, Dikow R, Stremmel W, Encke J Severe rhabdomyolysis and renal failure triggered by a sauna visit in sickle cell trait: a case report. Clin Nephrol. 2005 Mar;63(3):229-31. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15786826

Yan JH, Ataga K, Kaul S, Olson JS, Grasela DM, Gothelf S, Kutlar A, Orringer E. The influence of renal function on hydroxyurea pharmacokinetics in adults
with sickle cell disease. J Clin Pharmacol. 2005 Apr;45(4):434-45. Full Text at http://jcp.sagepub.com/cgi/content/full/45/4/434

Ahmed S, Siddiqui AK, Sison CP, Shahid RK, Mattana J. Hemoglobin oxygen saturation discrepancy using various methods in patients with sickle cell vaso-occlusive painful crisis.Eur J Haematol. 2005 Apr;74(4):309-14. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15777343

March 2005

Beth Kladny, MS, CGC1,3, Elizabeth A. Gettig, MS, CGC2, and Lakshmanan Krishnamurti, MD3 Systematic follow-up and case management of the abnormal newborn screen can improve acceptance of genetic counseling for sickle cell or other hemoglobinopathy trait. Genetics In Medicine February 2005 Vol. 7No. 2 Click Here for a PDF full text copy

Hankins J, Jeng M, Harris S, Li CS, Liu T, Wang W. Chronic Transfusion Therapy for Children With Sickle Cell Disease and Recurrent Acute Chest Syndrome.J Pediatr Hematol Oncol. 2005 Mar;27(3):158-161. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15750449

Ahn H, Li CS, Wang W. Sickle cell hepatopathy: Clinical presentation, treatment, and outcome in pediatric and adult patients.Pediatr Blood Cancer. 2005 Mar 3;  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15747337

Knight-Madden JM, Forrester TS, Lewis NA, Greenough A Asthma in children with sickle cell disease and its association with acute chest syndrome.Thorax. 2005 Mar;60(3):206-10. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15741436

Lin EE, Rodgers GP, Gladwin MT. Hemolytic Anemia-associated Pulmonary Hypertension in Sickle Cell Disease.Curr Hematol Rep. 2005 Mar;4(2):117-25. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15720960

Steen, RG, T Emudianughe, M Hunte, J Glass, S Wu, X Xiong, and WE Reddick. 
2005. Brain volume in pediatric patients with sickle cell disease: evidence of
volumetric growth delay? Am. J. Neuroradiol. 26: 1- 8  http://www.ajnr.org/cgi/content/abstract/26/3/455

Steen, RG and RJ Ogg. 2005. Abnormally high levels of brain N-acetyl-
aspartate in children with sickle cell disease. Am. J. Neuroradiol. 26: 1-5 http://www.ajnr.org/cgi/content/figsonly/26/3/463

February 2005

Bakanay SM, Dainer E, Clair B, Adekile A, Daitch L, Wells L, Holley L, Smith D,
Kutlar A. Mortality in sickle cell patients on hydroxyurea therapy. Blood. 2005 Jan 15;105(2):545-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15454485

Day SW. Development and evaluation of a sickle cell assessment instrument.Pediatr Nurs. 2004 Nov-Dec;30(6):451-8.  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15704592

Fitzhugh CD, Wigfall DR, Ware RE. Enalapril and hydroxyurea therapy for children with sickle nephropathy.Pediatr Blood Cancer. 2005 Feb 9; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15704213

Adams RJ. TCD in sickle cell disease: an important and useful test.Pediatr Radiol. 2005 Feb 10; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15703904

Bernaudin F, Verlhac S, Coic L, Lesprit E, Brugieres P, Reinert P. Long-term follow-up of pediatric sickle cell disease patients with abnormal high velocities on transcranial Doppler. Pediatr Radiol. 2005 Feb 10 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15703901

Raj A, Bertolone S, Bond S, Burnett D, Denker A. Cathlink(R) 20: A subcutaneous implanted central venous access device used in children with sickle cell disease on long-term erythrocytapheresis-a report of low complication rates.Pediatr Blood Cancer. 2005 Feb 7; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15700248

Pawloski JR, Hess DT, Stamler JS. Impaired vasodilation by red blood cells in sickle cell disease.Proc Natl Acad Sci U S A. 2005 Feb 7 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15699345

Adorno EV, Couto FD, Moura Neto JP, Menezes JF, Rego M, Reis MG, Goncalves
MS. Hemoglobinopathies in newborns from Salvador, Bahia, Northeast Brazil.Cad Saude Publica. 2005 Feb;21(1):292-298. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15692663

Osby M, Shulman IA.Phenotype matching of donor red blood cell units for nonalloimmunized sickle cell disease patients: a survey of 1182 North American laboratories.Arch Pathol Lab Med. 2005 Feb;129(2):190-3. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15679419

January 2005

Hibbert JM, Hsu LL, Bhathena SJ, Irune I, Sarfo B, Creary MS, Gee BE, Mohamed
AI, Buchanan ID, Al-Mahmoud A, Stiles JK. Proinflammatory cytokines and the hypermetabolism of children with sickle cell disease. Exp Biol Med (Maywood). 2005 Jan;230(1):68-74.  Click here for full text PDF http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15618128

Magana MT, Perea FJ, Ongay Z, Ibarra B. 3' haplotypes of the beta-globin gene in beta(s)-chromosomes of Mexican individuals.Blood Cells Mol Dis. 2005 Jan-Feb;34(1):48-52. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15607699

Somjee SS, Warrier RP, Thomson JL, Ory-Ascani J, Hempe JMAdvanced glycation end-products in sickle cell anaemia.Br J Haematol. 2005 Jan;128(1):112-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15606557

 Gulbis B, Haberman D, Dufour D, Christophe C, Vermylen C, Kagambega F, Corazza F, Devalck C, Dresse MF, Hunninck K, Klein A, Le PQ, Loop M, Maes P, Philippet P, Sariban E, Van Geet C, Ferster A.Hydroxyurea for sickle cell disease in children and for prevention of cerebrovascular events. The Belgian experience.Blood. 2004 Dec 16; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15604217

Bonds DR. Three decades of innovation in the management of sickle cell disease: the
road to understanding the sickle cell disease clinical phenotype. Blood Rev. 2005 Mar;19(2):99-110. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15603913

Treadwell MJ, Law AW, Sung J, Hackney-Stephens E, Quirolo K, Murray E,
Glendenning GA, Vichinsky E. Barriers to adherence of deferoxamine usage in sickle cell disease.Pediatr Blood Cancer. 2004 Dec 15; http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15602707

Stephen H. Embury, Neil M. Matsui, Sahana Ramanujam, Tanya N. Mayadas, Constance T. Noguchi, Bhalchandra A. Diwan, Narla Mohandas, and Anthony T. W. Cheung The contribution of endothelial cell P-selectin to the microvascular flow of mouse sickle erythrocytes in vivo Blood. 2004 Nov 15;104(10):3378-85 For Full Text PDF Click Here for the abstract: http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15271798

Dampier C, Setty BN, Eggleston B, Brodecki D, O'neal P, Stuart M.Vaso-occlusion in children with sickle cell disease: clinical characteristics and biologic correlates.J Pediatr Hematol Oncol. 2004 Dec;26(12):785-90. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15591896

December 2004

Marie J Stuart, Ronald L Nagel. Sickle-cell disease - www.thelancet.com Vol 364 October 9, 2004 - Lancet Seminar article on Sickle Cell Disease. Click her for a full pfd version of this summary review article 

R.E. Eckart, S.L. Scoville, C.L. Campbell, E.A. Shry, K.C. Stajduhar, R.N. Potter, L.A. Pearse, and R. Virman  Sudden Death in Young Adults: A 25-Year Review
of Autopsies in Military Recruits 7 December 2004 issue of Annals of Internal
Medicine (volume 141, pages 829-834) - n 44 of the 126 recruits who died, examination of medical records and autopsy results revealed no explanation for
the death. Other causes of death included sickle-cell crisis (3 deaths) http://www.annals.org/cgi/content/summary/141/11/829

Wagner MC, Eckman JR, Wick TM. Sickle cell adhesion depends on hemodynamics and endothelial activation. J Lab Clin Med. 2004 Nov;144(5):260-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15570244

Buchanan GR, Debaun MR, Quinn CT, Steinberg MH. Sickle cell disease.Hematology (Am Soc Hematol Educ Program). 2004;:35-47.  An excellent review available Full Text by PDF or HTML at http://www.asheducationbook.org/cgi/reprint/2004/1/35

Kaur N, Motwani B, Sivasubramaniam D, Feldman L, Allen S, Ferguson R, Shiomoto
G, Ansell D, Westerman M, Feldman L. Potential role of the ventilation and perfusion (V/Q) lung scan in the diagnosis of acute chest syndrome in adults with sickle cell disease. Am J Hematol. 2004 Dec;77(4):407-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15551281

Christoph GW, Hofrichter J, Eaton WA. Understanding the shape of sickled red cells. Biophys J. 2004 Nov 12;  Full Text at http://www.biophysj.org/cgi/rapidpdf/biophysj.104.051250v1

Nelson J. Chao, Stephen G. Emerson, and Kenneth I. Weinberg  Stem Cell Transplantation (Cord Blood Transplants)  Hematology 2004:354-371 Full Text at http://www.asheducationbook.org/cgi/content/abstract/2004/1/354

November 2004

Horan JT, Liesveld JL, Fenton P, Blumberg N, Walters MC. Hematopoietic stem cell transplantation for multiply transfused patients with sickle cell disease and thalassemia after low-dose total body irradiation, fludarabine, and rabbit anti-thymocyte globulin.Bone Marrow Transplant. 2004 Nov 08 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15531901

Wild BJ, Green BN, Stephens AD.The potential of electrospray ionization mass spectrometry for the diagnosis of hemoglobin variants found in newborn screening. Blood Cells Mol Dis. 2004 Nov-Dec;33(3):308-17. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15528150

Bergeron MF, Cannon JG, Hall EL, Kutlar A. Erythrocyte Sickling During Exercise and Thermal Stress.Clin J Sport Med. 2004 Nov;14(6):354-356. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15523207

Buison AM, Kawchak DA, Schall J, Ohene-Frempong K, Stallings VA, Zemel BS. Low vitamin D status in children with sickle cell disease. J Pediatr. 2004 Nov;145(5):622-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15520761

Suell MN, Horton TM, Dishop MK, Mahoney DH, Olutoye OO, Mueller BU. Outcomes for children with gallbladder abnormalities and sickle cell disease. J Pediatr. 2004 Nov;145(5):617-21. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15520760

Kwiatkowski JL, Cohen AR. Iron chelation therapy in sickle-cell disease and other
transfusion-dependent anemias. Hematol Oncol Clin North Am. 2004 Dec;18(6):1355-77. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15511620

Persons DA, Tisdale JF. Gene therapy for the hemoglobin disorders. Semin Hematol. 2004 Oct;41(4):279-86. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15508113

October 2004

Imren S, Fabry ME, Westerman KA, Pawliuk R, Tang P, Rosten PM, Nagel RL,
Leboulch P, Eaves CJ, Humphries RK. High-level beta-globin expression and preferred intragenic integration after lentiviral transduction of human cord blood stem cells.J Clin Invest. 2004 Oct;114(7):953-62. Free Full Text article at http://www.pubmedcentral.nih.gov/articlerender.fcgi?tool=pubmed&pubmedid=15467834

Trzepacz AM, Vannatta K, Gerhardt CA, Ramey C, Noll RB. Emotional, Social, and Behavioral Functioning of Children With Sickle Cell Disease and Comparison Peers.J Pediatr Hematol Oncol. 2004 Oct;26(10):642-648. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15454835

Minniti CP, Gidvani VK, Bulas D, Brown WA, Vezina G, Driscoll MC. Transcranial Doppler Changes in Children With Sickle Cell Disease on Transfusion Therapy J Pediatr Hematol Oncol. 2004 Oct;26(10):626-630. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15454832

Williams R, Olivi S, Li CS, Storm M, Cremer L, Mackert P, Wang WOral Glutamine Supplementation Decreases Resting Energy Expenditure in Children and Adolescents With Sickle Cell Anemia. J Pediatr Hematol Oncol. 2004 Oct;26(10):619-625. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15454831

Bakanay SM, Dainer E, Clair B, Adekile A, Daitch L, Wells L, Holley L, Smith D,
Kutlar A. Mortality in Sickle Cell Patients on Hydroxyurea Therapy. Blood. 2004 Sep 28 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15454485

September 2004

Telfair, Joseph. Alexander, Leah R. Loosier, Penny S. Alleman-Velez, Patty L. Simmons, Julie. Providers' Perspectives and Beliefs Regarding Transition to Adult Care for Adolescents with Sickle Cell Disease Journal of Health Care for the Poor and Underserved Volume 15, Number 3, August 2004  Click here for full text in PDF format

Brousseau DC, Scott JP, Hillery CA, Panepinto JA. The effect of magnesium on length of stay for pediatric sickle cell pain crisis. Acad Emerg Med. 2004 Sep;11(9):968-72. Click here for full text in PDF format

Rivera A, Ferreira A, Bertoni D, Romero JR, Brugnara C.Abnormal regulation of Mg transport via Na/Mg exchange in sickle erythrocytes. Blood. 2004 Sep 7 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15353477

Wright J, Bareford D, Wright C, Augustine G, Olley K, Musamadi L, Dhanda C, Knight C. Day case management of sickle pain: 3 years experience in a UK sickle cell
unit.Br J Haematol. 2004 Sep;126(6):878-80 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15352993

Moussavou A, Vierin Y, Eloundou-Orima C, Mboussou M, Keita M. Sickle cell disease pain management following the World Health Organization's protocol Arch Pediatr. 2004 Sep;11(9):1041-1045. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15350992

Ware RE, Zimmerman SA, Sylvestre PB, Mortier NA, Davis JS, Treem WR, Schultz
WH. Prevention of secondary stroke and resolution of transfusional iron overload in children with sickle cell anemia using hydroxyurea and phlebotomy. J Pediatr. 2004 Sep;145(3):346-52. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15343189

August 2004

Shaiova L, Wallenstein D. Outpatient management of sickle cell pain with chronic opioid pharmacotherapy. J Natl Med Assoc. 2004 Jul;96(7):984-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15253332

Click here for a PDF file of this entire article: 

Wang H, Laslett LJ, Richman CM, Wun T. Acute myocardial infarction in hemoglobin SC disease.Ann Hematol. 2004 Aug 5  http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15300406

Dourakis SP, Alexopoulou A, Papageorgiou C, Kaloterakis A, Hadziyannis SJ. Acute chest syndrome in sickle-cell trait; Two case reports in persons of Mediterranean origin and review of the literature. Eur J Intern Med. 2004 Jul;15(4):248-250. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15288680

Conran N, Fattori A, Saad ST, Costa FF. Increased levels of soluble ICAM-1 in the plasma of sickle cell patients are reversed by hydroxyurea.Am J Hematol. 2004 Aug;76(4):343-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15282666

Kirkham FJ, DeBaun MR. Stroke in Children with Sickle Cell Disease.Curr Treat Options Neurol. 2004 Sep;6(5):357-375. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15279758

Boyd JH, Moinuddin A, Strunk RC, DeBaun MR.Asthma and acute chest in sickle-cell disease. Pediatr Pulmonol. 2004 Sep;38(3):229-32. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15274102

Cordeiro N, Oniyangi O. Phytomedicines (medicines derived from plants) for sickle cell disease.Cochrane Database Syst Rev. 2004;3:CD004448. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15266534

July 2004

Telfair J, Ehiri JE, Loosier PS, Baskin ML. Transition to adult care for adolescents with sickle cell disease: results of a national survey. Int J Adolesc Med Health. 2004 Jan-Mar;16(1):47-64. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15148858

Adamkiewicz TV, Mehta PS, Boyer MW, Kedar A, Olson TA, Olson E, Chiang KY, Maurer D, Mogul MJ, Wingard JR, Yeager AM. Transplantation of unrelated placental blood cells in children with high-risk sickle cell disease. Bone Marrow Transplant. 2004 Jul 12 http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15247929

Schall JI, Zemel BS, Kawchak DA, Ohene-Frempong K, Stallings VA. Vitamin A status, hospitalizations, and other outcomes in young children with sickle cell disease. J Pediatr. 2004 Jul;145(1):99-106. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15238915

Ergul S, Brunson CY, Hutchinson J, Tawfik A, Kutlar A, Webb RC, Ergul A. Vasoactive factors in sickle cell disease: In vitro evidence for endothelin-1-mediated vasoconstriction. Am J Hematol. 2004 Jul;76(3):245-51. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15224360

Ahmed S, Siddiqui AK, Sadiq A, Shahid RK, Patel DV, Russo LA.  Echocardiographic abnormalities in sickle cell disease. Am J Hematol. 2004 Jul;76(3):195-8. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15224351

Sherman SC, Sule HP. Acute myocardial infarction in a young man with sickle cell disease.J Emerg Med. 2004 Jul;27(1):31-5. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15219301

Bodhise PB, Dejoie M, Brandon Z, Simpkins S, Ballas SK. Non-pharmacologic Management of Sickle Cell Pain.Hematology. 2004 Jun;9(3):235-7. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15204105

June 2004

Kokoska Er E, West Kw K, Carney De D, Engum Se S, Heiny Me M, Rescorla Fj F. Risk factors for acute chest syndrome in children with sickle cell disease
undergoing abdominal surgery. J Pediatr Surg. 2004 Jun;39(6):848-50. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15185210

 Ballas SK, Files B, Luchtman-Jones L, Benjamin L, Swerdlow P, Hilliard L, Coates T, Abboud M, Wojtowicz-Praga S, Grindel JM. Safety of purified poloxamer 188 in sickle cell disease: phase I study of a non-ionic surfactant in the management of acute chest syndrome. Hemoglobin. 2004 May;28(2):85-102. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15182051

Zhang C, Li X, Lian L, Chen Q, Abdulmalik O, Vassilev V, Lai CS, Asakura T. Anti-sickling effect of MX-1520, a prodrug of vanillin: an in vivo study
using rodents. Br J Haematol. 2004 Jun;125(6):788-95. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15180869

Serjeant GR, Loy LL, Crowther M, Hambleton IR, Thame M.  Outcome of Pregnancy in Homozygous Sickle Cell Disease. Obstet Gynecol. 2004 Jun;103(6):1278-1285. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15172865

Ballas SK, Viscusi ER, Epstein KR. Management of acute chest wall sickle cell pain with nebulized morphine.Am J Hematol. 2004 Jun;76(2):190-1. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15164390

McKerrell TD, Cohen HW, Billett HH. The older sickle cell patient.Am J Hematol. 2004 Jun;76(2):101-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15164373

Gebreyohanns M, Adams RJ. Sickle cell disease: primary stroke prevention.CNS Spectr. 2004 Jun;9(6):445-9. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15162093

Juwah AI, Nlemadim EU, Kaine W Types of anaemic crises in paediatric patients with sickle cell anaemia seen in Enugu, Nigeria.Arch Dis Child. 2004 Jun;89(6):572-6. http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15155406

May 2004

Brendan Flannery, PhD; Stephanie Schrag, DPhil; Nancy M. Bennett, MD;
Ruth Lynfield, MD; Lee H. Harrison, MD; Arthur Reingold, MD; Paul R. Cieslak, MD; James Hadler, MD, MPH; Monica M. Farley, MD; Richard R. Facklam, PhD;
Elizabeth R. Zell, MStat; Cynthia G. Whitney, MD, MPH; for the Active Bacterial Core Surveillance/Emerging Infections Program Network:  Impact of Childhood Vaccination on Racial Disparities in Invasive Streptococcus pneumoniae Infections JAMA. 2004;291:2197-2203.

http://jama.ama-assn.org/cgi/content/full/291/18/2197

Gil KM, Carson JW, Porter LS, Scipio C, Bediako SM, Orringer E. Daily mood and stress predict pain, health care use, and work activity in african american adults with sickle-cell disease. Health Psychol. 2004 May;23(3):267-74. http://www.ncbi.nlm.nih.gov:80/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15099167

Makrydimas G, Georgiou I, Bouba I, Lolis D, Nicolaides KH. Early prenatal diagnosis by celocentesis. Ultrasound Obstet Gynecol. 2004 May;23(5):482-5.  http://www.ncbi.nlm.nih.gov:80/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15133800

Kral MC, Brown RT. Transcranial Doppler ultrasonography and executive dysfunction in children with sickle cell disease.J Pediatr Psychol. 2004 Apr-May;29(3):185-95. http://www.ncbi.nlm.nih.gov:80/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15131136

Walters MC. Sickle cell anemia and hematopoietic cell transplantation: When is a pound of cure worth more than an ounce of prevention? Pediatr Transplant. 2004;8 Suppl 5:33-8. http://www.ncbi.nlm.nih.gov:80/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15125704

Sakhalkar VS, Rao SP, Weedon J, Miller ST. Elevated plasma sVCAM-1 levels in children with sickle cell disease: Impact of chronic transfusion therapy.Am J Hematol. 2004 May;76(1):57-60. http://www.ncbi.nlm.nih.gov:80/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15114598

Schnog JB, Mac Gillavry MR, Van Zanten AP, Meijers JC, Rojer RA, Duits AJ, Ten
Cate H, Brandjes DP. Protein C and S and inflammation in sickle cell disease.Am J Hematol. 2004 May;76(1):26-32.